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Volumn 30, Issue 5, 2009, Pages 579-586

Nutrition in cystic fibrosis

Author keywords

CFTR; Cystic fibrosis; Gastrointestinal; Malabsorption; Nutrition; Pancreatic insufficiency

Indexed keywords

GLUCOSE; PANCREAS ENZYME; PROTEIN; TRACE ELEMENT; TRANSMEMBRANE CONDUCTANCE REGULATOR;

EID: 70350445912     PISSN: 10693424     EISSN: 10989048     Source Type: Journal    
DOI: 10.1055/s-0029-1238916     Document Type: Review
Times cited : (63)

References (69)
  • 1
  • 3
    • 0024824522 scopus 로고
    • The pathophysiology of the pancreatic defect in cystic fibrosis
    • Durie P R. The pathophysiology of the pancreatic defect in cystic fibrosis. Acta Paediatr Scand Suppl 1989 363 41-44
    • (1989) Acta Paediatr Scand Suppl , vol.363 , pp. 41-44
    • Durie, P.R.1
  • 4
    • 30944452334 scopus 로고    scopus 로고
    • Diagnosis and treatment of intestinal malabsorption in cystic fibrosis
    • Littlewood J M., Wolfe S P., Conway S P. Diagnosis and treatment of intestinal malabsorption in cystic fibrosis. Pediatr Pulmonol 2006 41 35-49
    • (2006) Pediatr Pulmonol , vol.41 , pp. 35-49
    • Littlewood, J.M.1    Wolfe, S.P.2    Conway, S.P.3
  • 5
    • 0025013283 scopus 로고
    • Duodenal pH in cystic fibrosis and its relationship to fat malabsorption
    • Robinson P J., Smith A L., Sly P D. Duodenal pH in cystic fibrosis and its relationship to fat malabsorption. Dig Dis Sci 1990 35 1299-1304
    • (1990) Dig Dis Sci , vol.35 , pp. 1299-1304
    • Robinson, P.J.1    Smith, A.L.2    Sly, P.D.3
  • 6
    • 39849106615 scopus 로고    scopus 로고
    • The changing face of the exocrine pancreas in cystic fibrosis: Pancreatic sufficiency, pancreatitis and genotype
    • Walkowiak J, Lisowska A, Blaszczysski M. The changing face of the exocrine pancreas in cystic fibrosis: pancreatic sufficiency, pancreatitis and genotype. Eur J Gastroenterol Hepatol 2008 20 157-160
    • (2008) Eur J Gastroenterol Hepatol , vol.20 , pp. 157-160
    • Walkowiak, J.1    Lisowska, A.2    Blaszczysski, M.3
  • 8
    • 0031950258 scopus 로고    scopus 로고
    • Risk of death in cystic fibrosis patients with severely compromised lung function
    • Milla C E., Warwick W J. Risk of death in cystic fibrosis patients with severely compromised lung function. Chest 1998 113 1230-1234
    • (1998) Chest , vol.113 , pp. 1230-1234
    • Milla, C.E.1    Warwick, W.J.2
  • 9
  • 10
    • 0029850934 scopus 로고    scopus 로고
    • Long-term survival and nutritional data in patients with cystic fibrosis treated in a Danish centre
    • Nir M, Lanng S, Johansen H K., Koch C. Long-term survival and nutritional data in patients with cystic fibrosis treated in a Danish centre. Thorax 1996 51 1023-1027
    • (1996) Thorax , vol.51 , pp. 1023-1027
    • Nir, M.1    Lanng, S.2    Johansen, H.K.3    Koch, C.4
  • 11
    • 0023923679 scopus 로고
    • A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto
    • Corey M, McLaughlin F J., Williams M, Levison H. A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto. J Clin Epidemiol 1988 41 583-591
    • (1988) J Clin Epidemiol , vol.41 , pp. 583-591
    • Corey, M.1    McLaughlin, F.J.2    Williams, M.3    Levison, H.4
  • 12
    • 0032965421 scopus 로고    scopus 로고
    • Comparison of growth status of patients with cystic fibrosis between the United States and Canada
