Abnormal motoneuron migration, differentiation, and axon outgrowth in spinal muscular atrophy

Acta Neuropathologica

Volumn 115, Issue 3, 2008, Pages 313-326

  Simic, Goran ^a   Mladinov, Mihovil ^a   Simic, Durdica Seso ^b   Milosevic, Natasa Jovanov ^a   Islam, Atiqul ^c   Pajtak, Alen ^a   Barisic, Nina ^b   Sertic, Jadranka ^b   Lucassen, Paul J ^d   Hof, Patrick R ^e   Kruslin, Bozo ^a  

^a UNIVERSITY OF ZAGREB   (Croatia)

^b KBC Zagreb   (Croatia)

^c KAROLINSKA INSTITUTE   (Sweden)

^d UNIVERSITY OF AMSTERDAM   (Netherlands)

^e MOUNT SINAI SCHOOL OF MEDICINE   (United States)

Author keywords

Migration; Motoneurons; Pathogenesis; SMN1 gene; Spinal muscular atrophy

Indexed keywords

CD68 ANTIGEN; GLIAL FIBRILLARY ACIDIC PROTEIN; MICROTUBULE ASSOCIATED PROTEIN 2; PHOSPHOPROTEIN;

AGE DISTRIBUTION; APOPTOSIS; ARTICLE; ASTROCYTE; CELL ACTIVATION; CELL MIGRATION; CLINICAL ARTICLE; CONTROLLED STUDY; CORRELATION ANALYSIS; DENDRITE; DISEASE SEVERITY; EXON; FEMALE; GENE DELETION; HOMOZYGOSITY; HUMAN; HUMAN CELL; HUMAN TISSUE; MALE; MICROGLIA; MOTOR NEURON DISEASE; NERVE CELL DIFFERENTIATION; NERVE CELL NECROSIS; NERVE FIBER GROWTH; PRIORITY JOURNAL; PROTEIN ANALYSIS; QUANTITATIVE ANALYSIS; SPINAL CORD VENTRAL HORN; SPINAL MUSCULAR ATROPHY; SYNAPSE; TELOMERE; WHITE MATTER;

AXONS; BRAIN; CELL DIFFERENTIATION; CELL MOVEMENT; HUMANS; IMMUNOHISTOCHEMISTRY; IN SITU NICK-END LABELING; MOTOR NEURONS; MUSCLE, SKELETAL; SPINAL CORD; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD;

EID: 39749168988     PISSN: 00016322     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00401-007-0327-1     Document Type: Article

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