-
1
-
-
0034737602
-
Calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes
-
Alderton J.M. Steinhardt R.A. (2000) Calcium influx through calcium leak channels is responsible for the elevated levels of calcium-dependent proteolysis in dystrophic myotubes. J. Biol. Chem. 275, 9452 9460.
-
(2000)
J. Biol. Chem.
, vol.275
, pp. 9452-9460
-
-
Alderton, J.M.1
Steinhardt, R.A.2
-
3
-
-
0033970498
-
Eye muscle sparing by the muscular dystrophies: Lessons to be learned?
-
Andrade F.H., Porter J.D., Kaminski H.J. (2000) Eye muscle sparing by the muscular dystrophies: lessons to be learned? Micros. Res. Tec. 48, 192 203.
-
(2000)
Micros. Res. Tec.
, vol.48
, pp. 192-203
-
-
Andrade, F.H.1
Porter, J.D.2
Kaminski, H.J.3
-
4
-
-
25444500449
-
Calcineurin/NFAT signaling, together with GABP and PGC-1alpha, drives utrophin gene expression at the neuromuscular junction
-
Angus L.M., Chakkalakal J.V., Mejat A. et al. (2005) Calcineurin/NFAT signaling, together with GABP and PGC-1alpha, drives utrophin gene expression at the neuromuscular junction. Am. J. Physiol. Cell Physiol. 289, C908 C917.
-
(2005)
Am. J. Physiol. Cell Physiol.
, vol.289
-
-
Angus, L.M.1
Chakkalakal, J.V.2
Mejat, A.3
-
5
-
-
1842431755
-
Calsequestrin and the calcium release channel of skeletal and cardiac muscle
-
Beard N.A., Laver D.R., Dulhunty A.F. (2004) Calsequestrin and the calcium release channel of skeletal and cardiac muscle. Prog. Biophys. Mol. Biol. 85, 33 69.
-
(2004)
Prog. Biophys. Mol. Biol.
, vol.85
, pp. 33-69
-
-
Beard, N.A.1
Laver, D.R.2
Dulhunty, A.F.3
-
6
-
-
37849000464
-
Prevention of dystrophin-deficient cardiomyopathy in twenty-one-month-old carrier mice by mosaic dystrophin expression or complementary dystrophin/utrophin expression
-
Bostick B., Yue Y., Long C., Duan D. (2008) Prevention of dystrophin-deficient cardiomyopathy in twenty-one-month-old carrier mice by mosaic dystrophin expression or complementary dystrophin/utrophin expression. Circ. Res. 102, 121 130.
-
(2008)
Circ. Res.
, vol.102
, pp. 121-130
-
-
Bostick, B.1
Yue, Y.2
Long, C.3
Duan, D.4
-
7
-
-
0345731966
-
X chromosome-linked muscular dystrophy (mdx) in the mouse
-
Bulfield G., Siller W.G., Wigth P.A.L., Moore K.J.X. (1984) X chromosome-linked muscular dystrophy (mdx) in the mouse. Proc. Natl Acad. Sci. USA 81, 1189 1192. (Pubitemid 14171480)
-
(1984)
Proceedings of the National Academy of Sciences of the United States of America
, vol.81
, pp. 1189-1192
-
-
Bulfield, G.1
Siller, W.G.2
Wight, P.A.L.3
Moore, K.J.4
-
9
-
-
0034256090
-
Calmodulin: A prototypical calcium sensor
-
Chin D. Means A.R. (2000) Calmodulin: a prototypical calcium sensor. Trends Cell Biol. 10, 322 328.
-
(2000)
Trends Cell Biol.
, vol.10
, pp. 322-328
-
-
Chin, D.1
Means, A.R.2
-
10
-
-
0036092560
-
Drastic reduction of calsequestrin-like proteins and impaired calcium binding in dystrophic mdx muscle
-
Culligan K., Banville N., Dowling P., Ohlendieck K. (2002) Drastic reduction of calsequestrin-like proteins and impaired calcium binding in dystrophic mdx muscle. J. Appl. Physiol. 92, 435 445.
-
(2002)
J. Appl. Physiol.
, vol.92
, pp. 435-445
-
-
Culligan, K.1
Banville, N.2
Dowling, P.3
Ohlendieck, K.4
-
12
-
-
33646102225
-
Reduced expression of regucalcin in young and aged mdx diaphragm indicates abnormal cytosolic calcium handling in dystrophin-deficient muscle
-
Doran P., Dowling P., Donoghue P., Buffini M., Ohlendieck K. (2006) Reduced expression of regucalcin in young and aged mdx diaphragm indicates abnormal cytosolic calcium handling in dystrophin-deficient muscle. Biochem. Biophys. Acta 1764, 773 785.
