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Volumn 298, Issue 15, 2007, Pages 1787-1793

Adult cystic fibrosis

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA TOCOPHEROL; ANTIBIOTIC AGENT; AZITHROMYCIN; AZTREONAM; CHLORIDE; COLISTIMETHATE; COTRIMOXAZOLE; DORNASE ALFA; INSULIN; MEROPENEM; RETINOL; SODIUM CHLORIDE; TOBRAMYCIN; TRANSMEMBRANE CONDUCTANCE REGULATOR; VITAMIN D; VITAMIN K GROUP;

EID: 35348961960     PISSN: 00987484     EISSN: 15383598     Source Type: Journal    
DOI: 10.1001/jama.298.15.1787     Document Type: Article
Times cited : (93)

References (43)
  • 1
    • 84965055013 scopus 로고
    • Respiratory function tests: Normal values at median altitudes and the prediction of normal results
    • Goldman HI, Becklake MR. Respiratory function tests: normal values at median altitudes and the prediction of normal results. Am Rev Tuberc. 1959;79(4):457-467.
    • (1959) Am Rev Tuberc , vol.79 , Issue.4 , pp. 457-467
    • Goldman, H.I.1    Becklake, M.R.2
  • 2
    • 0024423668 scopus 로고
    • Identification of the cystic fibrosis gene: Genetic analysis
    • Kerem B, Rommens JM, Buchanan JA, et al. Identification of the cystic fibrosis gene: genetic analysis. Science. 1989;245(4922):1073-1080.
    • (1989) Science , vol.245 , Issue.4922 , pp. 1073-1080
    • Kerem, B.1    Rommens, J.M.2    Buchanan, J.A.3
  • 3
    • 33846051977 scopus 로고    scopus 로고
    • Strategies for identifying modifier genes in cystic fibrosis
    • Boyle MP. Strategies for identifying modifier genes in cystic fibrosis. Proc Am Thorac Soc. 2007;4(1):52-57.
    • (2007) Proc Am Thorac Soc , vol.4 , Issue.1 , pp. 52-57
    • Boyle, M.P.1
  • 4
    • 0032433707 scopus 로고    scopus 로고
    • Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
    • Matsui H, Grubb BR, Tarran R, et al. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell. 1998;95(7):1005-1015.
    • (1998) Cell , vol.95 , Issue.7 , pp. 1005-1015
    • Matsui, H.1    Grubb, B.R.2    Tarran, R.3
  • 5
    • 0036258208 scopus 로고    scopus 로고
    • Cystic fibrosis: A worldwide analysis of CFTR mutations - correlation with incidence data and application to screening
    • Bobadilla JL, Macek M Jr, Fine JP, et al. Cystic fibrosis: a worldwide analysis of CFTR mutations - correlation with incidence data and application to screening. Hum Mutat. 2002;19(6):575-606.
    • (2002) Hum Mutat , vol.19 , Issue.6 , pp. 575-606
    • Bobadilla, J.L.1    Macek Jr, M.2    Fine, J.P.3
  • 6
    • 0031953194 scopus 로고    scopus 로고
    • Comparison of the clinical manifestations of cystic fibrosis in black and white patients
    • Hamosh A, Fitz-Simmons SC, Macek M Jr, et al. Comparison of the clinical manifestations of cystic fibrosis in black and white patients. J Pediatr. 1998;132(2):255-259.
    • (1998) J Pediatr , vol.132 , Issue.2 , pp. 255-259
    • Hamosh, A.1    Fitz-Simmons, S.C.2    Macek Jr, M.3
  • 7
    • 0003038952 scopus 로고    scopus 로고
    • Genetics, diagnosis, and clinical phenotype
    • Yankaskas JR, Knowles MR, eds, Philadelphia, PA: Lippincott-Raven;
    • Knowles MR, Friedman KJ, Silverman LM. Genetics, diagnosis, and clinical phenotype. In: Yankaskas JR, Knowles MR, eds. Cystic Fibrosis in Adults. Philadelphia, PA: Lippincott-Raven; 1999:27-42.