    • Lai H C., Corey M, FitzSimmons S, Kosorok M R., Farrell P M. Comparison of growth status of patients with cystic fibrosis between the United States and Canada. Am J Clin Nutr 1999 69 531-538
    • (1999) Am J Clin Nutr , vol.69 , pp. 531-538
    • Lai, H.C.1    Corey, M.2    Fitzsimmons, S.3    Kosorok, M.R.4    Farrell, P.M.5
  • 13
    • 0035321043 scopus 로고    scopus 로고
    • Stature as a prognostic factor in cystic fibrosis survival
    • Beker L T., Russek-Cohen E, Fink R J. Stature as a prognostic factor in cystic fibrosis survival. J Am Diet Assoc 2001 101 438-442
    • (2001) J Am Diet Assoc , vol.101 , pp. 438-442
    • Beker, L.T.1    Russek-Cohen, E.2    Fink, R.J.3
  • 15
    • 34247497756 scopus 로고    scopus 로고
    • Nutrition and lung disease in cystic fibrosis
    • Milla C. Nutrition and lung disease in cystic fibrosis. Clin Chest Med 2007 28 319-330
    • (2007) Clin Chest Med , vol.28 , pp. 319-330
    • Milla, C.1
  • 18
    • 0027525146 scopus 로고
    • Tumour necrosis factor-alpha, resting energy expenditure and cachexia in cystic fibrosis
    • Elborn J S., Cordon S M., Western P J., Macdonald I A., Shale D J. Tumour necrosis factor-alpha, resting energy expenditure and cachexia in cystic fibrosis. Clin Sci (Lond) 1993 85 563-568
    • (1993) Clin Sci (Lond) , vol.85 , pp. 563-568
    • Elborn, J.S.1    Cordon, S.M.2    Western, P.J.3    MacDonald, I.A.4    Shale, D.J.5
  • 19
    • 0030023479 scopus 로고    scopus 로고
    • Resting energy expenditure and oxygen cost of breathing in patients with cystic fibrosis
    • Bell S C., Saunders M J., Elborn J S., Shale D J. Resting energy expenditure and oxygen cost of breathing in patients with cystic fibrosis. Thorax 1996 51 126-131
    • (1996) Thorax , vol.51 , pp. 126-131
    • Bell, S.C.1    Saunders, M.J.2    Elborn, J.S.3    Shale, D.J.4
  • 20
    • 0032190336 scopus 로고    scopus 로고
    • Nutrition and cystic fibrosis
    • Wilson D C., Pencharz P B. Nutrition and cystic fibrosis. Nutrition 1998 14 792-795
    • (1998) Nutrition , vol.14 , pp. 792-795
    • Wilson, D.C.1    Pencharz, P.B.2
  • 22
    • 0030768159 scopus 로고    scopus 로고
    • Lower airway inflammation in infants and young children with cystic fibrosis
    • Armstrong D S., Grimwood K, Carlin J B. et al. Lower airway inflammation in infants and young children with cystic fibrosis. Am J Respir Crit Care Med 1997 156 (4 Pt 1) 1197-1204
    • (1997) Am J Respir Crit Care Med , vol.156 , Issue.PART 1 , pp. 1197-1204
    • Armstrong, D.S.1    Grimwood, K.2    Carlin, J.B.3
  • 23
    • 67650712233 scopus 로고    scopus 로고
    • Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening
    • Sly P D., Brennan S, Gangell C et al. Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening. Am J Respir Crit Care Med 2009 180 146-152
    • (2009) Am J Respir Crit Care Med , vol.180 , pp. 146-152
    • Sly, P.D.1    Brennan, S.2    Gangell, C.3
  • 27
    • 0030391747 scopus 로고    scopus 로고
    • Resting energy expenditure, pulmonary inflammation, and genotype in the early course of cystic fibrosis
    • Thomson M A., Wilmott R W., Wainwright C, Masters B, Francis P J., Shepherd R W. Resting energy expenditure, pulmonary inflammation, and genotype in the early course of cystic fibrosis. J Pediatr 1996 129 367-373
    • (1996) J Pediatr , vol.129 , pp. 367-373
    • Thomson, M.A.1    Wilmott, R.W.2    Wainwright, C.3    Masters, B.4    Francis, P.J.5    Shepherd, R.W.6