-
(2006)
Biochem. Biophys. Acta
, vol.1764
, pp. 773-785
-
-
Doran, P.1
Dowling, P.2
Donoghue, P.3
Buffini, M.4
Ohlendieck, K.5
-
13
-
-
0038823857
-
Comparative analysis of Dp427-deficient mdx tissues shows that the milder dystrophic phenotype of extraocular and toe muscle fibres is associated with a persistent expression of β-dystroglycan
-
Dowling P., Lohan J., Ohlendieck K. (2003) Comparative analysis of Dp427-deficient mdx tissues shows that the milder dystrophic phenotype of extraocular and toe muscle fibres is associated with a persistent expression of β-dystroglycan. Eur. J. Cell Biol. 82, 222 230.
-
(2003)
Eur. J. Cell Biol.
, vol.82
, pp. 222-230
-
-
Dowling, P.1
Lohan, J.2
Ohlendieck, K.3
-
14
-
-
2342614190
-
Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa) - Deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy
-
Dowling P., Doran P., Ohlendieck K. (2004) Drastic reduction of sarcalumenin in Dp427 (dystrophin of 427 kDa) - deficient fibres indicates that abnormal calcium handling plays a key role in muscular dystrophy. Biochem. J. 379, 479 488.
-
(2004)
Biochem. J.
, vol.379
, pp. 479-488
-
-
Dowling, P.1
Doran, P.2
Ohlendieck, K.3
-
16
-
-
33846271135
-
Dystrophin, its interaction with other proteins, and implications for muscular dytrophy
-
Ervasti J.M. (2007) Dystrophin, its interaction with other proteins, and implications for muscular dytrophy. Biochem. Biophys. Acta 1772, 108 117.
-
(2007)
Biochem. Biophys. Acta
, vol.1772
, pp. 108-117
-
-
Ervasti, J.M.1
-
17
-
-
65949093523
-
Sarcoplasmic-endoplasmic-reticulum ca(2+)-atpase and calsequestrin are overexpressed in spared intrinsic laryngeal muscles of dystrophin-deficient mdx mice
-
Ferretti R., Marques M.J., Pertille A., Santo Neto H. (2009) Sarcoplasmic-endoplasmic-reticulum ca(2+)-atpase and calsequestrin are overexpressed in spared intrinsic laryngeal muscles of dystrophin-deficient mdx mice. Muscle Nerve 39, 609 615.
-
(2009)
Muscle Nerve
, vol.39
, pp. 609-615
-
-
Ferretti, R.1
Marques, M.J.2
Pertille, A.3
Santo Neto, H.4
-
18
-
-
0037020667
-
New aspects of calcium signaling in skeletal muscle cells: Implications in Duchenne muscular dystrophy
-
Gailly P. (2002) New aspects of calcium signaling in skeletal muscle cells: Implications in Duchenne muscular dystrophy. Biochem. Biophys. Acta 1600, 38 44.
-
(2002)
Biochem. Biophys. Acta
, vol.1600
, pp. 38-44
-
-
Gailly, P.1
-
19
-
-
45049087094
-
Towards developing standard operating procedures for pre-clinical testing in the mdx mouse model of Duchenne muscular dystrophy
-
Grounds M.D., Radley H.G., Lynch G.S., Nagaraju K., De Luca A. (2008) Towards developing standard operating procedures for pre-clinical testing in the mdx mouse model of Duchenne muscular dystrophy. Neurobiol. Dis. 31, 1 19.
-
(2008)
Neurobiol. Dis.
, vol.31
, pp. 1-19
-
-
Grounds, M.D.1
Radley, H.G.2
Lynch, G.S.3
Nagaraju, K.4
De Luca, A.5
-
20
-
-
32944472015
-
The influence of muscle type and dystrophin deficiency on murine expression profiles
-
Haslett J.N., Kang P.B., Han M. et al. (2005) The influence of muscle type and dystrophin deficiency on murine expression profiles. Mamm. Genome 16, 739 748.
-
(2005)
Mamm. Genome
, vol.16
, pp. 739-748
-
-
Haslett, J.N.1
Kang, P.B.2
Han, M.3
-
21
-
-
0023614188
-
Dystrophin: The protein product of the Duchenne muscular dystrophy locus
-
Hoffman E.P., Brown Jr. R.H., Kunkel L.M. (1987) Dystrophin: the protein product of the Duchenne muscular dystrophy locus. Cell 51, 919 928.
