-
1
-
-
0024424270
-
Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA
-
Riordan JR, Rommens JM, Kerem B, Alon N, Rozmahel R, et al. (1989) Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA. Science 245: 106-173.
-
(1989)
Science
, vol.245
, pp. 106-173
-
-
Riordan, J.R.1
Rommens, J.M.2
Kerem, B.3
Alon, N.4
Rozmahel, R.5
-
2
-
-
0025277214
-
Abnormal regulation of ion channels in cystic fibrosis epithelia
-
Welsh MJ (1990) Abnormal regulation of ion channels in cystic fibrosis epithelia. FASEB J 4: 2718-2725.
-
(1990)
FASEB J
, vol.4
, pp. 2718-2725
-
-
Welsh, M.J.1
-
3
-
-
0029912194
-
Regulation of epithelial sodium channels by the cystic fibrosis transmembrane conductance regulator
-
Ismailov II, Awayda MS, Jovov B, Berdiev BK, Fuller CM, et al. (1996) Regulation of epithelial sodium channels by the cystic fibrosis transmembrane conductance regulator. J Biol Chem 271: 4725-4732.
-
(1996)
J Biol Chem
, vol.271
, pp. 4725-4732
-
-
Ismailov, I.I.1
Awayda, M.S.2
Jovov, B.3
Berdiev, B.K.4
Fuller, C.M.5
-
4
-
-
0036891133
-
Altered phospholipid composition and aggregate structure of lung surfactant is associated with impaired lung function in young children with respiratory infections
-
Mander A, Langton-Hewer S, Bernhard W, Warner JO, Postle AD (2002) Altered phospholipid composition and aggregate structure of lung surfactant is associated with impaired lung function in young children with respiratory infections. Am J Respir Cell Mol Biol 27: 714-721.
-
(2002)
Am J Respir Cell Mol Biol
, vol.27
, pp. 714-721
-
-
Mander, A.1
Langton-Hewer, S.2
Bernhard, W.3
Warner, J.O.4
Postle, A.D.5
-
5
-
-
0033930359
-
Function and composition of pulmonary surfactant and surfactant-derived fatty acid profiles are altered in young adults with cystic fibrosis
-
Meyer KC, Sharma A, Brown R, Weatherly M, Moya FR, et al. (2000) Function and composition of pulmonary surfactant and surfactant-derived fatty acid profiles are altered in young adults with cystic fibrosis. Chest 118: 164-174.
-
(2000)
Chest
, vol.118
, pp. 164-174
-
-
Meyer, K.C.1
Sharma, A.2
Brown, R.3
Weatherly, M.4
Moya, F.R.5
-
6
-
-
35348961960
-
Adult cystic fibrosis
-
Boyle MP (2007) Adult cystic fibrosis. JAMA 298: 1787-1793.
-
(2007)
JAMA
, vol.298
, pp. 1787-1793
-
-
Boyle, M.P.1
-
7
-
-
0034353227
-
The deltaF508 mutation in the cystic fibrosis transmembrane conductance regulator alters control of essential fatty acid utilization in epithelial cells
-
Bhura-Bandali FN, Suh M, Man SF, Clandinin MT (2000) The deltaF508 mutation in the cystic fibrosis transmembrane conductance regulator alters control of essential fatty acid utilization in epithelial cells. J Nutr 130: 2870-2875.
-
(2000)
J Nutr
, vol.130
, pp. 2870-2875
-
-
Bhura-Bandali, F.N.1
Suh, M.2
Man, S.F.3
Clandinin, M.T.4
-
8
-
-
0028982894
-
CFTR as a cAMP-dependent regulator of sodium channels
-
Stutts MJ, Canessa CM, Olsen JC, Hamrick M, Cohn JA, et al. (1995) CFTR as a cAMP-dependent regulator of sodium channels. Science 269: 847-850.
-
(1995)
Science
, vol.269
, pp. 847-850
-
-
Stutts, M.J.1
Canessa, C.M.2
Olsen, J.C.3
Hamrick, M.4
Cohn, J.A.5
-
9
-
-
0027191065
-
CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship
-
Gabriel SE, Clarke LL, Boucher RC, Stutts MJ (1993) CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship. Nature 363: 263-268.
-
(1993)
Nature
, vol.363
, pp. 263-268
-
-
Gabriel, S.E.1
Clarke, L.L.2
Boucher, R.C.3
Stutts, M.J.4
-
10
-
-
0028130394
-
Cystic fibrosis and phosphatidylcholine biosynthesis
-
Ulane MM, Butler JD, Peri A, Miele L, Ulane RE, et al. (1994) Cystic fibrosis and phosphatidylcholine biosynthesis. Clin Chim Acta 230: 109-116.
