Cytophagic histiocytic panniculitis with fatal haemophagocytic lymphohistiocytosis in a paediatric patient with perforin gene mutation

Journal of Clinical Pathology

Volumn 60, Issue 10, 2007, Pages 1168-1169

  Chen, Rong Long ^a   Hsu, Yung Hsiang ^b   Ueda, Ikuyo ^c   Imashuku, Shinsaku ^d   Takeuchi, Kengo ^e   Tu, Benjamin Pang Hsien ^f   Chuang, Shih Sung ^g,h,i  

^a CHI MEI MEDICAL CENTER   (Taiwan)

^b Buddhist Tzu Chi Medical Centre and University   (Taiwan)

^c KYOTO PREFECTURAL UNIVERSITY OF MEDICINE   (Japan)

^d Takasago seibu Hospital   (Japan)

^e CANCER INSTITUTE   (Japan)

^f INSTITUTE OF BIOMEDICAL SCIENCES   (Taiwan)

^g CHI MEI FOUNDATION HOSPITAL   (Taiwan)

^h TAIPEI MEDICAL UNIVERSITY   (Taiwan)

ⁱ Chi Mei Foundation Hospital   (Taiwan)

Author keywords

[No Author keywords available]

Indexed keywords

CYCLOSPORIN A; ISOTRETINOIN; METHOTREXATE; PERFORIN; PREDNISOLONE;

ANAMNESIS; ARTICLE; AUTOPSY; CASE REPORT; CLINICAL FEATURE; CYTOPHAGIC HISTIOCYTIC PANNICULITIS; DISEASE ASSOCIATION; FEMALE; GENE MUTATION; GENETIC ASSOCIATION; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; IMMUNOHISTOCHEMISTRY; LABORATORY TEST; PANNICULITIS; PHYSICAL EXAMINATION; PRIORITY JOURNAL; SCHOOL CHILD; SKIN BIOPSY; TREATMENT OUTCOME;

EID: 35348993736     PISSN: 00219746     EISSN: None     Source Type: Journal    
DOI: 10.1136/jcp.2007.049551     Document Type: Article

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