A novel mouse model reveals that polycystin-1 deficiency in ependyma and choroid plexus results in dysfunctional cilia and hydrocephalus

PLoS ONE

Volumn 4, Issue 9, 2009, Pages

  Wodarczyk, Claas ^a   Rowe, Isaline ^a   Chiaravalli, Marco ^a   Pema, Monika ^a   Qian, Feng ^b   Boletta, Alessandra ^a  

^a DULBECCO TELETHON INSTITUTE   (Italy)

^b JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

MYC PROTEIN; POLYCYSTIN 1; EPITOPE; POLYCYSTIC KIDNEY DISEASE 1 PROTEIN; POLYCYSTIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CHOROID PLEXUS; CONTROLLED STUDY; EMBRYO; EPENDYMA; EXPERIMENTAL MOUSE; GENE INSERTION; GENE LOCUS; HOMOLOGOUS RECOMBINATION; HYDROCEPHALUS; IN VIVO STUDY; MOUSE; NEWBORN; NONHUMAN; PHENOTYPE; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; SIGNAL TRANSDUCTION; ANIMAL; BRAIN; C57BL MOUSE; CHEMISTRY; EUKARYOTIC FLAGELLUM; GENETICS; HETEROZYGOTE; METABOLISM; MOUSE MUTANT; MUTATION; PROTEIN TERTIARY STRUCTURE;

MUS;

ANIMALS; ANIMALS, NEWBORN; BRAIN; CHOROID PLEXUS; CILIA; EPENDYMA; EPITOPES; HETEROZYGOTE; HYDROCEPHALUS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUTATION; PROTEIN STRUCTURE, TERTIARY; TRPP CATION CHANNELS;

EID: 70349612312     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0007137     Document Type: Article

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