Abnormal extracellular matrix protein transport associated with increased apoptosis of vascular smooth muscle cells in Marfan syndrome and bicuspid aortic valve thoracic aortic aneurysm

Circulation

Volumn 108, Issue 10 SUPPL., 2003, Pages

  Nataatmadja, Maria ^b   West, Malcolm ^a   West, Jenny ^b   Summers, Kim ^b   Walker, Philip ^b   Nagata, Michio ^b   Watanabe, Teruo ^b  

^a UNIVERSITY OF QUEENSLAND   (Australia)

^b NONE

Author keywords

Aneurysm; Apoptosis; Congenital heart disease

Indexed keywords

FIBRILLIN; FIBRONECTIN; GELATINASE A; SCLEROPROTEIN; TENASCIN;

ADULT; AGED; AORTA ANEURYSM; AORTA ANOMALY; AORTA VALVE DISEASE; APOPTOSIS; ARTICLE; ASCENDING AORTA; CELL DEATH; CLINICAL ARTICLE; CONGENITAL HEART MALFORMATION; CONTROLLED STUDY; CULTURE MEDIUM; CYSTIC MEDIAL NECROSIS; DISEASE ASSOCIATION; ENZYME REGULATION; FBN1 GENE; FEMALE; GENE MUTATION; GENETIC ANALYSIS; GENETIC DISORDER; HISTOPATHOLOGY; HUMAN; IMMUNOHISTOCHEMISTRY; INCUBATION TIME; INFLAMMATION; MALE; MARFAN SYNDROME; PREMATURITY; PRIORITY JOURNAL; PROTEIN QUALITY; PROTEIN SECRETION; PROTEIN TRANSPORT; THORACIC AORTA; VASCULAR SMOOTH MUSCLE;

ADULT; AGED; AORTIC ANEURYSM, THORACIC; AORTIC VALVE; APOPTOSIS; BLOTTING, WESTERN; CELLS, CULTURED; EXTRACELLULAR MATRIX PROTEINS; FEMALE; FIBRONECTINS; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; MARFAN SYNDROME; MATRIX METALLOPROTEINASE 2; MICROFILAMENT PROTEINS; MIDDLE AGED; MUSCLE, SMOOTH, VASCULAR; PROTEIN TRANSPORT; TENASCIN;

EID: 0042416827     PISSN: 00097322     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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