Smn deficiency causes neuritogenesis and neurogenesis defects in the retinal neurons of a mouse model of spinal muscular atrophy

Developmental Neurobiology

Volumn 71, Issue 2, 2011, Pages 153-169

  Liu, Hong ^a   Beauvais, Ariane ^a   Baker, Adam N ^a   Tsilfidis, Catherine ^a,b   Kothary, Rashmi ^a,b  

^a OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF OTTAWA   (Canada)

Author keywords

Retina; Spinal muscular atrophy; Survival of motor neuron

Indexed keywords

MESSENGER RNA; SURVIVAL MOTOR NEURON PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CELL COMPOSITION; CONTROLLED STUDY; ELECTRORETINOGRAPHY; GENE MUTATION; GLIA CELL; HISTOPATHOLOGY; MOUSE; NERVE CELL; NERVOUS SYSTEM DEVELOPMENT; NERVOUS SYSTEM MALFORMATION; NEUROFILAMENT; NEUROPATHOLOGY; NONHUMAN; OPTIC NERVE; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; RETINA AMACRINE CELL; RETINA GANGLION CELL; RETINA NERVE CELL; RETINA NEUROEPITHELIAL LAYER; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; SPINAL MUSCULAR ATROPHY; SYNAPTOGENESIS;

ANIMALS; BLOTTING, WESTERN; CELLS, CULTURED; DISEASE MODELS, ANIMAL; ELECTRORETINOGRAPHY; GENE EXPRESSION; GENE EXPRESSION PROFILING; IMMUNOHISTOCHEMISTRY; IN SITU NICK-END LABELING; MICE; MICE, INBRED C57BL; MICE, MUTANT STRAINS; MUSCULAR ATROPHY, SPINAL; NEUROGENESIS; NEURONS; OPTIC NERVE; RETINA; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; SURVIVAL OF MOTOR NEURON 1 PROTEIN;

EID: 78650946814     PISSN: 19328451     EISSN: 10974695     Source Type: Journal    
DOI: 10.1002/dneu.20840     Document Type: Article

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