Altered expression and distribution of cathepsins in neuronopathic forms of Gaucher disease and in other sphingolipidoses

Human Molecular Genetics

Volumn 19, Issue 18, 2010, Pages 3583-3590

  Vitner, Einat B ^a   Dekel, Hani ^a   Zigdon, Hila ^a   Shachar, Tamar ^a   Farfel Becker, Tamar ^a   Eilam, Raya ^a   Karlsson, Stefan ^b   Futerman, Anthony H ^a  

^a WEIZMANN INSTITUTE OF SCIENCE   (Israel)

^b LUND UNIVERSITY   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

CATHEPSIN; CATHEPSIN B; CATHEPSIN F; CATHEPSIN H; CATHEPSIN K; CATHEPSIN L; IBUPROFEN; MESSENGER RNA;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; ASTROCYTOSIS; BRAIN CORTEX; CONTROLLED STUDY; DISEASE SEVERITY; ENZYME ACTIVITY; GAUCHER DISEASE; GLOBUS PALLIDUS; IMMUNOHISTOCHEMISTRY; LIPIDOSIS; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FOLDING; PROTEIN LOCALIZATION; THALAMUS; UPREGULATION; WESTERN BLOTTING;

ANIMALS; BRAIN; CATHEPSINS; DISEASE MODELS, ANIMAL; FEMALE; GAUCHER DISEASE; GENE EXPRESSION; HUMANS; MALE; MICE; MICE, KNOCKOUT; NEURONS; PROTEIN ISOFORMS; PROTEIN TRANSPORT; SPHINGOLIPIDOSES;

MUS;

EID: 77956131970     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq273     Document Type: Article

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