-
(1994)
Clin Chim Acta
, vol.230
, pp. 109-116
-
-
Ulane, M.M.1
Butler, J.D.2
Peri, A.3
Miele, L.4
Ulane, R.E.5
-
11
-
-
0033598714
-
A membrane lipid imbalance plays a role in the phenotype expression of cystic fibrosis in CFTR -/- mice
-
Freedman SD, Katz MH, Parker EM, Laposata M, Urman MY, et al. (1999) A membrane lipid imbalance plays a role in the phenotype expression of cystic fibrosis in CFTR -/- mice. Proc Natl Acad Sci Usa 96: 13995-14000.
-
(1999)
Proc Natl Acad Sci Usa
, vol.96
, pp. 13995-14000
-
-
Freedman, S.D.1
Katz, M.H.2
Parker, E.M.3
Laposata, M.4
Urman, M.Y.5
-
12
-
-
0035192463
-
Essential fatty acid deficiency in relation to genotype in patients with cystic fibrosis
-
Strandvik B, Gronowitz E, Enlund F, Martinsson T, Wahlstrom J (2001) Essential fatty acid deficiency in relation to genotype in patients with cystic fibrosis. J Pediatr 139: 650-655.
-
(2001)
J Pediatr
, vol.139
, pp. 650-655
-
-
Strandvik, B.1
Gronowitz, E.2
Enlund, F.3
Martinsson, T.4
Wahlstrom, J.5
-
14
-
-
0024513463
-
Aberrant free radical activity in cystic fibrosis
-
Salh B, Webb K, Guyan PM, Day JP, Wickens D, et al. (1989) Aberrant free radical activity in cystic fibrosis. Clin Chim Acta 181: 65-74.
-
(1989)
Clin Chim Acta
, vol.181
, pp. 65-74
-
-
Salh, B.1
Webb, K.2
Guyan, P.M.3
Day, J.P.4
Wickens, D.5
-
15
-
-
0028213618
-
Oxygen free radicals and antioxidants in cystic fibrosis: The concept of an oxidant-antioxidant imbalance
-
Winklhofer-Roob BM (1994) Oxygen free radicals and antioxidants in cystic fibrosis: the concept of an oxidant-antioxidant imbalance. Acta Paediatr Suppl 395: 49-57.
-
(1994)
Acta Paediatr
, Issue.SUPPL. 395
, pp. 49-57
-
-
Winklhofer-Roob, B.M.1
-
16
-
-
7444269737
-
Cystic fibrosis transmembrane conductance regulator in human and mouse red blood cell membranes and its interaction with ecto-apyrase
-
Sterling KM Jr, Shah S, Kim RJ, Johnston NI, Salikhova AY, et al. (2004) Cystic fibrosis transmembrane conductance regulator in human and mouse red blood cell membranes and its interaction with ecto-apyrase. J Cell Biochem 91: 1174-1182.
-
(2004)
J Cell Biochem
, vol.91
, pp. 1174-1182
-
-
Sterling Jr, K.M.1
Shah, S.2
Kim, R.J.3
Johnston, N.I.4
Salikhova, A.Y.5
-
17
-
-
33947301605
-
Long-term docosahexaenoic acid therapy in a congenic murine model of cystic fibrosis
-
Beharry S, Ackerley C, Corey M, Kent G, Heng YM, et al. (2007) Long-term docosahexaenoic acid therapy in a congenic murine model of cystic fibrosis. Am J Physiol Gastrointest Liver Physiol 292: G839-848.
-
(2007)
Am J Physiol Gastrointest Liver Physiol
, vol.292
-
-
Beharry, S.1
Ackerley, C.2
Corey, M.3
Kent, G.4
Heng, Y.M.5
-
18
-
-
10744223051
-
Association of cystic fibrosis with abnormalities in fatty acid metabolism
-
Freedman SD, Blanco PG, Zaman MM, Shea JC, Ollero M, et al. (2004) Association of cystic fibrosis with abnormalities in fatty acid metabolism. The New England journal of medicine 350: 560-569.
-
(2004)
The New England journal of medicine
, vol.350
, pp. 560-569
-
-
Freedman, S.D.1
Blanco, P.G.2
Zaman, M.M.3
Shea, J.C.4
Ollero, M.5
-
19
-
-
34548235901
-
Fatty acids platelets and oxidative markers following intravenous n-3 fatty acids administration in cystic fibrosis: An open pilot observational study
-
Durieu I, Vericel E, Guichardant D, Roth H, Steghens JP, et al. (2007) Fatty acids platelets and oxidative markers following intravenous n-3 fatty acids administration in cystic fibrosis: An open pilot observational study. J Cyst Fibros 6: 320-326.