  • 28
  • 29
    • 0018390987 scopus 로고
    • Mitochondrial calcium uptake and oxygen consumption in cystic fibrosis
    • Feigal R J., Shapiro B L. Mitochondrial calcium uptake and oxygen consumption in cystic fibrosis. Nature 1979 278 276-277
    • (1979) Nature , vol.278 , pp. 276-277
    • Feigal, R.J.1    Shapiro, B.L.2
  • 30
    • 0027516249 scopus 로고
    • Regulation of CFTR Cl- conductance in secretion by cellular energy levels
    • Bell C L., Quinton P M. Regulation of CFTR Cl- conductance in secretion by cellular energy levels. Am J Physiol 1993 264 (4 Pt 1) C925-C931
    • (1993) Am J Physiol , vol.264 , Issue.PART 1
    • Bell, C.L.1    Quinton, P.M.2
  • 31
    • 0028859688 scopus 로고
    • Normal energy expenditure in the infant with presymptomatic cystic fibrosis
    • Bronstein M N., Davies P S., Hambidge K M., Accurso F J. Normal energy expenditure in the infant with presymptomatic cystic fibrosis. J Pediatr 1995 126 28-33
    • (1995) J Pediatr , vol.126 , pp. 28-33
    • Bronstein, M.N.1    Davies, P.S.2    Hambidge, K.M.3    Accurso, F.J.4
  • 34
    • 0033827478 scopus 로고    scopus 로고
    • Longitudinal relationship among growth, nutritional status, and pulmonary function in children with cystic fibrosis: Analysis of the Cystic Fibrosis Foundation National CF Patient Registry
    • Zemel B S., Jawad A F., FitzSimmons S, Stallings V A. Longitudinal relationship among growth, nutritional status, and pulmonary function in children with cystic fibrosis: analysis of the Cystic Fibrosis Foundation National CF Patient Registry. J Pediatr 2000 137 374-380
    • (2000) J Pediatr , vol.137 , pp. 374-380
    • Zemel, B.S.1    Jawad, A.F.2    Fitzsimmons, S.3    Stallings, V.A.4
  • 35
    • 0029833357 scopus 로고    scopus 로고
    • Nutrition and survival in cystic fibrosis
    • Elborn J S., Bell S C. Nutrition and survival in cystic fibrosis. Thorax 1996 51 971-972
    • (1996) Thorax , vol.51 , pp. 971-972
    • Elborn, J.S.1    Bell, S.C.2
  • 37
    • 66749174619 scopus 로고    scopus 로고
    • Growth and long-term lung function in cystic fibrosis: A longitudinal study of patients diagnosed by neonatal screening
    • Assael B M., Casazza G, Iansa P, Volpi S, Milani S. Growth and long-term lung function in cystic fibrosis: a longitudinal study of patients diagnosed by neonatal screening. Pediatr Pulmonol 2009 44 209-215
    • (2009) Pediatr Pulmonol , vol.44 , pp. 209-215
    • Assael, B.M.1    Casazza, G.2    Iansa, P.3    Volpi, S.4    Milani, S.5
  • 38
    • 0029101397 scopus 로고
    • Nutritional growth retardation is associated with defective lung growth in cystic fibrosis: A preventable determinant of progressive pulmonary dysfunction
    • Thomson M A., Quirk P, Swanson C E. et al. Nutritional growth retardation is associated with defective lung growth in cystic fibrosis: a preventable determinant of progressive pulmonary dysfunction. Nutrition 1995 11 350-354
    • (1995) Nutrition , vol.11 , pp. 350-354
    • Thomson, M.A.1    Quirk, P.2    Swanson, C.E.3
  • 40
    • 0033044371 scopus 로고    scopus 로고
    • Bone mineral content and body composition in children and young adults with cystic fibrosis
    • Henderson R C., Madsen C D. Bone mineral content and body composition in children and young adults with cystic fibrosis. Pediatr Pulmonol 1999 27 80-84
