Animal models for glutaryl-CoA dehydrogenase deficiency

Journal of Inherited Metabolic Disease

Volumn 27, Issue 6, 2004, Pages 813-818

  Koeller, D M ^a   Sauer, S ^b   Wajner, M ^c,d   De Mello, C F ^e   Goodman, S I ^f   Woontner, M ^f   Muhlhausen C ^g   Okun, J G ^b   Kolker S ^b  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

^b UNIVERSITY HOSPITAL HEIDELBERG   (Germany)

^c FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^d HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^e University of Santa Maria   (Brazil)

^f UNIVERSITY OF COLORADO   (United States)

^g UNIVERSITY MEDICAL CENTER HAMBURG EPPENDORF   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

BRAIN ENZYME; CYTOKINE; GLUTARYL COENZYME A DEHYDROGENASE; KIDNEY ENZYME; LIVER ENZYME; MYELIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BAT; BRAIN SPONGIOSIS; CATABOLISM; CONTROLLED STUDY; CORPUS STRIATUM; CYTOKINE PRODUCTION; DEMYELINATION; DYSTONIA; EMBRYO; ENZYME ACTIVITY; ENZYME DEFICIENCY; GENE TARGETING; IN VIVO STUDY; MOUSE; NERVE CELL NECROSIS; NERVOUS SYSTEM INFLAMMATION; NEUROMODULATION; NEUROPROTECTION; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; SPECIES DIFFERENCE; STEM CELL;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; CHIROPTERA; DISEASE MODELS, ANIMAL; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; INJECTIONS; MICE; MICE, KNOCKOUT; NEOSTRIATUM; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS;

EID: 7244234276     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/B:BOLI.0000045763.52907.5e     Document Type: Article

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