-
(2007)
J Cyst Fibros
, vol.6
, pp. 320-326
-
-
Durieu, I.1
Vericel, E.2
Guichardant, D.3
Roth, H.4
Steghens, J.P.5
-
20
-
-
33745975493
-
Can 5-methyltetrahydrofolate modify the phospholipid fatty acid pattern in cystic fibrosis pediatric patients?
-
Scambi C, Guarini P, De Franceschi L, Bambara LM (2006) Can 5-methyltetrahydrofolate modify the phospholipid fatty acid pattern in cystic fibrosis pediatric patients? J Cyst Fibros 5: 197-199.
-
(2006)
J Cyst Fibros
, vol.5
, pp. 197-199
-
-
Scambi, C.1
Guarini, P.2
De Franceschi, L.3
Bambara, L.M.4
-
21
-
-
0033831799
-
Folate administration increases n-3 polyunsaturated fatty acids in rat plasma and tissue lipids
-
Pita ML, Delgrado MJ (2000) Folate administration increases n-3 polyunsaturated fatty acids in rat plasma and tissue lipids. Thromb Haemost 84: 420-423.
-
(2000)
Thromb Haemost
, vol.84
, pp. 420-423
-
-
Pita, M.L.1
Delgrado, M.J.2
-
22
-
-
0032589204
-
Folate and vitamin B12
-
Scott JM (1999) Folate and vitamin B12. Proc Nutr Soc 58: 441-448.
-
(1999)
Proc Nutr Soc
, vol.58
, pp. 441-448
-
-
Scott, J.M.1
-
23
-
-
0022408024
-
Phosphatidylcholine produced in rat synaptosomes by N-methylation is enriched in polyunsaturated fatty acids
-
Tacconi M, Wurtman RJ (1985) Phosphatidylcholine produced in rat synaptosomes by N-methylation is enriched in polyunsaturated fatty acids. Proc Natl Acad Sci U S A 82: 4828-4831.
-
(1985)
Proc Natl Acad Sci U S A
, vol.82
, pp. 4828-4831
-
-
Tacconi, M.1
Wurtman, R.J.2
-
24
-
-
0037125962
-
Role for phospholipid interactions in the trafficking defect of Delta F508-CFTR
-
Eidelman O, BarNoy S, Razin M, Zhang J, McPhie P, et al. (2002) Role for phospholipid interactions in the trafficking defect of Delta F508-CFTR. Biochemistry 41: 11161-11170.
-
(2002)
Biochemistry
, vol.41
, pp. 11161-11170
-
-
Eidelman, O.1
BarNoy, S.2
Razin, M.3
Zhang, J.4
McPhie, P.5
-
25
-
-
0141839070
-
Increased plasma homocysteine and S-adenosylhomocysteine and decreased methionine is associated with altered phosphatidylcholine and phosphatidylethanolamine in cystic fibrosis
-
Innis SM, Davidson AG, Chen A, Dyer R, Melnyk S, et al. (2003) Increased plasma homocysteine and S-adenosylhomocysteine and decreased methionine is associated with altered phosphatidylcholine and phosphatidylethanolamine in cystic fibrosis. J Pediatr 143: 351-356.
-
(2003)
J Pediatr
, vol.143
, pp. 351-356
-
-
Innis, S.M.1
Davidson, A.G.2
Chen, A.3
Dyer, R.4
Melnyk, S.5
-
26
-
-
33747418536
-
Red blood cell folate concentrations increase more after supplementation with [6S]-5-methyltetrahydrofolate than with folic acid in women of childbearing age
-
Lamers Y, Prinz-Langenohl R, Brämswig S, Pietrzik K (2006) Red blood cell folate concentrations increase more after supplementation with [6S]-5-methyltetrahydrofolate than with folic acid in women of childbearing age. Am J Clin Nutr 84: 156-161.
-
(2006)
Am J Clin Nutr
, vol.84
, pp. 156-161
-
-
Lamers, Y.1
Prinz-Langenohl, R.2
Brämswig, S.3
Pietrzik, K.4
-
27
-
-
36248946255
-
Calculation of red blood cell folate steady state conditions and elimination kinetics after daily supplementation with various folate forms and doses in women of childbearing age
-
Pietrzik K, Lamers Y, Brämswig S, Prinz-Langenohl R (2007) Calculation of red blood cell folate steady state conditions and elimination kinetics after daily supplementation with various folate forms and doses in women of childbearing age. Am J Clin Nutr 86: 1414-1419.
