Protective protein/cathepsin A rescues N-glycosylation defects in neuraminidase-1

Biochimica et Biophysica Acta - General Subjects

Volumn 1790, Issue 4, 2009, Pages 275-282

  Wang, Dongning ^a   Zaitsev, Slava ^b   Taylor, Garry ^b   d'Azzo, Alessandra ^a   Bonten, Erik ^a  

^a ST JUDE CHILDREN S RESEARCH HOSPITAL   (United States)

^b UNIVERSITY OF ST ANDREWS   (United Kingdom)

Author keywords

Chaperone therapy; Glycosylation; NEU1; Neuraminidase; Protective protein cathepsin A; Sialidase; Sialidosis

Indexed keywords

CARBOXYPEPTIDASE C; SIALIDASE;

AMINO ACID SEQUENCE; ANIMAL CELL; ANIMAL CELL CULTURE; ARTICLE; CARBOXY TERMINAL SEQUENCE; CATALYSIS; CONTROLLED STUDY; ENDOSOME; GENE DELETION; HUMAN; HUMAN CELL; HUMAN CELL CULTURE; LUNG FIBROBLAST; LYSOSOME; MISSENSE MUTATION; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN GLYCOSYLATION; PROTEIN STRUCTURE; SIALIDOSIS; SITE DIRECTED MUTAGENESIS; UPREGULATION;

ANIMALS; CARBOXYPEPTIDASE C; GLYCOSYLATION; HUMANS; MICE; MODELS, MOLECULAR; MUCOLIPIDOSES; MUTATION, MISSENSE; NEURAMINIDASE; POINT MUTATION; SEQUENCE HOMOLOGY, AMINO ACID;

MURINAE;

EID: 61749086125     PISSN: 03044165     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbagen.2009.01.006     Document Type: Article

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