Molecular basis of ADAMTS13 dysfunction in thrombotic thrombocytopenic purpura

Pediatric Nephrology

Volumn 24, Issue 3, 2009, Pages 447-458

  Manea, Minola ^a   Karpman, Diana ^a  

^a LUND UNIVERSITY   (Sweden)

Author keywords

ADAMTS13; Kidney; Plasma; Podocytes; Thrombotic thrombocytopenic purpura

Indexed keywords

AUTOANTIBODY; FRESH FROZEN PLASMA; RITUXIMAB; VON WILLEBRAND FACTOR; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

AUTOSOMAL RECESSIVE DISORDER; BLOOD TRANSFUSION; CLINICAL FEATURE; DIFFERENTIAL DIAGNOSIS; GENE MUTATION; GENETIC ASSOCIATION; HEMOLYTIC UREMIC SYNDROME; HISTOPATHOLOGY; HUMAN; NONHUMAN; PATHOPHYSIOLOGY; PLASMAPHERESIS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN DEGRADATION; PROTEIN DETERMINATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; PROTEIN STRUCTURE; REVIEW; RISK FACTOR; SPLENECTOMY; THROMBOGENESIS; THROMBOTIC THROMBOCYTOPENIC PURPURA;

ADAM PROTEINS; DIAGNOSIS, DIFFERENTIAL; HUMANS; MUTATION; PURPURA, THROMBOTIC THROMBOCYTOPENIC; VON WILLEBRAND FACTOR;

EID: 59849115176     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-008-0986-8     Document Type: Review

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