Clinical aspects, immunologic assessment, and genetic analysis in taiwanese children with hemophagocytic lymphohistiocytosis

Pediatric Infectious Disease Journal

Volumn 28, Issue 1, 2009, Pages 30-34

  Lee, Wen I ^a,b   Chen, Shih Hsiang ^a   Hung, Iou Jih ^a   Yang, Chao Ping ^a   Jaing, Tang Her ^a   Chen, Chih Jung ^a   Li, Shin Pai ^a   Huang, Jing Long ^a  

^a CHANG GUNG UNIVERSITY   (Taiwan)

^b Department of Neurology Chang Gung   (Taiwan)

Author keywords

cyclosporine A; cytotoxicity; etoposide; Hemophagocytic lymphohistiocytosis (HLH); Mun 13 4; perforin; SH2D1A; syntaxin11

Indexed keywords

CD16 ANTIGEN; CD4 ANTIGEN; CD56 ANTIGEN; CD8 ANTIGEN; IMMUNOGLOBULIN; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; PERFORIN;

ACUTE LYMPHOBLASTIC LEUKEMIA; ADOLESCENT; ARTICLE; BONE MARROW BIOPSY; CELL STRAIN K 562; CHEDIAK HIGASHI SYNDROME; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; COHORT ANALYSIS; CONTROLLED STUDY; CYTOTOXICITY; DISEASE COURSE; EPSTEIN BARR VIRUS; FATALITY; FEMALE; GENE; GENE MUTATION; GENETIC ANALYSIS; GENETIC VARIABILITY; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; HUMAN CELL; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOREGULATION; INFANT; JUVENILE RHEUMATOID ARTHRITIS; LYMPHOCYTE SUBPOPULATION; MALE; MEMORY CELL; MEMORY T LYMPHOCYTE; MUN13 4 GENE; PFR1 GENE; PRIORITY JOURNAL; PROGNOSIS; PROTEIN EXPRESSION; QUANTITATIVE ANALYSIS; RETROSPECTIVE STUDY; SH2D1A GENE; STEM CELL TRANSPLANTATION; STX11 GENE; SURVIVAL; SYSTEMIC LUPUS ERYTHEMATOSUS; TAIWAN;

ADOLESCENT; CELL SURVIVAL; CHILD; CHILD, PRESCHOOL; FEMALE; HUMANS; IMMUNOGLOBULINS; INFANT; K562 CELLS; KILLER CELLS, NATURAL; LYMPHOCYTE SUBSETS; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MALE; PERFORIN; RETROSPECTIVE STUDIES; TAIWAN;

EID: 66149141742     PISSN: 08913668     EISSN: 15320987     Source Type: Journal    
DOI: 10.1097/INF.0b013e3181813592     Document Type: Article

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