    • (1999) Cystic Fibrosis in Adults , pp. 27-42
    • Knowles, M.R.1    Friedman, K.J.2    Silverman, L.M.3
  • 8
    • 33750356035 scopus 로고    scopus 로고
    • Cystic Fibrosis Foundation, Bethesda, MD: Cystic Fibrosis Foundation;
    • Cystic Fibrosis Foundation. Patient Registry 2005 Annual Report. Bethesda, MD: Cystic Fibrosis Foundation; 2006.
    • (2006) Patient Registry 2005 Annual Report
  • 9
    • 35348979044 scopus 로고    scopus 로고
    • Cystic Fibrosis Worldwide. Annual Report 2005. Worcester, MA: Cystic Fibrosis Worldwide; 2006.
    • Cystic Fibrosis Worldwide. Annual Report 2005. Worcester, MA: Cystic Fibrosis Worldwide; 2006.
  • 10
    • 0031900652 scopus 로고    scopus 로고
    • Cystic Fibrosis Foundation Consensus Panel. The diagnosis of cystic fibrosis: A consensus statement
    • Rosenstein BJ, Cutting GR; Cystic Fibrosis Foundation Consensus Panel. The diagnosis of cystic fibrosis: a consensus statement. J Pediatr. 1998;132(4):589-595.
    • (1998) J Pediatr , vol.132 , Issue.4 , pp. 589-595
    • Rosenstein, B.J.1    Cutting, G.R.2
  • 11
    • 33745809841 scopus 로고    scopus 로고
    • Cystic fibrosis: Terminology and diagnostic algorithms
    • De Boeck K, Wilschanski M, Castellani C, et al. Cystic fibrosis: terminology and diagnostic algorithms. Thorax. 2006;61(7):627-635.
    • (2006) Thorax , vol.61 , Issue.7 , pp. 627-635
    • De Boeck, K.1    Wilschanski, M.2    Castellani, C.3
  • 12
    • 39049166110 scopus 로고    scopus 로고
    • Desax MC, Ammann RA, Hammer J, et al. Nanoduct(R) sweat testing for rapid diagnosis in newborns, infants and children with cystic fibrosis [published online April 14, 2007]. Eur J Pediatr. doi:10.1007/s00431-007-0485-0.
    • Desax MC, Ammann RA, Hammer J, et al. Nanoduct(R) sweat testing for rapid diagnosis in newborns, infants and children with cystic fibrosis [published online April 14, 2007]. Eur J Pediatr. doi:10.1007/s00431-007-0485-0.
  • 13
    • 0142074353 scopus 로고    scopus 로고
    • Nonclassic cystic fibrosis and CFTR-related diseases
    • Boyle MP. Nonclassic cystic fibrosis and CFTR-related diseases. Curr Opin Pulm Med. 2003;9(6): 498-503.
    • (2003) Curr Opin Pulm Med , vol.9 , Issue.6 , pp. 498-503
    • Boyle, M.P.1
  • 14
    • 0347301908 scopus 로고    scopus 로고
    • Yankaskas JR, Marshall BC, Sufian B, et al. Cystic fibrosis adult care: consensus conference report. Chest. 2004;125(1)(suppl):1S-39S.
    • Yankaskas JR, Marshall BC, Sufian B, et al. Cystic fibrosis adult care: consensus conference report. Chest. 2004;125(1)(suppl):1S-39S.
  • 15
    • 34247463796 scopus 로고    scopus 로고
    • Newborn screening for cystic fibrosis
    • Rock MJ. Newborn screening for cystic fibrosis. Clin Chest Med. 2007;28(2):297-305.
    • (2007) Clin Chest Med , vol.28 , Issue.2 , pp. 297-305
    • Rock, M.J.1
  • 16
    • 0026520359 scopus 로고
    • Prediction of mortality in patients with cystic fibrosis
    • Kerem E, Reisman J, Corey M, et al. Prediction of mortality in patients with cystic fibrosis. N Engl J Med. 1992;326(18):1187-1191.
    • (1992) N Engl J Med , vol.326 , Issue.18 , pp. 1187-1191
    • Kerem, E.1    Reisman, J.2    Corey, M.3
  • 17
    • 0037115262 scopus 로고    scopus 로고
    • Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality
    • Mayer-Hamblett N, Rosenfeld M, Emerson J, et al. Developing cystic fibrosis lung transplant referral criteria using predictors of 2-year mortality. Am J Respir Crit Care Med. 2002;166(12 pt 1):1550-1555.
