Long term survival and nutritional data in patients with cystic fibrosis treated in a Danish centre

Thorax

Volumn 51, Issue 10, 1996, Pages 1023-1027

  Nir, Martha ^a   Lanng, Susanne ^a   Johansen, Helle Krogh ^a   Koch, Christian ^a  

^a Rigshospitalet   (Denmark)

Author keywords

Cystic fibrosis; Nutrition; Survival

Indexed keywords

ANTIBIOTIC AGENT;

ADULT; ARTICLE; BODY MASS; CONTROLLED STUDY; CYSTIC FIBROSIS; DENMARK; FEMALE; HEALTH CARE QUALITY; HUMAN; LUNG FUNCTION; LUNG INFECTION; MAJOR CLINICAL STUDY; MALE; NUTRITION; PRIORITY JOURNAL; PSEUDOMONAS AERUGINOSA; SURVIVAL RATE;

EID: 0029850934     PISSN: 00406376     EISSN: None     Source Type: Journal    
DOI: 10.1136/thx.51.10.1023     Document Type: Article

References (31)

1. MacDonald A, Holden C, Harris G. Nutritional strategies in cystic fibrosis: current issues. J R Soc Med 1991;Suppl 18:28-35.
2. Bertrand JM, Morin CL, Lasalle R, Patrick J, Coates A. Short-term clinical, nutritional, and functional effects of continuous elemental enteral alimentation in children with cystic fibrosis. J Pediatr 1984;104:41-6.
3. O'Loughlin E, Forbes D, Parsons H, Scott B, Cooper D, Gall G. Nutritional rehabilitation of malnourished patients with cystic fibrosis. Am J Clin Nutr 1986;43:732-7.
4. Shepherd RW, Holt TL, Thomas BJ, Kay L, Isles A, Francis PJ, Ward LC. Nutritional rehabilitation in cystic fibrosis: controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease. J Pediatr 1986;109:788-94.
5. Shepherd RW, Holt TL, Cleghorn G, Ward LC, Isles A, Francis P. Short-term nutritional supplementation during management of pulmonary exacerbations in cystic fibrosis: a controlled study, including effects on protein turnover. Am J Clin Nutr 1988;48:235-9.
6. Levy DL, Durie PR, Pencharz PB, Corey ML. Effects of long-term nutritional rehabilitation on body composition and clinical status in malnourished children and adolescents with cystic fibrosis. J Pediatr 1985;107:225-30.
7. Gaskin KJ, Waters DL, Baur LA, Soutter VL, Gruca MA. Nutritional status, growth and development in children undergoing intensive treatment for cystic fibrosis. Acta Paediatr Scand (Suppl) 1990;366:106-10.
8. Vaisman N, Clarke R, Pencharz PB. Nutritional rehabilitation increases resting energy expenditure without affecting protein turnover in patients with cystic fibrosis. J Pediatr Gastroenterol Nutr 1991;13:383-90.
9. Boland MP, Stoski DS, MacDonald NE, Soucy P, Patrick J. Chronic jejunostomy feeding with a non-elemental formula in undernourished patients with cystic fibrosis. Lancet 1986;i:232-4.
10. Shepherd RW, Cooksley WGE, Cooke WDD. Improved growth and clinical, nutritional, and respiratory changes in response to nutritional therapy in cystic fibrosis. J Pediatr 1980;97:351-7.
11. Mansell AI, Andersen JC, Muttart CR, Ores CN, Loeff DS, Levy JS, et al. Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis. J Pediatr 1984;104:700-5.
12. Corey M, McLaughlin FJ, Williams M, Levison H. A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto. J Clin Epidemiol 1988;6:583-91.
13. Koch C, Høiby N. Management of cystic fibrosis in Copenhagen. Thorax 1991;46:385-6.
14. Pedersen SS, Jensen T, Høiby N, Koch C, Flensborg EW. Management of Pseudomonas aeruginosa lung infection in Danish cystic fibrosis patients. Acta Paediatr Scand 1987; 76:955-61.
15. Andersen E, Hutchings B. Jansen J, Nyholm M. Heights and weights of Danish children. Ugeskr Laeger 1982;144: 1760-5.
16. The Copenhagen City Heart Study Group. The Copenhagen City Heart Study. Osterbroundersogelsen. Scand J Social Med 1991;Suppl 41:88-93.
17. Ibsen KK. Factors influencing blood pressure in children and adolescents. Acta Paediatr Scand 1985;74:416-22.
18. Polgar GE, Promadhad V. Pulmonary function testing in children: techniques and standards. Philadelphia: WB Saunders, 1971: 88-107, 178-80.
19. Schwartz M, Johansen HK, Koch C, et al. Frequency of the delta F508 mutation on cystic fibrosis chromosomes in Denmark. Hum Genet 1990;85:427-8.
20. Soutter VL, Kristidis P, Gruca MA, Gaskin KJ. Chronic undernutrition/growth retardation in cystic fibrosis. Clin Gastroenterol 1986;15:137-55.
21. FitzSimmonns SC. The changing epidemiology of cystic fibrosis. J Pediatr 1993;122:1-9.
22. Nielsen OH, Schiøtz PO. Cystic fibrosis in Denmark in the period 1945-1981. Evaluation of centralized treatment. Acta Paediatr Scand 1982;Suppl 301:107-19.
23. Szaff M, Høiby N, Flensborg EW. Frequent antibiotic therapy improves survival of cystic fibrosis patients with chronic Pseudomonas aeruginosa infection. Acta Paediatr Scand 1983;72:651-7.
24. Pedersen SS, Jensen T, Høiby N, Koch C, Flensborg EW. Management of Pseudomonas aeruginosa lung infection in Danish cystic fibrosis patients. Acta Paediatr Scand 1987; 76:955-61.
25. Høiby N, Pedersen SS. Estimated risk of cross-infection with Pseudomonas aeruginosa in Danish cystic fibrosis patients. Acta Paediatr Scand 1989;78:395-404.
26. Valerius NH, Koch C, Høiby N. Prevention of chronic Pseudomonas aeruginosa colonization in cystic fibrosis by early treatment. Lancet 1991;338:725-6.
27. Kane RE, Hobbs P. Energy and respiratory metabolism in cystic fibrosis: the influence of carbohydrate content of nutritional supplements. J Pediatr Gastroenterol Nutr 1991; 12:217-23.
28. Holt TL, Thomas BJ, Ward LC, Shepherd RW. Nitrogen losses from sputum in cystic fibrosis: an unexpected factor in assessing protein energy balance. IRCS-Med Sci 1984; 12:370.
29. Vaisman N, Pencharz PB, Corey M, Canny GJ, Hahn E. Energy expenditure of patients with cystic fibrosis. J Pediatr 1987;111:496-500.
30. Suter S, Schaad UB, Roux-Lombard P, Girardin E, Grau G, Dayer J-M. Relation between tumor necrosis factor-alpha and granulocyte elastase-alpha 1-proteinase inhibitor complexes in the plasma of patients with cystic fibrosis. Am Rev Respir Dis 1989;140:1640-4.
31. Zeitlin SR, Bond S, Wootton S, Gregson RK, Radford M. Increased resting energy expenditure in childhood asthma: does this contribute towards growth failure? Arch Dis Child 1992;67:1366-9.