Lysosomal compromise and brain dysfunction: Examining the role of neuroaxonal dystrophy

Biochemical Society Transactions

Volumn 38, Issue 6, 2010, Pages 1436-1441

  Walkley, Steven U ^a   Sikora, Jakub ^b   Micsenyi, Matthew ^a   Davidson, Cristin ^a   Dobrenis, Kostantin ^a  

^a ALBERT EINSTEIN COLLEGE OF MEDICINE   (United States)

^b Charles University in Prague and General University Hospital in Prague   (Czech Republic)

Author keywords

Autophagy; Axonal spheroid; Axoplasmic transport; Lysosomal disease; Niemann Pick type C disease; Purkinje cell

Indexed keywords

4 AMINOBUTYRIC ACID; 4 AMINOBUTYRIC ACID RECEPTOR; PROTEASOME;

ALZHEIMER DISEASE; ATAXIA; BRAIN DYSFUNCTION; BRAIN NERVE CELL; CALCIUM HOMEOSTASIS; CONFERENCE PAPER; DENDRITE; ENDOPLASMIC RETICULUM STRESS; GM1 GANGLIOSIDOSIS; GM2 GANGLIOSIDOSIS; HUMAN; LYSOSOME; LYSOSOME STORAGE DISEASE; MUCOLIPIDOSIS; MUCOLIPIDOSIS TYPE 4; NERVE FIBER; NEUROAXONAL DYSTROPHY; NIEMANN PICK DISEASE; NONHUMAN; PHAGOCYTOSIS; PRIORITY JOURNAL; PURKINJE CELL; VESTIBULAR NUCLEUS;

ANIMALS; BRAIN; ENDOSOMES; HUMANS; LYSOSOMES; MICE; MICE, TRANSGENIC; NEUROAXONAL DYSTROPHIES; NEURONS; PROTEINS; PURKINJE CELLS; SIGNAL TRANSDUCTION;

EID: 78649752501     PISSN: 03005127     EISSN: 14708752     Source Type: Journal    
DOI: 10.1042/BST0381436     Document Type: Conference Paper

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