    • (2002) Am J Respir Crit Care Med , vol.166 , Issue.12 PART 1 , pp. 1550-1555
    • Mayer-Hamblett, N.1    Rosenfeld, M.2    Emerson, J.3
  • 18
    • 85101247918 scopus 로고    scopus 로고
    • Testing lung function decline to time lung transplantation
    • Liou TG, Adler FR, Cahill BC. Testing lung function decline to time lung transplantation. Chest. 2005;128(1):472-473.
    • (2005) Chest , vol.128 , Issue.1 , pp. 472-473
    • Liou, T.G.1    Adler, F.R.2    Cahill, B.C.3
  • 19
    • 18144404644 scopus 로고    scopus 로고
    • Use of lung transplantation survival models to refine patient selection in cystic fibrosis
    • Liou TG, Adler FR, Huang D. Use of lung transplantation survival models to refine patient selection in cystic fibrosis. Am J Respir Crit Care Med. 2005;171(9):1053-1059.
    • (2005) Am J Respir Crit Care Med , vol.171 , Issue.9 , pp. 1053-1059
    • Liou, T.G.1    Adler, F.R.2    Huang, D.3
  • 20
    • 0035865730 scopus 로고    scopus 로고
    • Predictive 5-year survivorship model of cystic fibrosis
    • Liou TG, Adler FR, FitzSimmons SC, et al. Predictive 5-year survivorship model of cystic fibrosis. Am J Epidemiol. 2001;153(4):345-352.
    • (2001) Am J Epidemiol , vol.153 , Issue.4 , pp. 345-352
    • Liou, T.G.1    Adler, F.R.2    FitzSimmons, S.C.3
  • 21
    • 0142043977 scopus 로고    scopus 로고
    • Pathophysiology and management of pulmonary infections in cystic fibrosis
    • Gibson RL, Burns JL, Ramsey BW. Pathophysiology and management of pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med. 2003;168(8):918-951.
    • (2003) Am J Respir Crit Care Med , vol.168 , Issue.8 , pp. 918-951
    • Gibson, R.L.1    Burns, J.L.2    Ramsey, B.W.3
  • 22
    • 0346552843 scopus 로고    scopus 로고
    • Airway clearance techniques
    • Flume PA. Airway clearance techniques. Semin Respir Crit Care Med. 2003;24(6):727-736.
    • (2003) Semin Respir Crit Care Med , vol.24 , Issue.6 , pp. 727-736
    • Flume, P.A.1
  • 23
    • 0028129568 scopus 로고
    • Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
    • Fuchs HJ, Borowitz DS, Christiansen DH, et al; Pulmozyme Study Group. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. N Engl J Med. 1994;331(10):637-642.
    • (1994) N Engl J Med , vol.331 , Issue.10 , pp. 637-642
    • Fuchs, H.J.1    Borowitz, D.S.2    Christiansen, D.H.3
  • 24
    • 30944452384 scopus 로고    scopus 로고
    • Mucus clearance and lung function in cystic fibrosis with hypertonic saline
    • Donaldson SH, Bennett WD, Zeman KL, et al. Mucus clearance and lung function in cystic fibrosis with hypertonic saline. N Engl J Med. 2006;354(3):241-250.
    • (2006) N Engl J Med , vol.354 , Issue.3 , pp. 241-250
    • Donaldson, S.H.1    Bennett, W.D.2    Zeman, K.L.3
  • 25
    • 30944466084 scopus 로고    scopus 로고
    • A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
    • Elkins MR, Robinson M, Rose BR, et al. A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. N Engl J Med. 2006;354(3):229-240.
    • (2006) N Engl J Med , vol.354 , Issue.3 , pp. 229-240
    • Elkins, M.R.1    Robinson, M.2    Rose, B.R.3
  • 26
    • 0033531143 scopus 로고    scopus 로고
    • Cystic Fibrosis Inhaled Tobramycin Study Group. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis
    • Ramsey BW, Pepe MS, Quan JM, et al; Cystic Fibrosis Inhaled Tobramycin Study Group. Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. N Engl J Med. 1999;340(1):23-30.
