Heparin cofactor II-thrombin complex: A biomarker of MPS disease

Molecular Genetics and Metabolism

Volumn 94, Issue 4, 2008, Pages 456-461

  Randall, Derrick R ^a   Colobong, Karen E ^a   Hemmelgarn, Harmony ^a   Sinclair, Graham B ^a   Hetty, Elly ^a   Thomas, Anita ^a   Bodamer, Olaf A ^b   Volkmar, Barbara ^c   Fernhoff, Paul M ^d   Casey, Robin ^e   Chan, Alicia K ^f   Mitchell, Grant ^g   Stockler, Silvia ^a   Melancon, Serge ^h   Rupar, Tony ⁱ   Clarke, Lorne A ^a  

^a UNIVERSITY OF BRITISH COLUMBIA   (Canada)

^b UNIVERSITY OF VIENNA   (Austria)

^c Paracelsus Medical School Salzburg   (Austria)

^d EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^e UNIVERSITY OF CALGARY   (Canada)

^f UNIVERSITY OF ALBERTA   (Canada)

^g UNIVERSITÉ DE MONTRÉAL   (Canada)

^h MCGILL UNIVERSITY   (Canada)

ⁱ UNIVERSITY OF WESTERN ONTARIO   (Canada)

Author keywords

Biomarker; Enzyme replacement therapy; Glycosaminoglycan; Heparin cofactor II; Lysosomal storage disease; Lysosome; Mucopolysaccharidosis; Thrombin

Indexed keywords

GLYCOSAMINOGLYCAN; HEPARIN COFACTOR II; HEPARIN DERIVATIVE;

ADOLESCENT; ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BLOOD LEVEL; BODY BURDEN; CHILD; CONTROLLED STUDY; DISEASE COURSE; DISEASE SEVERITY; ENZYME LINKED IMMUNOSORBENT ASSAY; ENZYME REPLACEMENT; GENE MUTATION; HUMAN; HUMAN CELL; HUNTER SYNDROME; HURLER SYNDROME; INFANT; MAROTEAUX LAMY SYNDROME; MOUSE; NONHUMAN; PRIORITY JOURNAL; TREATMENT RESPONSE;

ANIMALS; BIOLOGICAL MARKERS; BLOOD CHEMICAL ANALYSIS; ENZYME-LINKED IMMUNOSORBENT ASSAY; FEMALE; HEPARIN COFACTOR II; HUMANS; LONGITUDINAL STUDIES; MALE; MICE; MUCOPOLYSACCHARIDOSES; THROMBIN;

EID: 46749143719     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2008.05.001     Document Type: Article

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