-
(1987)
Cell
, vol.51
, pp. 919-928
-
-
Hoffman, E.P.1
Brown Jr., R.H.2
Kunkel, L.M.3
-
22
-
-
0025932274
-
Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle
-
Khurana T.S., Watkins S.C., Chafey P. et al. (1991) Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle. Neuromuscul. Disord. 1, 185 194.
-
(1991)
Neuromuscul. Disord.
, vol.1
, pp. 185-194
-
-
Khurana, T.S.1
Watkins, S.C.2
Chafey, P.3
-
23
-
-
0029143830
-
Absence of extraocular muscle pathology in Duchenne's muscular dystrophy: Role for calcium homeostasis in extraocular muscle sparing
-
Khurana T.S., Predergast R.A., Alameddine H.S. et al. (1995) Absence of extraocular muscle pathology in Duchenne's muscular dystrophy: role for calcium homeostasis in extraocular muscle sparing. J. Exp. Med. 182, 467 474.
-
(1995)
J. Exp. Med.
, vol.182
, pp. 467-474
-
-
Khurana, T.S.1
Predergast, R.A.2
Alameddine, H.S.3
-
24
-
-
0026323638
-
Structure and function of the neuromuscular junction in young adult mdx mice
-
Lyons P.R. Slater C.R. (1991) Structure and function of the neuromuscular junction in young adult mdx mice. J. Neurocytol. 20, 969 981.
-
(1991)
J. Neurocytol.
, vol.20
, pp. 969-981
-
-
Lyons, P.R.1
Slater, C.R.2
-
25
-
-
33847684752
-
Intrinsic laryngeal muscles are spared from myonecrosis in the mdx mouse model of Duchenne muscular dystrophy
-
Marques M.J., Ferretti R., Vomero V.U., Minatel E., Santo Neto H. (2007a) Intrinsic laryngeal muscles are spared from myonecrosis in the mdx mouse model of Duchenne muscular dystrophy. Muscle Nerve 35, 349 353.
-
(2007)
Muscle Nerve
, vol.35
, pp. 349-353
-
-
Marques, M.J.1
Ferretti, R.2
Vomero, V.U.3
Minatel, E.4
Santo Neto, H.5
-
26
-
-
34547402504
-
Acetylcholine receptor organization at the dystrophic extraocular muscle neuromuscular junction
-
Marques M.J., Pertille A., Carvalho C.L.T., Santo Neto H. (2007b) Acetylcholine receptor organization at the dystrophic extraocular muscle neuromuscular junction. Anat. Rec. 290, 846 854.
-
(2007)
Anat. Rec.
, vol.290
, pp. 846-854
-
-
Marques, M.J.1
Pertille, A.2
Carvalho, C.L.T.3
Santo Neto, H.4
-
27
-
-
0026621608
-
Association of dystrophin-related protein with dystrophin associated proteins in mdx mouse muscle
-
Matsumura K., Ervasti J.M., Ohlendieck K., Kahl S.D., Campbell K.P. (1992) Association of dystrophin-related protein with dystrophin associated proteins in mdx mouse muscle. Nature 360, 588 591.
-
(1992)
Nature
, vol.360
, pp. 588-591
-
-
Matsumura, K.1
Ervasti, J.M.2
Ohlendieck, K.3
Kahl, S.D.4
Campbell, K.P.5
-
28
-
-
60549115816
-
Diltiazem and verapamil protect dystrophin-deficient muscle fibers of mdx mice from degeneration: A potential role in calcium buffering and sarcolemmal stability
-
Matsumura C.Y., Albuquerque T.C.P., Pertille A., Santo Neto H., Marques M.J. (2009) Diltiazem and verapamil protect dystrophin-deficient muscle fibers of mdx mice from degeneration: a potential role in calcium buffering and sarcolemmal stability. Muscle Nerve 39, 167 176.
-
(2009)
Muscle Nerve
, vol.39
, pp. 167-176
-
-
Matsumura, C.Y.1
Albuquerque, T.C.P.2
Pertille, A.3
Santo Neto, H.4
Marques, M.J.5
-
29
-
-
0028027749
-
Time course of changes in plasma membrane permeability in the dystrophin-deficient mdx mouse
-
McArdle A., Edwards R.H., Jackson M.J. (1994) Time course of changes in plasma membrane permeability in the dystrophin-deficient mdx mouse. Muscle Nerve 17, 1378 1384.