-
(2007)
Am J Clin Nutr
, vol.86
, pp. 1414-1419
-
-
Pietrzik, K.1
Lamers, Y.2
Brämswig, S.3
Prinz-Langenohl, R.4
-
28
-
-
0037371082
-
Comparison of the effect of low-dose supplementation with L-5-methyltetrahydrofolate or folic acid on plasma homocysteine: A randomized placebo-controlled study
-
Venn BJ, Green TJ, Moser R, Mann JI (2003) Comparison of the effect of low-dose supplementation with L-5-methyltetrahydrofolate or folic acid on plasma homocysteine: a randomized placebo-controlled study. Am J Clin Nutr 77: 658-662.
-
(2003)
Am J Clin Nutr
, vol.77
, pp. 658-662
-
-
Venn, B.J.1
Green, T.J.2
Moser, R.3
Mann, J.I.4
-
29
-
-
0034691317
-
Controlled Comparison of L-5-Methyltetrahydrofolate Versus Folic Acid for the Treatment of Hyperhomocysteinemia in Hemodialysis Patients
-
Bostom AG, Shemin D, Bagley P, Massy ZA, Zanabli A, et al. (2000) Controlled Comparison of L-5-Methyltetrahydrofolate Versus Folic Acid for the Treatment of Hyperhomocysteinemia in Hemodialysis Patients. Circulation 101: 2829-2832.
-
(2000)
Circulation
, vol.101
, pp. 2829-2832
-
-
Bostom, A.G.1
Shemin, D.2
Bagley, P.3
Massy, Z.A.4
Zanabli, A.5
-
30
-
-
0016610909
-
Folate deficiency in the alcoholic-its relationship to clinical and haematological abnormalities, liver disease and folate stores
-
Wu A, Chanarin I, Slavin G, Levi AJ (1975) Folate deficiency in the alcoholic-its relationship to clinical and haematological abnormalities, liver disease and folate stores. Br J Haematol 29: 469-478.
-
(1975)
Br J Haematol
, vol.29
, pp. 469-478
-
-
Wu, A.1
Chanarin, I.2
Slavin, G.3
Levi, A.J.4
-
31
-
-
15744398506
-
Erythrocytes of humans with cystic fibrosis fail to stimulate nitric oxide synthesis in isolated rabbit lungs
-
Liang G, Stephenson AH, Lonigro AJ, Sprague RS (2005) Erythrocytes of humans with cystic fibrosis fail to stimulate nitric oxide synthesis in isolated rabbit lungs. Am J Physiol Heart Circ Physiol 288: H1580-1585.
-
(2005)
Am J Physiol Heart Circ Physiol
, vol.288
-
-
Liang, G.1
Stephenson, A.H.2
Lonigro, A.J.3
Sprague, R.S.4
-
32
-
-
0035051127
-
Erythrocyte membrane ATP binding cassette (ABC) proteins: MRP1 and CFTR as well as CD39 (ecto-apyrase) involved in RBC ATP transport and elevated blood plasma ATP of cystic fibrosis
-
Abraham EH, Sterling KM, Kim RJ, Salikhova AY, Huffman HB, et al. (2001) Erythrocyte membrane ATP binding cassette (ABC) proteins: MRP1 and CFTR as well as CD39 (ecto-apyrase) involved in RBC ATP transport and elevated blood plasma ATP of cystic fibrosis. Blood Cells Mol Dis 27: 165-180.
-
(2001)
Blood Cells Mol Dis
, vol.27
, pp. 165-180
-
-
Abraham, E.H.1
Sterling, K.M.2
Kim, R.J.3
Salikhova, A.Y.4
Huffman, H.B.5
-
33
-
-
34248504870
-
Chloride channels in normal and cystic fibrosis human erythrocyte membrane
-
Decherf G, Bouyer G, Egée S, Thomas SL (2007) Chloride channels in normal and cystic fibrosis human erythrocyte membrane. Blood Cells Mol Dis 39: 24-34.
-
(2007)
Blood Cells Mol Dis
, vol.39
, pp. 24-34
-
-
Decherf, G.1
Bouyer, G.2
Egée, S.3
Thomas, S.L.4
-
34
-
-
33750440785
-
Reduced number of CFTR molecules in erythrocyte plasma membrane of cystic fibrosis patients
-
Lange T, Jungmann P, Haberle J, Falk S, Duebbers A, et al. (2006) Reduced number of CFTR molecules in erythrocyte plasma membrane of cystic fibrosis patients. Mol Membr Biol 23: 317-323.
-
(2006)
Mol Membr Biol
, vol.23
, pp. 317-323
-
-
Lange, T.1
Jungmann, P.2
Haberle, J.3
Falk, S.4
Duebbers, A.5
-
35
-
-
0026322389
-
Increased susceptibility to peroxide-induced haemolysis with normal vitamin E concentrations in cystic fibrosis
-
James DR, Alfaham M, Goodchild MC (1991) Increased susceptibility to peroxide-induced haemolysis with normal vitamin E concentrations in cystic fibrosis. Clin Chim Acta 204: 279-290.
