Microfibrils: A cornerstone of extracellular matrix and a key to understand Marfan syndrome

Italian Journal of Anatomy and Embryology

Volumn 114, Issue 4, 2009, Pages 201-224

  Bonetti, Maria Ida ^a  

^a Section Enrico Aliara   (Italy)

Author keywords

Arterial wall; Elastic fibers; Fibrillin; Skin; Tgf

Indexed keywords

ACTIN BINDING PROTEIN; FIBRILLIN; TRANSFORMING GROWTH FACTOR BETA;

ANIMAL; ARTICLE; CONNECTIVE TISSUE; EXTRACELLULAR MATRIX; FIBER; GENETIC PREDISPOSITION; GENETICS; HUMAN; MARFAN SYNDROME; METABOLISM; MUTATION; PATHOLOGY; PATHOPHYSIOLOGY; SIGNAL TRANSDUCTION; ULTRASTRUCTURE;

ANIMALS; CONNECTIVE TISSUE; EXTRACELLULAR MATRIX; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MARFAN SYNDROME; MICROFIBRILS; MICROFILAMENT PROTEINS; MUTATION; SIGNAL TRANSDUCTION; TRANSFORMING GROWTH FACTOR BETA;

EID: 77953271373     PISSN: 11226714     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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