-
(1994)
Muscle Nerve
, vol.17
, pp. 1378-1384
-
-
McArdle, A.1
Edwards, R.H.2
Jackson, M.J.3
-
30
-
-
0027460658
-
Dystrophin protects the sarcolemma from stresses developed during muscle contraction
-
Petrof B.J., Shrager J.B., Stedman H.H., Kelly A.M., Sweeney H.L. (1993) Dystrophin protects the sarcolemma from stresses developed during muscle contraction. Proc. Natl Acad. Sci. USA 90, 3710 3714.
-
(1993)
Proc. Natl Acad. Sci. USA
, vol.90
, pp. 3710-3714
-
-
Petrof, B.J.1
Shrager, J.B.2
Stedman, H.H.3
Kelly, A.M.4
Sweeney, H.L.5
-
31
-
-
0029997931
-
Muscles of a different color: The unusual properties of the extraocular muscles may predispose or protect them in neurogenic and myogenic disease
-
Porter J.D. Baker R.S. (1996) Muscles of a different color: the unusual properties of the extraocular muscles may predispose or protect them in neurogenic and myogenic disease. Neurology 46, 30 37.
-
(1996)
Neurology
, vol.46
, pp. 30-37
-
-
Porter, J.D.1
Baker, R.S.2
-
32
-
-
0028999265
-
Extraocular muscles: Basic and clinical aspects of structure and function
-
Porter J.D., Baker R.S., Ragusa R.J., Brueckner J.K. (1995) Extraocular muscles: basic and clinical aspects of structure and function. Surv. Ophthalmol. 39, 451 484.
-
(1995)
Surv. Ophthalmol.
, vol.39
, pp. 451-484
-
-
Porter, J.D.1
Baker, R.S.2
Ragusa, R.J.3
Brueckner, J.K.4
-
33
-
-
0031824850
-
The sparing of extraocular muscle is lost in mice lacking utrophin and dystrophin
-
Porter J.D., Rafael J.A., Ragusa R.J., Brueckner J.K., Trickett J.I., Davies K.E. (1998) The sparing of extraocular muscle is lost in mice lacking utrophin and dystrophin. J. Cell Sci. 111, 1801 1811.
-
(1998)
J. Cell Sci.
, vol.111
, pp. 1801-1811
-
-
Porter, J.D.1
Rafael, J.A.2
Ragusa, R.J.3
Brueckner, J.K.4
Trickett, J.I.5
Davies, K.E.6
-
34
-
-
4344658776
-
Evolution of the mdx mouse cardiomyopathy: Physiological and morphological findings
-
Quinlan J.G., Hahn H.S., Wong B.L., Lorenz J.N., Wenisch A.S., Levin L.S. (2004) Evolution of the mdx mouse cardiomyopathy: physiological and morphological findings. Neuromuscul. Disor. 14, 491 496.
-
(2004)
Neuromuscul. Disor.
, vol.14
, pp. 491-496
-
-
Quinlan, J.G.1
Hahn, H.S.2
Wong, B.L.3
Lorenz, J.N.4
Wenisch, A.S.5
Levin, L.S.6
-
35
-
-
0035190381
-
The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies
-
Rando T.A. (2001) The dystrophin-glycoprotein complex, cellular signaling, and the regulation of cell survival in the muscular dystrophies. Muscle Nerve 24, 1575 1594.
-
(2001)
Muscle Nerve
, vol.24
, pp. 1575-1594
-
-
Rando, T.A.1
-
36
-
-
33744955800
-
Sarcoplasmic reticulum: The dynamic calcium governor of muscle
-
Rossi A.E. Dirksen R.T. (2006) Sarcoplasmic reticulum: the dynamic calcium governor of muscle. Muscle Nerve 33, 715 731.
-
(2006)
Muscle Nerve
, vol.33
, pp. 715-731
-
-
Rossi, A.E.1
Dirksen, R.T.2
-
37
-
-
0024353559
-
The molecular basis of muscular dystrophy in the mdx mouse: A point mutation
-
Sicinski Y.G., Ryder-Cook A.S., Barnard E.A., Darlison M.G., Barnard P.J. (1989) The molecular basis of muscular dystrophy in the mdx mouse: a point mutation. Science 244, 1578 1580.
