Phenotypic effects of Ehlers-Danlos syndrome-associated mutation on the FnIII domain of tenascin-X

Protein Science

Volumn 19, Issue 11, 2010, Pages 2231-2239

  Zhuang, Shulin ^a   Linhananta, Apichart ^b   Li, Hongbin ^a  

^a UNIVERSITY OF BRITISH COLUMBIA   (Canada)

^b LAKEHEAD UNIVERSITY   (Canada)

Author keywords

Ehlers Danlos syndrome; Mechanotransduction; Molecular dynamics simulations; Mutation; Single molecule force spectroscopy; Tenascin X

Indexed keywords

COLLAGEN; FIBRONECTIN; SCLEROPROTEIN; TENASCIN; TENASCIN X; UNCLASSIFIED DRUG;

ARTICLE; ATOMIC FORCE MICROSCOPY; EHLERS DANLOS SYNDROME; GENE MUTATION; HUMAN; MOLECULAR DYNAMICS; MOLECULAR MODEL; PATHOGENESIS; PHENOTYPE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN DOMAIN; PROTEIN PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN STRUCTURE; THERMODYNAMICS;

AMINO ACID SEQUENCE; CIRCULAR DICHROISM; EHLERS-DANLOS SYNDROME; HUMANS; MECHANOTRANSDUCTION, CELLULAR; MICROSCOPY, ATOMIC FORCE; MOLECULAR DYNAMICS SIMULATION; MOLECULAR SEQUENCE ANNOTATION; MOLECULAR SEQUENCE DATA; PHENOTYPE; PLIABILITY; POINT MUTATION; PROTEIN CONFORMATION; PROTEIN DENATURATION; PROTEIN ENGINEERING; PROTEIN INTERACTION MAPPING; PROTEIN STABILITY; PROTEIN STRUCTURE, TERTIARY; REPRODUCIBILITY OF RESULTS; TENASCIN;

EID: 78349240376     PISSN: 09618368     EISSN: 1469896X     Source Type: Journal    
DOI: 10.1002/pro.503     Document Type: Article

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