Neuropathological heterogeneity in frontotemporal lobar degeneration with TDP-43 proteinopathy: A quantitative study of 94 cases using principal components analysis

Journal of Neural Transmission

Volumn 117, Issue 2, 2010, Pages 227-239

  Armstrong, Richard A ^a   Ellis, William ^b   Hamilton, Ronald L ^c   MacKenzie, Ian R A ^d   Hedreen, John ^e   Gearing, Marla ^f   Montine, Thomas ^g   Vonsattel, Jean Paul ^h   Head, Elizabeth ⁱ   Lieberman, Andrew P ^j   Cairns, Nigel J ^k  

^a ASTON UNIVERSITY   (United Kingdom)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c UNIVERSITY OF PITTSBURGH SCHOOL OF MEDICINE   (United States)

^d VANCOUVER GENERAL HOSPITAL   (Canada)

^e MCLEAN HOSPITAL   (United States)

^f EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^g UNIVERSITY OF WASHINGTON   (United States)

^h Och Spine at New York Presbyterian Hospitals   (United States)

ⁱ UNIVERSITY OF CALIFORNIA   (United States)

^j UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

^k WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

more..

Author keywords

Frontotemporal lobar degeneration with TDP 43 proteinopathy; FTLD with ubiquitin positive inclusions; Neuronal cytoplasmic inclusions; Neuropathologic heterogeneity; Principal components analysis; TAR DNA binding protein of 43 kDa

Indexed keywords

PROGRANULIN; TAR DNA BINDING PROTEIN;

ADULT; AGED; ARTICLE; CELL DENSITY; CELL INCLUSION; CELL NUCLEUS INCLUSION BODY; CELL SURVIVAL; CELL VACUOLE; FEMALE; FRONTAL LOBE; FRONTOTEMPORAL DEMENTIA; GENE MUTATION; GENETIC HETEROGENEITY; HIPPOCAMPAL SCLEROSIS; HUMAN; IMMUNOREACTIVITY; MAJOR CLINICAL STUDY; MALE; MOTOR NEURON DISEASE; NEURITE; NEUROPATHOLOGY; OLIGODENDROGLIA; PHENOTYPE; PRINCIPAL COMPONENT ANALYSIS; PRIORITY JOURNAL; TEMPORAL LOBE;

ADULT; AGED; AGED, 80 AND OVER; BRAIN DISEASES; DNA-BINDING PROTEINS; FEMALE; FRONTAL LOBE; FRONTOTEMPORAL LOBAR DEGENERATION; HIPPOCAMPUS; HUMANS; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; MALE; MIDDLE AGED; MOTOR NEURON DISEASE; MUTATION; PRINCIPAL COMPONENT ANALYSIS; SCLEROSIS; TDP-43 PROTEINOPATHIES; TEMPORAL LOBE;

EID: 77249088114     PISSN: 03009564     EISSN: 14351463     Source Type: Journal    
DOI: 10.1007/s00702-009-0350-6     Document Type: Article

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