    • (1999) N Engl J Med , vol.340 , Issue.1 , pp. 23-30
    • Ramsey, B.W.1    Pepe, M.S.2    Quan, J.M.3
  • 27
    • 34247531384 scopus 로고    scopus 로고
    • Macrolides in cystic fibrosis
    • McArdle JR, Talwalkar JS. Macrolides in cystic fibrosis. Clin Chest Med. 2007;28(2):347-360.
    • (2007) Clin Chest Med , vol.28 , Issue.2 , pp. 347-360
    • McArdle, J.R.1    Talwalkar, J.S.2
  • 28
    • 0037245866 scopus 로고    scopus 로고
    • So many drugs, so little time: The future challenge of cystic fibrosis care
    • Boyle MP. So many drugs, so little time: the future challenge of cystic fibrosis care. Chest. 2003;123(1):3-5.
    • (2003) Chest , vol.123 , Issue.1 , pp. 3-5
    • Boyle, M.P.1
  • 29
    • 0035814353 scopus 로고    scopus 로고
    • Survival effect of lung transplantation among patients with cystic fibrosis
    • Liou TG, Adler FR, Cahill BC, et al. Survival effect of lung transplantation among patients with cystic fibrosis. JAMA. 2001;286(21):2683-2689.
    • (2001) JAMA , vol.286 , Issue.21 , pp. 2683-2689
    • Liou, T.G.1    Adler, F.R.2    Cahill, B.C.3
  • 30
    • 27644445124 scopus 로고    scopus 로고
    • Update on the Burkholderia cepacia complex
    • Lipuma JJ. Update on the Burkholderia cepacia complex. Curr Opin Pulm Med. 2005;11(6):528-533.
    • (2005) Curr Opin Pulm Med , vol.11 , Issue.6 , pp. 528-533
    • Lipuma, J.J.1
  • 31
    • 0037820620 scopus 로고    scopus 로고
    • Saiman L, Siegel J; Cystic Fibrosis Foundation Consensus Conference on Infection Control Participants. Infection control recommendations for patients with cystic fibrosis: microbiology, important pathogens, and infection control practices to prevent patient-to-patient transmission. Am J Infect Control. 2003;31(3 suppl):S1-S62.
    • Saiman L, Siegel J; Cystic Fibrosis Foundation Consensus Conference on Infection Control Participants. Infection control recommendations for patients with cystic fibrosis: microbiology, important pathogens, and infection control practices to prevent patient-to-patient transmission. Am J Infect Control. 2003;31(3 suppl):S1-S62.
  • 32
    • 34548048797 scopus 로고    scopus 로고
    • incidence and risk factors for multiple antibiotic-resistant Pseudomonas aeruginosa in cystic fibrosis
    • Merlo CA, Boyle MP, Diener-West M, et al. incidence and risk factors for multiple antibiotic-resistant Pseudomonas aeruginosa in cystic fibrosis. Chest. 2007;132(2):562-568.
    • (2007) Chest , vol.132 , Issue.2 , pp. 562-568
    • Merlo, C.A.1    Boyle, M.P.2    Diener-West, M.3
  • 33
    • 0037445273 scopus 로고    scopus 로고
    • Non-tuberculous mycobacteria, I: Multicenter prevalence study in cystic fibrosis
    • Olivier KN, Weber DJ, Wallace RJ Jr, et al. Non-tuberculous mycobacteria, I: multicenter prevalence study in cystic fibrosis. Am J Respir Crit Care Med. 2003;167(6):828-834.
    • (2003) Am J Respir Crit Care Med , vol.167 , Issue.6 , pp. 828-834
    • Olivier, K.N.1    Weber, D.J.2    Wallace Jr, R.J.3
  • 34
    • 0141956255 scopus 로고    scopus 로고
    • Allergic bronchopulmonary aspergillosis in cystic fibrosis-state of the art: Cystic fibrosis foundation consensus conference
    • 37(suppl 3):S
    • Stevens DA, Moss RB, Kurup VP, et al. Allergic bronchopulmonary aspergillosis in cystic fibrosis-state of the art: cystic fibrosis foundation consensus conference. Clin Infect Dis. 2003;37(suppl 3):S225-S264.