    • (1999) Pediatr Pulmonol , vol.27 , pp. 80-84
    • Henderson, R.C.1    Madsen, C.D.2
  • 41
    • 0027412961 scopus 로고
    • Bio-electrical impedance analysis for estimation of fat-free mass and muscle mass in cystic fibrosis patients
    • Spicher V, Roulet M, Schaffner C, Schutz Y. Bio-electrical impedance analysis for estimation of fat-free mass and muscle mass in cystic fibrosis patients. Eur J Pediatr 1993 152 222-225
    • (1993) Eur J Pediatr , vol.152 , pp. 222-225
    • Spicher, V.1    Roulet, M.2    Schaffner, C.3    Schutz, Y.4
  • 42
    • 0028054770 scopus 로고
    • Body composition of children with cystic fibrosis with mild clinical manifestations compared with normal children
    • Tomezsko J L., Scanlin T F., Stallings V A. Body composition of children with cystic fibrosis with mild clinical manifestations compared with normal children. Am J Clin Nutr 1994 59 123-128
    • (1994) Am J Clin Nutr , vol.59 , pp. 123-128
    • Tomezsko, J.L.1    Scanlin, T.F.2    Stallings, V.A.3
  • 43
    • 0032079627 scopus 로고    scopus 로고
    • Assessment of body composition of children with cystic fibrosis (CF)
    • Allen J R., Humphries I R., McCauley J C. et al. Assessment of body composition of children with cystic fibrosis (CF). Appl Radiat Isot 1998 49 591-592
    • (1998) Appl Radiat Isot , vol.49 , pp. 591-592
    • Allen, J.R.1    Humphries, I.R.2    McCauley, J.C.3
  • 44
    • 0029785305 scopus 로고    scopus 로고
    • Prospective evaluation of resting energy expenditure, nutritional status, pulmonary function, and genotype in children with cystic fibrosis
    • Zemel B S., Kawchak D A., Cnaan A, Zhao H, Scanlin T F., Stallings V A. Prospective evaluation of resting energy expenditure, nutritional status, pulmonary function, and genotype in children with cystic fibrosis. Pediatr Res 1996 40 578-586
    • (1996) Pediatr Res , vol.40 , pp. 578-586
    • Zemel, B.S.1    Kawchak, D.A.2    Cnaan, A.3    Zhao, H.4    Scanlin, T.F.5    Stallings, V.A.6
  • 46
    • 0021815052 scopus 로고
    • Whole body protein turnover in malnourished cystic fibrosis patients and its relationship to pulmonary disease
    • Holt T L., Ward L C., Francis P J., Isles A, Cooksley W G., Shepherd R W. Whole body protein turnover in malnourished cystic fibrosis patients and its relationship to pulmonary disease. Am J Clin Nutr 1985 41 1061-1066
    • (1985) Am J Clin Nutr , vol.41 , pp. 1061-1066
    • Holt, T.L.1    Ward, L.C.2    Francis, P.J.3    Isles, A.4    Cooksley, W.G.5    Shepherd, R.W.6
  • 47
    • 0020267606 scopus 로고
    • Altered body composition and muscle protein degradation in nutritionally growth-retarded children with cystic fibrosis
    • Miller M, Ward L, Thomas B J., Cooksley W G., Shepherd R W. Altered body composition and muscle protein degradation in nutritionally growth-retarded children with cystic fibrosis. Am J Clin Nutr 1982 36 492-499
    • (1982) Am J Clin Nutr , vol.36 , pp. 492-499
    • Miller, M.1    Ward, L.2    Thomas, B.J.3    Cooksley, W.G.4    Shepherd, R.W.5
  • 48
    • 0022995617 scopus 로고
    • Nutritional rehabilitation in cystic fibrosis: Controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease
    • Shepherd R W., Holt T L., Thomas B J. et al. Nutritional rehabilitation in cystic fibrosis: controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease. J Pediatr 1986 109 788-794
    • (1986) J Pediatr , vol.109 , pp. 788-794