-
(1991)
Clin Chim Acta
, vol.204
, pp. 279-290
-
-
James, D.R.1
Alfaham, M.2
Goodchild, M.C.3
-
36
-
-
0033011470
-
Lipid peroxidation and antioxidant defenses in cystic fibrosis patients
-
Benabdeslam H, Abidi H, Garcia I, Bellon G, Gilly R, et al. (1999) Lipid peroxidation and antioxidant defenses in cystic fibrosis patients. Clin Chem Lab Med 37: 511-516.
-
(1999)
Clin Chem Lab Med
, vol.37
, pp. 511-516
-
-
Benabdeslam, H.1
Abidi, H.2
Garcia, I.3
Bellon, G.4
Gilly, R.5
-
37
-
-
0042333268
-
Antioxidant status in erythrocytes of cystic fibrosis children
-
Laskowska-klita T, Chelchowska M (2001) Antioxidant status in erythrocytes of cystic fibrosis children. Acta Biochim Pol 48: 283-285.
-
(2001)
Acta Biochim Pol
, vol.48
, pp. 283-285
-
-
Laskowska-klita, T.1
Chelchowska, M.2
-
40
-
-
0030897995
-
Altered erythrocyte sodium-lithium counter-transport and Na+/ K(+)-ATPase activity in cystic fibrosis
-
Luczay A, Vásárhelyi B, Dobos M, Holics K, Ujhelyi R, et al. (1997) Altered erythrocyte sodium-lithium counter-transport and Na+/ K(+)-ATPase activity in cystic fibrosis. Acta Paediatr 86: 245-247.
-
(1997)
Acta Paediatr
, vol.86
, pp. 245-247
-
-
Luczay, A.1
Vásárhelyi, B.2
Dobos, M.3
Holics, K.4
Ujhelyi, R.5
-
41
-
-
0018087847
-
Calcium and sodium transport processes in patients with cystic fibrosis. I. A specific decrease in Mg2+-dependent, Ca2+-adenosine triphosphatase activity in erythrocyte membranes from cystic fibrosis patients
-
Katz S (1978) Calcium and sodium transport processes in patients with cystic fibrosis. I. A specific decrease in Mg2+-dependent, Ca2+-adenosine triphosphatase activity in erythrocyte membranes from cystic fibrosis patients. Pediatr Res 12: 1033-1038.
-
(1978)
Pediatr Res
, vol.12
, pp. 1033-1038
-
-
Katz, S.1
-
42
-
-
0022546662
-
K dependence of the Na-K pump is abnormal in erythrocytes from patients with cystic fibrosis and obligate heterozygotes
-
Reznik VM, Harwood IR, Mendoza SA (1986) K dependence of the Na-K pump is abnormal in erythrocytes from patients with cystic fibrosis and obligate heterozygotes. Biochem Biophys Res Commun 137: 1021-1027.
-
(1986)
Biochem Biophys Res Commun
, vol.137
, pp. 1021-1027
-
-
Reznik, V.M.1
Harwood, I.R.2
Mendoza, S.A.3
-
43
-
-
0023772786
-
Kinetic parameters of rubidium transport pathways are normal in cystic fibrosis red cells
-
Joiner CH (1988) Kinetic parameters of rubidium transport pathways are normal in cystic fibrosis red cells. Pediatr Res 24: 495-498.
-
(1988)
Pediatr Res
, vol.24
, pp. 495-498
-
-
Joiner, C.H.1
-
44
-
-
0026089714
-
Low concentrations of sodium and magnesium in erythrocytes from cystic fibrosis heterozygotes
-
Foucard T, Gebre-Medhin M, Gustavson KH, Lindh U (1991) Low concentrations of sodium and magnesium in erythrocytes from cystic fibrosis heterozygotes. Acta Paediatr Scand 80: 57-61.
-
(1991)
Acta Paediatr Scand
, vol.80
, pp. 57-61
-
-
Foucard, T.1
Gebre-Medhin, M.2
Gustavson, K.H.3
Lindh, U.4
-
45
-
-
0023628783
-
Determination of free and total homocysteine in human plasma by high-performance liquid chromatography with fluorescence detection
-
Araki A, Sako Y (1987) Determination of free and total homocysteine in human plasma by high-performance liquid chromatography with fluorescence detection. Journal of chromatography 422: 43-52.
-
(1987)
Journal of chromatography
, vol.422
, pp. 43-52
-
-
Araki, A.1
Sako, Y.2
-
46
-
-
0025848779
-
Rapid high-performance liquid chromatographic assay for total homocysteine levels in human serum
-
Ubbink JB, Hayward Vermaak WJ, Bissbort S (1991) Rapid high-performance liquid chromatographic assay for total homocysteine levels in human serum. Journal of chromatography 565: 441-446.
