Gli3Xt-J/Xt-J mice exhibit lambdoid suture craniosynostosis which results from altered osteoprogenitor proliferation and differentiation

Human Molecular Genetics

Volumn 19, Issue 17, 2010, Pages 3457-3467

  Rice, David P C ^a,b,c   Connor, Elaine C ^b   Veltmaat, Jacqueline M ^d,e   Lana Elola, Eva ^b   Veistinen, Lotta ^a   Tanimoto, Yukiho ^a   Bellusci, Saverio ^d,f   Rice, Ritva ^b  

^a UNIVERSITY OF HELSINKI   (Finland)

^b KING'S COLLEGE LONDON   (United Kingdom)

^c HELSINKI UNIVERSITY CENTRAL HOSPITAL   (Finland)

^d CHILDREN S HOSPITAL LOS ANGELES   (United States)

^e INSTITUTE OF MOLECULAR AND CELL BIOLOGY   (Singapore)

^f JUSTUS LIEBIG UNIVERSITY   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

PROTEIN PATCHED 1; TRANSCRIPTION FACTOR GLI3; TRANSCRIPTION FACTOR RUNX2; TRANSCRIPTION FACTOR TWIST; GLI3 PROTEIN, MOUSE; KRUPPEL LIKE FACTOR; NERVE PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BONE DEVELOPMENT; CELL DIFFERENTIATION; CELL PROLIFERATION; CONNECTIVE TISSUE; CRANIOFACIAL MALFORMATION; CRANIOFACIAL SYNOSTOSIS; LAMBDOID SUTURE; MOUSE; NONHUMAN; OSTEOBLAST; PRIORITY JOURNAL; PROTEIN BINDING; PROTEIN EXPRESSION; SYNOSTOSIS; ANIMAL; C57BL MOUSE; CONGENITAL MALFORMATION; CYTOLOGY; DISEASE MODEL; FEMALE; GENE EXPRESSION REGULATION; GENETICS; HUMAN; MALE; METABOLISM; MOUSE MUTANT; PATHOPHYSIOLOGY; PRENATAL DEVELOPMENT; SKULL; STEM CELL;

ERINACEIDAE; MUS;

ANIMALS; CELL DIFFERENTIATION; CELL PROLIFERATION; CRANIOSYNOSTOSES; DISEASE MODELS, ANIMAL; FEMALE; GENE EXPRESSION REGULATION, DEVELOPMENTAL; HUMANS; KRUPPEL-LIKE TRANSCRIPTION FACTORS; MALE; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; NERVE TISSUE PROTEINS; OSTEOBLASTS; OSTEOGENESIS; SKULL; STEM CELLS;

EID: 77955435438     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddq258     Document Type: Article

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