A secreted variant of cartilage oligomeric matrix protein carrying a chondrodysplasia-causing mutation (p.H587R) disrupts collagen fibrillogenesis

Arthritis and Rheumatism

Volumn 63, Issue 1, 2011, Pages 159-167

  Hansen, Uwe ^a   Platz, Nicole ^b   Becker, Alexander ^b   Bruckner, Peter ^a   Paulsson, Mats ^b   Zaucke, Frank ^b  

^a UNIVERSITY HOSPITAL MÜNSTER   (Germany)

^b UNIVERSITY OF COLOGNE   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

CARTILAGE OLIGOMERIC MATRIX PROTEIN; COLLAGEN FIBRIL; COLLAGEN TYPE 1; COLLAGEN TYPE 11;

ARTICLE; CHONDRODYSPLASIA; CONTROLLED STUDY; GENE MUTATION; HUMAN; HUMAN CELL; IMMUNOGOLD ELECTRON MICROSCOPY; NUCLEOTIDE SEQUENCE; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN PURIFICATION;

ACHONDROPLASIA; CELLS, CULTURED; COLLAGEN; EXTRACELLULAR MATRIX; EXTRACELLULAR MATRIX PROTEINS; GLYCOPROTEINS; HEK293 CELLS; HUMANS; IMMUNOHISTOCHEMISTRY; MICROSCOPY, ELECTRON; MUTATION;

EID: 78650800703     PISSN: 00043591     EISSN: 15290131     Source Type: Journal    
DOI: 10.1002/art.30073     Document Type: Article

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