-
(1991)
Journal of chromatography
, vol.565
, pp. 441-446
-
-
Ubbink, J.B.1
Hayward Vermaak, W.J.2
Bissbort, S.3
-
47
-
-
0037173514
-
Rapid, fluorimetric-liquid chromatographic determination of malondialdehyde in biological samples
-
Agarwal R, Chase SD (2002) Rapid, fluorimetric-liquid chromatographic determination of malondialdehyde in biological samples. J Chromatogr B Analyt Technol Biomed Life Sci 775: 121-126.
-
(2002)
J Chromatogr B Analyt Technol Biomed Life Sci
, vol.775
, pp. 121-126
-
-
Agarwal, R.1
Chase, S.D.2
-
48
-
-
0025940814
-
Free and bound malondialdehyde measured as thiobarbituric acid adduct by HPLC in serum and plasma
-
Carbonneau MA, Peuchant E, Sess D, Canioni P, Clerc M (1991) Free and bound malondialdehyde measured as thiobarbituric acid adduct by HPLC in serum and plasma. Clinical chemistry 37: 1423-1429.
-
(1991)
Clinical chemistry
, vol.37
, pp. 1423-1429
-
-
Carbonneau, M.A.1
Peuchant, E.2
Sess, D.3
Canioni, P.4
Clerc, M.5
-
49
-
-
0022548964
-
Direct transesterification of all classes of lipid in a one-step reaction
-
Lepage G, Roy CC (1986) Direct transesterification of all classes of lipid in a one-step reaction. J Lipid Res 27: 114-120.
-
(1986)
J Lipid Res
, vol.27
, pp. 114-120
-
-
Lepage, G.1
Roy, C.C.2
-
50
-
-
0026497204
-
Red blood cells and platelet membrane fatty acids in non-dialyzed and dialyzed uremics
-
Girelli D, Azzini M, Olivieri O, Guarini P, Trevisan MT, et al. (1992) Red blood cells and platelet membrane fatty acids in non-dialyzed and dialyzed uremics. Clin Chim Acta 211: 155-166.
-
(1992)
Clin Chim Acta
, vol.211
, pp. 155-166
-
-
Girelli, D.1
Azzini, M.2
Olivieri, O.3
Guarini, P.4
Trevisan, M.T.5
-
51
-
-
0028951432
-
Docosahexaenoic acid in red blood cells of patients with X-linked retinitis pigmentosa
-
Hoffman DR, Birch DG (1995) Docosahexaenoic acid in red blood cells of patients with X-linked retinitis pigmentosa. Investigative ophthalmology&visual science 36: 1009-1018.
-
(1995)
Investigative ophthalmology&visual science
, vol.36
, pp. 1009-1018
-
-
Hoffman, D.R.1
Birch, D.G.2
-
52
-
-
0028826919
-
Red blood cell cation transports in uraemic anaemia: Evidence for an increased K/Cl co-transport activity. Effects of dialysis and erythropoietin treatment
-
De Franceschi L, Olivieri O, Girelli D, Lupo A, Bernich P, et al. (1995) Red blood cell cation transports in uraemic anaemia: evidence for an increased K/Cl co-transport activity. Effects of dialysis and erythropoietin treatment. Eur J Clin Invest 25: 762-768.
-
(1995)
Eur J Clin Invest
, vol.25
, pp. 762-768
-
-
De Franceschi, L.1
Olivieri, O.2
Girelli, D.3
Lupo, A.4
Bernich, P.5
-
53
-
-
0030964677
-
Oral magnesium supplements reduce erythrocyte dehydration in patients with sickle cell disease
-
De Franceschi L, Bachir D, Galacteros F, Tchernia G, Cynober T, et al. (1997) Oral magnesium supplements reduce erythrocyte dehydration in patients with sickle cell disease. J Clin Invest 100: 1847-1852
-
(1997)
J Clin Invest
, vol.100
, pp. 1847-1852
-
-
De Franceschi, L.1
Bachir, D.2
Galacteros, F.3
Tchernia, G.4
Cynober, T.5
-
54
-
-
33751120184
-
Effect of complete protein 4.1R deficiency on ion transport properties of murine erythrocytes
-
Rivera A, De Franceschi L, Peters LL, Gascard P, Mohandas N, et al. (2006) Effect of complete protein 4.1R deficiency on ion transport properties of murine erythrocytes. Am J Physiol Cell Physiol 291: C880-886.
