Expression of mutant cartilage oligomeric matrix protein in human chondrocytes induces the pseudoachondroplasia phenotype

Journal of Orthopaedic Research

Volumn 24, Issue 4, 2006, Pages 700-707

  Merritt, Thomas M ^a,b   Alcorn, Joseph L ^a,b   Haynes, Richard ^c   Hecht, Jacqueline T ^a,b,c  

^a UNIVERSITY OF TEXAS MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF TEXAS   (United States)

^c Shriners Hospital for Children   (United States)

Author keywords

Cartilage oligomeric matrix protein; Chondrocytes; COMP; Dwarfism; Endoplasmic reticulum; Pseudoachondroplasia

Indexed keywords

CARTILAGE OLIGOMERIC MATRIX PROTEIN; COLLAGEN TYPE 9; CARTILAGE MATRIX PROTEIN; GLYCOPROTEIN; MATRILIN 3; SCLEROPROTEIN;

ACHONDROPLASIA; ADENOVIRUS; ARTICLE; BIOLOGICAL MODEL; CARTILAGE CELL; CELL CULTURE; CELL DIFFERENTIATION; CONTROLLED STUDY; GENETIC TRANSFECTION; HUMAN; HUMAN CELL; IMMUNOHISTOCHEMISTRY; IN VITRO STUDY; MOLECULAR MECHANICS; MUTANT; PHENOTYPE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SECRETION; VIRUS RECOMBINANT; WILD TYPE; ENDOPLASMIC RETICULUM; GENETICS; METABOLISM; MUTATION; PHYSIOLOGY;

ACHONDROPLASIA; CELLS, CULTURED; CHONDROCYTES; COLLAGEN TYPE IX; ENDOPLASMIC RETICULUM; EXTRACELLULAR MATRIX PROTEINS; GLYCOPROTEINS; HUMANS; MUTATION; PHENOTYPE; TRANSFECTION;

EID: 33646190753     PISSN: 07360266     EISSN: None     Source Type: Journal    
DOI: 10.1002/jor.20100     Document Type: Article

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