    • Shepherd, R.W.1    Holt, T.L.2    Thomas, B.J.3
  • 51
    • 0022384572 scopus 로고
    • Maximal inspiratory and expiratory pressures are reduced in hyperinflated, malnourished, young adult male patients with cystic fibrosis
    • Szeinberg A, England S, Mindorff C, Fraser I M., Levison H. Maximal inspiratory and expiratory pressures are reduced in hyperinflated, malnourished, young adult male patients with cystic fibrosis. Am Rev Respir Dis 1985 132 766-769
    • (1985) Am Rev Respir Dis , vol.132 , pp. 766-769
    • Szeinberg, A.1    England, S.2    Mindorff, C.3    Fraser, I.M.4    Levison, H.5
  • 52
    • 0025194596 scopus 로고
    • The effects of nutritional status and hyperinflation on respiratory muscle strength in children and young adults
    • Lands L, Desmond K J., Demizio D, Pavilanis A, Coates A L. The effects of nutritional status and hyperinflation on respiratory muscle strength in children and young adults. Am Rev Respir Dis 1990 141 1506-1509
    • (1990) Am Rev Respir Dis , vol.141 , pp. 1506-1509
    • Lands, L.1    Desmond, K.J.2    Demizio, D.3    Pavilanis, A.4    Coates, A.L.5
  • 53
    • 0027465362 scopus 로고
    • Relationships among nutritional status and skeletal and respiratory muscle function in cystic fibrosis: Does early dietary supplementation make a difference?
    • Hanning R M., Blimkie C J., Bar-Or O, Lands L C., Moss L A., Wilson W M. Relationships among nutritional status and skeletal and respiratory muscle function in cystic fibrosis: does early dietary supplementation make a difference? Am J Clin Nutr 1993 57 580-587
    • (1993) Am J Clin Nutr , vol.57 , pp. 580-587
    • Hanning, R.M.1    Blimkie, C.J.2    Bar-Or, O.3    Lands, L.C.4    Moss, L.A.5    Wilson, W.M.6
  • 54
    • 66749087511 scopus 로고    scopus 로고
    • Non-invasive assessment of exercise performance in children with cystic fibrosis (CF) and non-cystic fibrosis bronchiectasis: Is there a CF specific muscle defect?
    • Rosenthal M, Narang I, Edwards L, Bush A. Non-invasive assessment of exercise performance in children with cystic fibrosis (CF) and non-cystic fibrosis bronchiectasis: is there a CF specific muscle defect? Pediatr Pulmonol 2009 44 222-230
    • (2009) Pediatr Pulmonol , vol.44 , pp. 222-230
    • Rosenthal, M.1    Narang, I.2    Edwards, L.3    Bush, A.4
  • 55
    • 0021272843 scopus 로고
    • Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis
    • Mansell A L., Andersen J C., Muttart C R. et al. Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis. J Pediatr 1984 104 700-705
    • (1984) J Pediatr , vol.104 , pp. 700-705
    • Mansell, A.L.1    Andersen, J.C.2    Muttart, C.R.3
  • 56
    • 0028118698 scopus 로고
    • Improvement of nutritional status and lung function after long-term nocturnal gastrostomy feedings in cystic fibrosis
    • Steinkamp G, von der Hardt H. Improvement of nutritional status and lung function after long-term nocturnal gastrostomy feedings in cystic fibrosis. J Pediatr 1994 124 244-249
    • (1994) J Pediatr , vol.124 , pp. 244-249
    • Steinkamp, G.1    Von Der Hardt, H.2
  • 57
    • 0035200585 scopus 로고    scopus 로고
    • Growth hormone improves clinical status in prepubertal children with cystic fibrosis: Results of a randomized controlled trial
