Effect of gene dosage on single-cell hippocampal electrophysiology in a murine model of SSADH deficiency (γ-hydroxybutyric aciduria)

Epilepsy Research

Volumn 90, Issue 1-2, 2010, Pages 39-46

  Dósa, Zita ^a   Nieto Gonzalez, Jose Luis ^a   Korshoej, Anders Rosendal ^a   Gibson, Kenneth Michael ^c   Jensen, Kimmo ^a,b  

^a AARHUS UNIVERSITY   (Denmark)

^b AARHUS UNIVERSITY HOSPITAL   (Denmark)

^c MICHIGAN TECHNOLOGICAL UNIVERSITY   (United States)

Author keywords

Dentate gyrus; GABA; GABAA receptor; Granule cell; Interneuron; Mouse

Indexed keywords

4 AMINOBUTYRIC ACID; 4 AMINOBUTYRIC ACID A RECEPTOR; SUCCINATE SEMIALDEHYDE DEHYDROGENASE; 3 AMINO 2 (3 CARBOXYPROPYL) 6 (4 METHOXYPHENYL)PYRIDAZINIUM BROMIDE; 4 AMINOBUTYRIC ACID RECEPTOR BLOCKING AGENT; BIOCYTIN; LYSINE; PYRIDAZINE DERIVATIVE;

4 HYDROXYBUTYRIC ACIDURIA; ACIDURIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN ELECTROPHYSIOLOGY; CONTROLLED STUDY; DENTATE GYRUS; FEMALE; GABAERGIC TRANSMISSION; GENE DOSAGE; HETEROZYGOTE; HIPPOCAMPUS; KNOCKOUT MOUSE; MALE; MOUSE; NERVE CELL NETWORK; NONHUMAN; PRIORITY JOURNAL; SEIZURE; SYNAPTIC POTENTIAL; WILD TYPE; ANALOGS AND DERIVATIVES; ANIMAL; BIOPHYSICS; CLASSIFICATION; DEFICIENCY; DIAGNOSTIC USE; DISEASE MODEL; DOSE RESPONSE; DRUG EFFECTS; ELECTROSTIMULATION; GENETICS; HUMAN; IN VITRO STUDY; MEMBRANE POTENTIAL; METABOLISM; NERVE CELL; NEWBORN; PATCH CLAMP TECHNIQUE; PATHOLOGY; PATHOPHYSIOLOGY; PHYSIOLOGY; PROCEDURES; STATISTICAL MODEL;

ANIMALS; ANIMALS, NEWBORN; BIOPHYSICS; DISEASE MODELS, ANIMAL; DOSE-RESPONSE RELATIONSHIP, DRUG; ELECTRIC STIMULATION; FEMALE; GABA ANTAGONISTS; GAMMA-AMINOBUTYRIC ACID; GENE DOSAGE; HIPPOCAMPUS; HUMANS; LINEAR MODELS; LYSINE; MALE; MEMBRANE POTENTIALS; MICE; MICE, KNOCKOUT; NEURONS; PATCH-CLAMP TECHNIQUES; PYRIDAZINES; SEIZURES; SUCCINATE-SEMIALDEHYDE DEHYDROGENASE; IN VITRO TECHNIQUES;

EID: 77953536395     PISSN: 09201211     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.eplepsyres.2010.03.005     Document Type: Article

References (17)

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