-
(1989)
Science
, vol.244
, pp. 1578-1580
-
-
Sicinski, Y.G.1
Ryder-Cook, A.S.2
Barnard, E.A.3
Darlison, M.G.4
Barnard, P.J.5
-
38
-
-
43449105011
-
Dystrophin-deficient cardiomyopathy in mouse: Expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart
-
Spurney C.F., Knoblach S., Pistilli E.E., Nagaraju K., Martin G.R., Hoffman E.P. (2008) Dystrophin-deficient cardiomyopathy in mouse: expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart. Neuromuscul. Disor. 18, 371 381.
-
(2008)
Neuromuscul. Disor.
, vol.18
, pp. 371-381
-
-
Spurney, C.F.1
Knoblach, S.2
Pistilli, E.E.3
Nagaraju, K.4
Martin, G.R.5
Hoffman, E.P.6
-
39
-
-
0026419948
-
The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy
-
Stedman H.H., Sweeney H.L., Shrager J.B. et al. (1991) The mdx mouse diaphragm reproduces the degenerative changes of Duchenne muscular dystrophy. Nature 352, 536 539.
-
(1991)
Nature
, vol.352
, pp. 536-539
-
-
Stedman, H.H.1
Sweeney, H.L.2
Shrager, J.B.3
-
40
-
-
33646202742
-
Differential calcineurin signaling activity and regeneration efficacy in diaphragm and limb muscles of dystrophic mice
-
Stupka N., Michell B.J., Kemp B.E., Lynch G.S. (2006) Differential calcineurin signaling activity and regeneration efficacy in diaphragm and limb muscles of dystrophic mice. Neuromuscul. Disor. 16, 337 346.
-
(2006)
Neuromuscul. Disor.
, vol.16
, pp. 337-346
-
-
Stupka, N.1
Michell, B.J.2
Kemp, B.E.3
Lynch, G.S.4
-
42
-
-
0023091942
-
The mutant mdx: Inherited myopathy in the mouse. Morphological studies of nerves, muscle and end-plates.
-
Torres L.F. Duchen L.W. (1987) The mutant mdx: inherited myopathy in the mouse. Morphological studies of nerves, muscle and end-plates. Brain 110, 269 299.
-
(1987)
Brain
, vol.110
, pp. 269-299
-
-
Torres, L.F.1
Duchen, L.W.2
-
43
-
-
25444520238
-
Muscle regeneration in dystrophin-deficient mdx mice studied by gene expression profiling
-
Turk R., Sterrenburg E., de Meijer E.J., van Ommen G.-J.B., den Dunnen J.T., Hoen P.A.C. (2005) Muscle regeneration in dystrophin-deficient mdx mice studied by gene expression profiling. BMC Genomics 6, 98 112.
-
(2005)
BMC Genomics
, vol.6
, pp. 98-112
-
-
Turk, R.1
Sterrenburg, E.2
De Meijer, E.J.3
Van Ommen, G.-J.B.4
Den Dunnen, J.T.5
Hoen, P.A.C.6
-
44
-
-
33846839006
-
Regulation of capacitative calcium entries by α1-syntrophin: association of TRPC1 with dystrophin complex and the PDZ domain of α1-syntrophin
-
Vandebrouck A., Sabourin J., Rivet J. et al. (2007) Regulation of capacitative calcium entries by α1-syntrophin:association of TRPC1 with dystrophin complex and the PDZ domain of α1-syntrophin. FASEB J. 21, 608 617.
-
(2007)
FASEB J.
, vol.21
, pp. 608-617
-
-
Vandebrouck, A.1
Sabourin, J.2
Rivet, J.3
-
45
-
-
24044503385
-
L-arginine improves dystrophic phenotype in mdx mice
-
Voisin V., Sébrié C., Matecki S. et al. (2005) L-arginine improves dystrophic phenotype in mdx mice. Neurobiol. Dis. 20, 123 130.
-
(2005)
Neurobiol. Dis.
, vol.20
, pp. 123-130
-
-
Voisin, V.1
Sébrié, C.2
Matecki, S.3
-
46
-
-
33745168598
-
Muscle damage in mdx (dystrophic) mice: Role of calcium and reactive oxygen species
-
Whitehead N.P., Yeung E.W., Allen D.G. (2006) Muscle damage in mdx (dystrophic) mice: role of calcium and reactive oxygen species. Clin. Exp. Pharmacol. Physiol. 33, 657 662.
-
(2006)
Clin. Exp. Pharmacol. Physiol.
, vol.33
, pp. 657-662
-
-
Whitehead, N.P.1
Yeung, E.W.2
Allen, D.G.3
|