-
(2006)
Am J Physiol Cell Physiol
, vol.291
-
-
Rivera, A.1
De Franceschi, L.2
Peters, L.L.3
Gascard, P.4
Mohandas, N.5
-
55
-
-
0029165258
-
Role of hemichrome binding to erythrocyte membrane in the generation of band-3 alterations in beta-thalassemia intermedia erythrocytes
-
Mannu F, Arese P, Cappellini MD, Fiorelli G, Cappadoro M, et al. (1995) Role of hemichrome binding to erythrocyte membrane in the generation of band-3 alterations in beta-thalassemia intermedia erythrocytes. Blood 86: 2014-2020.
-
(1995)
Blood
, vol.86
, pp. 2014-2020
-
-
Mannu, F.1
Arese, P.2
Cappellini, M.D.3
Fiorelli, G.4
Cappadoro, M.5
-
56
-
-
20644464765
-
Acrylamide-agarose copolymers: Improved resolution of high molecular mass proteins in two-dimensional gel electrophoresis
-
Roncada P, Cretich M, Fortin R, Agosti S, De Franceschi L, et al. (2005) Acrylamide-agarose copolymers: improved resolution of high molecular mass proteins in two-dimensional gel electrophoresis. Proteomics 5: 2331-2339.
-
(2005)
Proteomics
, vol.5
, pp. 2331-2339
-
-
Roncada, P.1
Cretich, M.2
Fortin, R.3
Agosti, S.4
De Franceschi, L.5
-
57
-
-
31144465975
-
Protein/RNA coextraction and small two-dimensional polyacrylamide gel electrophoresis for proteomic/gene expression analysis of renal cancer biopsies
-
Barbero G, Carta F, Giribaldi G, Mandili G, Crobu S, et al. (2006) Protein/RNA coextraction and small two-dimensional polyacrylamide gel electrophoresis for proteomic/gene expression analysis of renal cancer biopsies. Anal Biochem 349: 62-71.
-
(2006)
Anal Biochem
, vol.349
, pp. 62-71
-
-
Barbero, G.1
Carta, F.2
Giribaldi, G.3
Mandili, G.4
Crobu, S.5
-
58
-
-
11244333118
-
A mathematical model of the folate cycle: New insights into folate homeostasis
-
Nijhout HF, Reed MC, Budu P, Ulrich CM (2004) A mathematical model of the folate cycle: new insights into folate homeostasis. J Biol Chem 279: 55008-55016.
-
(2004)
J Biol Chem
, vol.279
, pp. 55008-55016
-
-
Nijhout, H.F.1
Reed, M.C.2
Budu, P.3
Ulrich, C.M.4
-
59
-
-
33644916668
-
Cellular folate vitamer distribution during and after correction of vitamin B12 deficiency: A case for the methylfolate trap
-
Smulders YM, Smith DE, Kok RM, Teerlink T, Swinkels DW, et al. (2006) Cellular folate vitamer distribution during and after correction of vitamin B12 deficiency: a case for the methylfolate trap. Br J Haematol 132: 623-629.
-
(2006)
Br J Haematol
, vol.132
, pp. 623-629
-
-
Smulders, Y.M.1
Smith, D.E.2
Kok, R.M.3
Teerlink, T.4
Swinkels, D.W.5
-
60
-
-
0032573077
-
A common mutation in the methylenetetrahydrofolate reductase gene is associated with an accumulation of formylated tetrahydrofolates in red blood cells
-
Bagley PJ, Selhub J (1998) A common mutation in the methylenetetrahydrofolate reductase gene is associated with an accumulation of formylated tetrahydrofolates in red blood cells. Proceedings of the National Academy of Sciences of the United States of America 95: 13217-13220.
-
(1998)
Proceedings of the National Academy of Sciences of the United States of America
, vol.95
, pp. 13217-13220
-
-
Bagley, P.J.1
Selhub, J.2
-
61
-
-
0037657585
-
The interaction between MTHFR 677 CRT genotype and folate status is a determinant of coronary atherosclerosis risk
-
Girelli D, Martinelli N, Pizzolo F, Friso S, Olivieri O, et al. (2003) The interaction between MTHFR 677 CRT genotype and folate status is a determinant of coronary atherosclerosis risk. The Journal of nutrition 133: 1281-1285.
-
(2003)
The Journal of nutrition
, vol.133
, pp. 1281-1285
-
-
Girelli, D.1
Martinelli, N.2
Pizzolo, F.3
Friso, S.4
Olivieri, O.5
-
62
-
-
0347627540
-
Tetrahydrofolate and 5-methyltetrahydrofolate are folates with high antioxidant activity. Identification of the antioxidant pharmacophore
-
Rezk BM, Haenen GR, van der Vijgh WJ, Bast A (2003) Tetrahydrofolate and 5-methyltetrahydrofolate are folates with high antioxidant activity. Identification of the antioxidant pharmacophore. FEBS Lett 555: 601-605.
