Ion-abrasion scanning electron microscopy reveals distorted liver mitochondrial morphology in murine methylmalonic acidemia

Journal of Structural Biology

Volumn 171, Issue 2, 2010, Pages 125-132

  Murphy, Gavin E ^a   Lowekamp, Bradley C ^b   Zerfas, Patricia M ^c   Chandler, Randy J ^d,e   Narasimha, Rajesh ^a   Venditti, Charles P ^e   Subramaniam, Sriram ^a  

^a NATIONAL CANCER INSTITUTE   (United States)

^b NATIONAL INSTITUTES OF HEALTH   (United States)

^c NATIONAL INSTITUTES OF HEALTH   (United States)

^d GEORGE WASHINGTON UNIVERSITY   (United States)

^e NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

Author keywords

Diagnostic imaging; Focused ion beam; Ion abrasion; Methylmalonic acidemia; Mitochondria; Scanning electron microscopy

Indexed keywords

GALLIUM;

AGE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL SHAPE; CELL STRUCTURE; CELL VOLUME; CONTROLLED STUDY; DISEASE COURSE; GENE MUTATION; IMAGE ANALYSIS; IMAGE PROCESSING; ION ABRASION SCANNING ELECTRON MICROSCOPY; LIVER MITOCHONDRION; METHYLMALONIC ACIDEMIA; MOUSE; MUTANT; NONHUMAN; PRIORITY JOURNAL; SCANNING ELECTRON MICROSCOPY; WESTERN BLOTTING;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; BLOTTING, WESTERN; METHYLMALONIC ACID; MICE; MICROSCOPY, CONFOCAL; MICROSCOPY, ELECTRON, SCANNING; MITOCHONDRIA, LIVER; MODELS, BIOLOGICAL; OXIDATIVE PHOSPHORYLATION;

MURINAE;

EID: 77953720177     PISSN: 10478477     EISSN: 10958657     Source Type: Journal    
DOI: 10.1016/j.jsb.2010.04.005     Document Type: Article

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