    • (2003) Clin Infect Dis
    • Stevens, D.A.1    Moss, R.B.2    Kurup, V.P.3
  • 35
    • 0036735017 scopus 로고    scopus 로고
    • Consensus report on nutrition for pediatric patients with cystic fibrosis
    • Borowitz D, Baker RD, Stallings V. Consensus report on nutrition for pediatric patients with cystic fibrosis. J Pediatr Gastroenterol Nutr. 2002;35(3):246-259.
    • (2002) J Pediatr Gastroenterol Nutr , vol.35 , Issue.3 , pp. 246-259
    • Borowitz, D.1    Baker, R.D.2    Stallings, V.3
  • 36
    • 33750291829 scopus 로고    scopus 로고
    • Classification of nutritional status in cystic fibrosis
    • Lai HJ. Classification of nutritional status in cystic fibrosis. Curr Opin Pulm Med. 2006;12(6):422-427.
    • (2006) Curr Opin Pulm Med , vol.12 , Issue.6 , pp. 422-427
    • Lai, H.J.1
  • 37
    • 0032783588 scopus 로고    scopus 로고
    • Diagnosis, screening and management of cystic fibrosis related diabetes mellitus: A consensus conference report
    • 61-73
    • Moran A, Hardin D, Rodman D, et al. Diagnosis, screening and management of cystic fibrosis related diabetes mellitus: a consensus conference report. Diabetes Res Clin Pract. 1999;45(1):61-73.
    • (1999) Diabetes Res Clin Pract , vol.45 , Issue.1
    • Moran, A.1    Hardin, D.2    Rodman, D.3
  • 38
    • 18144377758 scopus 로고    scopus 로고
    • Epidemiology of cystic fibrosis-related diabetes
    • Marshall BC, Butler SM, Stoddard M, et al. Epidemiology of cystic fibrosis-related diabetes. J Pediatr. 2005;146(5):681-687.
    • (2005) J Pediatr , vol.146 , Issue.5 , pp. 681-687
    • Marshall, B.C.1    Butler, S.M.2    Stoddard, M.3
  • 39
    • 33750306258 scopus 로고    scopus 로고
    • Update on maintaining bone health in cystic fibrosis
    • Boyle MP. Update on maintaining bone health in cystic fibrosis. Curr Opin Pulm Med. 2006;12(6):453-458.
    • (2006) Curr Opin Pulm Med , vol.12 , Issue.6 , pp. 453-458
    • Boyle, M.P.1
  • 40
    • 33645111299 scopus 로고    scopus 로고
    • Impact of pregnancy on women with cystic fibrosis
    • McMullen AH, Pasta DJ, Frederick PD, et al. Impact of pregnancy on women with cystic fibrosis. Chest. 2006;129(3):706-711.
    • (2006) Chest , vol.129 , Issue.3 , pp. 706-711
    • McMullen, A.H.1    Pasta, D.J.2    Frederick, P.D.3
  • 41
    • 0033931136 scopus 로고    scopus 로고
    • Pregnancy in cystic fibrosis: Fetal and maternal outcome
    • Gilljam M, Antoniou M, Shin J, et al. Pregnancy in cystic fibrosis: fetal and maternal outcome. Chest. 2000;118(1):85-91.
    • (2000) Chest , vol.118 , Issue.1 , pp. 85-91
    • Gilljam, M.1    Antoniou, M.2    Shin, J.3
  • 42
    • 5644250620 scopus 로고    scopus 로고
    • CFTR mutations and polymorphisms in male infertility
    • Cuppens H, Cassiman JJ. CFTR mutations and polymorphisms in male infertility. Int J Androl. 2004;27(5):251-256.
    • (2004) Int J Androl , vol.27 , Issue.5 , pp. 251-256
    • Cuppens, H.1    Cassiman, J.J.2
  • 43
    • 0032480346 scopus 로고    scopus 로고
    • Relation between mutations of the cystic fibrosis gene and idiopathic pancreatitis
    • Cohn JA, Friedman KJ, Noone PG, et al. Relation between mutations of the cystic fibrosis gene and idiopathic pancreatitis. N Engl J Med. 1998;339(10):653-658.
    • (1998) N Engl J Med , vol.339 , Issue.10 , pp. 653-658
    • Cohn, J.A.1    Friedman, K.J.2    Noone, P.G.3


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