    • Hardin D S., Ellis K J., Dyson M, Rice J, McConnell R, Seilheimer D K. Growth hormone improves clinical status in prepubertal children with cystic fibrosis: results of a randomized controlled trial. J Pediatr 2001 139 636-642
    • (2001) J Pediatr , vol.139 , pp. 636-642
    • Hardin, D.S.1    Ellis, K.J.2    Dyson, M.3    Rice, J.4    McConnell, R.5    Seilheimer, D.K.6
  • 58
    • 0347320554 scopus 로고    scopus 로고
    • Prospective randomised treatment with recombinant human growth hormone in cystic fibrosis
    • Schibler A, von der Heiden R, Birrer P, Mullis P E. Prospective randomised treatment with recombinant human growth hormone in cystic fibrosis. Arch Dis Child 2003 88 1078-1081
    • (2003) Arch Dis Child , vol.88 , pp. 1078-1081
    • Schibler, A.1    Von Der Heiden, R.2    Birrer, P.3    Mullis, P.E.4
  • 59
    • 0036735017 scopus 로고    scopus 로고
    • Consensus report on nutrition for pediatric patients with cystic fibrosis
    • Borowitz D, Baker R D., Stallings V. Consensus report on nutrition for pediatric patients with cystic fibrosis. J Pediatr Gastroenterol Nutr 2002 35 246-259
    • (2002) J Pediatr Gastroenterol Nutr , vol.35 , pp. 246-259
    • Borowitz, D.1    Baker, R.D.2    Stallings, V.3
  • 60
    • 0028885145 scopus 로고
    • Use of pancreatic enzyme supplements for patients with cystic fibrosis in the context of fibrosing colonopathy
    • Consensus Committee
    • Borowitz D S., Grand R J., Durie P R., Consensus Committee. Use of pancreatic enzyme supplements for patients with cystic fibrosis in the context of fibrosing colonopathy. J Pediatr 1995 127 681-684
    • (1995) J Pediatr , vol.127 , pp. 681-684
    • Borowitz, D.S.1    Grand, R.J.2    Durie, P.R.3
  • 62
    • 57749196975 scopus 로고    scopus 로고
    • Pancreatic enzyme replacement therapy for young cystic fibrosis patients
    • Munck A, Duhamel J-F, Lamireau T et al. Pancreatic enzyme replacement therapy for young cystic fibrosis patients. J Cyst Fibros 2009 8 14-18
    • (2009) J Cyst Fibros , vol.8 , pp. 14-18
    • Munck, A.1    Duhamel, J.-F.2    Lamireau, T.3
  • 64
  • 66
    • 70350508997 scopus 로고    scopus 로고
    • Description of a standardized nutrition classification plan and its relation to nutritional outcomes in children with cystic fibrosis
    • May 6 (EPub ahead of print)
    • Leonard A, Davis E, Rosenstein B J. et al. Description of a standardized nutrition classification plan and its relation to nutritional outcomes in children with cystic fibrosis. J Pediatr Psychol 2009 May 6 (EPub ahead of print)
    • (2009) J Pediatr Psychol
    • Leonard, A.1    Davis, E.2    Rosenstein, B.J.3
  • 68
    • 0033063958 scopus 로고    scopus 로고
    • A comparison of target height estimated and final height attained between Swedish and Hong Kong Chinese children
    • Luo Z C., Low L C., Karlberg J. A comparison of target height estimated and final height attained between Swedish and Hong Kong Chinese children. Acta Paediatr 1999 88 248-252
    • (1999) Acta Paediatr , vol.88 , pp. 248-252
    • Luo, Z.C.1    Low, L.C.2    Karlberg, J.3
  • 69
    • 0023719202 scopus 로고
    • A Medical Information Relational Database System (MIRDS)
    • Budd J, Warwick W J., Wielinski C L. A Medical Information Relational Database System (MIRDS). Comput Biomed Res 1988 21 419-433
    • (1988) Comput Biomed Res , vol.21 , pp. 419-433
    • Budd, J.1    Warwick, W.J.2    Wielinski, C.L.3


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