-
(2003)
FEBS Lett
, vol.555
, pp. 601-605
-
-
Rezk, B.M.1
Haenen, G.R.2
van der Vijgh, W.J.3
Bast, A.4
-
65
-
-
25844494542
-
Sick chaperones, cellular stress, and disease
-
Macario AJ (2005) Sick chaperones, cellular stress, and disease. N Engl J Med 353: 1489-1501.
-
(2005)
N Engl J Med
, vol.353
, pp. 1489-1501
-
-
Macario, A.J.1
-
66
-
-
33750842131
-
Hsp90 cochaperone Aha1 downregulation rescues misfolding of CFTR in cystic fibrosis
-
Wang X, Venable J, LaPointe P, Hutt DM, Koulov AV, et al. (2006) Hsp90 cochaperone Aha1 downregulation rescues misfolding of CFTR in cystic fibrosis. Cell 127: 803-815.
-
(2006)
Cell
, vol.127
, pp. 803-815
-
-
Wang, X.1
Venable, J.2
LaPointe, P.3
Hutt, D.M.4
Koulov, A.V.5
-
67
-
-
0023019347
-
Lymphocyte and granulocyte phosphatidylethanolamine Nmethyltransferase: Properties and activity in cystic fibrosis
-
Davis PB (1986) Lymphocyte and granulocyte phosphatidylethanolamine Nmethyltransferase: properties and activity in cystic fibrosis. Pediatr Res 2: 1290-1296.
-
(1986)
Pediatr Res
, vol.2
, pp. 1290-1296
-
-
Davis, P.B.1
-
69
-
-
0020264385
-
The effect of variations in dietary fatty acids on the fatty acid composition of erythrocyte phosphatidylcholine and phosphatidylethanolamine in human infants
-
Putnam JC, Carlson SE, DeVoe PW, Barness LA (1982) The effect of variations in dietary fatty acids on the fatty acid composition of erythrocyte phosphatidylcholine and phosphatidylethanolamine in human infants. Am J Clin Nutr. pp 106-114.
-
(1982)
Am J Clin Nutr
, pp. 106-114
-
-
Putnam, J.C.1
Carlson, S.E.2
DeVoe, P.W.3
Barness, L.A.4
-
70
-
-
0036196984
-
Increased plasma fatty acid concentrations after respiratory exacerbations are associated with elevated oxidative stress in cystic fibrosis patients
-
Wood LG, Fitzgerald DA, Gibson PG, Cooper DM, Garg ML (2002) Increased plasma fatty acid concentrations after respiratory exacerbations are associated with elevated oxidative stress in cystic fibrosis patients. The American journal of clinical nutrition 75: 668-675.
-
(2002)
The American journal of clinical nutrition
, vol.75
, pp. 668-675
-
-
Wood, L.G.1
Fitzgerald, D.A.2
Gibson, P.G.3
Cooper, D.M.4
Garg, M.L.5
-
72
-
-
0035002932
-
Oxidative stress in cystic fibrosis: Dietary and metabolic factors
-
Wood LG, Fitzgerald DA, Gibson PG, Cooper DM, Collins CE, et al. (2001) Oxidative stress in cystic fibrosis: dietary and metabolic factors. J Am Coll Nutr 20: 157-165.
-
(2001)
J Am Coll Nutr
, vol.20
, pp. 157-165
-
-
Wood, L.G.1
Fitzgerald, D.A.2
Gibson, P.G.3
Cooper, D.M.4
Collins, C.E.5
-
73
-
-
3042548715
-
Longitudinal study of oxidative status in 312 cystic fibrosis patients in stable state and during bronchial exacerbation
-
Lagrange-Puget M, Durieu I, Ecochard R, Abbas-Chorfa F, Drai J, et al. (2004) Longitudinal study of oxidative status in 312 cystic fibrosis patients in stable state and during bronchial exacerbation. Pediatric pulmonology 38: 43-49.
-
(2004)
Pediatric pulmonology
, vol.38
, pp. 43-49
-
-
Lagrange-Puget, M.1
Durieu, I.2
Ecochard, R.3
Abbas-Chorfa, F.4
Drai, J.5
-
74
-
-
0031006176
-
Simultaneous measurement of seven carotenoids, retinol and alpha-tocopherol in serum by high-performance liquid chromatography
-
Steghens JP, van Kappel AL, Riboli E, Collombel C (1997) Simultaneous measurement of seven carotenoids, retinol and alpha-tocopherol in serum by high-performance liquid chromatography. J Chromatogr B Biomed Sci Appl 694: 71-81.
-
(1997)
J Chromatogr B Biomed Sci Appl
, vol.694
, pp. 71-81
-
-
Steghens, J.P.1
van Kappel, A.L.2
Riboli, E.3
Collombel, C.4
|