Mechanistic similarities between cultured cell models of cystic fibrosis and Niemann-pick type C

American Journal of Respiratory Cell and Molecular Biology

Volumn 31, Issue 5, 2004, Pages 538-543

  White, Nicole M ^a   Corey, Deborah A ^a   Kelley, Thomas J ^a,b  

^a CASE WESTERN RESERVE UNIVERSITY   (United States)

^b CASE WESTERN RESERVE UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FILIPIN; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; INDUCIBLE NITRIC OXIDE SYNTHASE; MESSENGER RNA; NITRIC OXIDE SYNTHASE; RHOA GUANINE NUCLEOTIDE BINDING PROTEIN; SMAD3 PROTEIN; SPHINGOMYELIN PHOSPHODIESTERASE; STAT1 PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ARTICLE; CELL CULTURE; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; CYSTIC FIBROSIS; ENZYME ACTIVITY; ENZYME INDUCTION; FIBROBLAST; HUMAN; HUMAN CELL; MOUSE; NIEMANN PICK DISEASE; NONHUMAN; PHENOTYPE; PROTEIN EXPRESSION; PROTEIN FUNCTION;

ACTINS; ANIMALS; BLOTTING, WESTERN; CELLS, CULTURED; CHOLESTEROL; CYSTIC FIBROSIS; DISEASE MODELS, ANIMAL; EPITHELIAL CELLS; FIBROBLASTS; FILIPIN; HUMANS; MICE; MICE, TRANSGENIC; MUTATION, MISSENSE; NIEMANN-PICK DISEASES; NITRIC OXIDE SYNTHASE; NITRIC OXIDE SYNTHASE TYPE II; PHENOTYPE; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RHOA GTP-BINDING PROTEIN; RNA, MESSENGER; SIGNAL TRANSDUCTION; SPHINGOMYELIN PHOSPHODIESTERASE; TEMPERATURE;

ANIMALIA;

EID: 7744231974     PISSN: 10441549     EISSN: None     Source Type: Journal    
DOI: 10.1165/rcmb.2004-0117OC     Document Type: Article

References (31)

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