Neurodevelopmental consequences of Smn depletion in a mouse model of spinal muscular atrophy

Journal of Neuroscience Research

Volumn 88, Issue 1, 2010, Pages 111-122

  Liu, Hong ^a   Shafey, Dina ^a,b   Mooresa, Justin N ^a   Kothary, Rashmi ^a,b  

^a OTTAWA HOSPITAL RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF OTTAWA   (Canada)

Author keywords

Alternative splicing; Degeneration; Gene expression; Neurodevelopment; Spinal muscular atrophy

Indexed keywords

EXCITATORY AMINO ACID TRANSPORTER; HYPOXIA INDUCIBLE FACTOR; MESSENGER RNA; SURVIVAL MOTOR NEURON PROTEIN; SURVIVAL MOTOR NEURON PROTEIN 2; UBIQUITIN PROTEIN LIGASE;

ALTERNATIVE RNA SPLICING; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL DEATH; CELL STRUCTURE; CONTROLLED STUDY; CRANIAL NERVE; DEVELOPMENTAL STAGE; DISEASE COURSE; EMBRYO; EMBRYO DEVELOPMENT; FEMALE; GENE DELETION; GENE EXPRESSION; GENETIC TRANSCRIPTION; LUMBAR SPINE; MALE; MOUSE; NERVE CELL DIFFERENTIATION; NONHUMAN; NUCLEOTIDE SEQUENCE; ORGANOGENESIS; PATHOGENESIS; PATHOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; RNA SPLICING; SPINAL MUSCULAR ATROPHY; SPINAL NERVE; TELENCEPHALON; TISSUE SPECIFICITY;

ALTERNATIVE SPLICING; ANIMALS; APOPTOSIS; BLOTTING, WESTERN; CELL COUNT; DISEASE MODELS, ANIMAL; GENE EXPRESSION REGULATION, DEVELOPMENTAL; IMMUNOHISTOCHEMISTRY; IN SITU HYBRIDIZATION; IN SITU NICK-END LABELING; MICE; MICE, KNOCKOUT; MUSCULAR ATROPHY, SPINAL; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER; STAINING AND LABELING; SURVIVAL OF MOTOR NEURON 1 PROTEIN; SURVIVAL OF MOTOR NEURON 2 PROTEIN; TELENCEPHALON;

EID: 73949131374     PISSN: 03604012     EISSN: 10974547     Source Type: Journal    
DOI: 10.1002/jnr.22189     Document Type: Article

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