-
1
-
-
0022517442
-
Subunit composition of plasma von Willebrand factor. Cleavage is present in normal individuals, increased in type IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE)
-
Zimmerman TS, Dent JA, Ruggeri ZM, Nannini LH. Subunit composition of plasma von Willebrand Factor. Cleavage is present in normal individuals, increased in type IIA and IIB von Willebrand disease, but minimal in variants with aberrant structure of individual oligomers (types IIC, IID, and IIE). J Clin Invest 1986; 77: 947-51.
-
(1986)
J Clin Invest
, vol.77
, pp. 947-951
-
-
Zimmerman, T.S.1
Dent, J.A.2
Ruggeri, Z.M.3
Nannini, L.H.4
-
2
-
-
0025044664
-
Identification of a cleavage site directing the immunochemical detection of molecular abnormalities in type IIA von Willebrand factor
-
Dent JA, Berkowitz SD, Ware J, Kasper CK, Ruggeri ZM. Identification of a cleavage site directing the immunochemical detection of molecular abnormalities in type IIA von Willebrand factor. Proc Natl Acad Sci USA 1990; 87: 6306-10.
-
(1990)
Proc Natl Acad Sci USA
, vol.87
, pp. 6306-6310
-
-
Dent, J.A.1
Berkowitz, S.D.2
Ware, J.3
Kasper, C.K.4
Ruggeri, Z.M.5
-
3
-
-
0029925856
-
Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis
-
Furlan M, Robles R, Lammle B. Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis. Blood 1996; 87: 4223-34.
-
(1996)
Blood
, vol.87
, pp. 4223-4234
-
-
Furlan, M.1
Robles, R.2
Lammle, B.3
-
4
-
-
0029878123
-
Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion
-
Tsai HM. Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion. Blood 1996; 87: 4235-44.
-
(1996)
Blood
, vol.87
, pp. 4235-4244
-
-
Tsai, H.M.1
-
5
-
-
0024356269
-
Multimeric composition of endothelial cell-derived von Willebrand factor
-
Tsai HM, Nagel RL, Hatcher VB, Sussman II. Multimeric composition of endothelial cell-derived von Willebrand factor. Blood 1989; 73: 2074-6.
-
(1989)
Blood
, vol.73
, pp. 2074-2076
-
-
Tsai, H.M.1
Nagel, R.L.2
Hatcher, V.B.3
Sussman, I.I.4
-
6
-
-
0031873311
-
Thrombotic thrombocytopenic purpura: Understanding a disease no longer rare
-
Moake JL, Chow TW. Thrombotic thrombocytopenic purpura: Understanding a disease no longer rare. Am J Med Sci 1998; 316: 105-19.
-
(1998)
Am J Med Sci
, vol.316
, pp. 105-119
-
-
Moake, J.L.1
Chow, T.W.2
-
7
-
-
0032569840
-
Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura
-
Tsai HM, Lian ECY. Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura. N Engl J Med 1998; 339: 1585-94.
-
(1998)
N Engl J Med
, vol.339
, pp. 1585-1594
-
-
Tsai, H.M.1
Lian, E.C.Y.2
-
8
-
-
0032569884
-
Von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome
-
Furlan M, Robles R, Galbusera M, Remuzzi G, Kyrle PA, Brenner B, Krause M, Scharrer I, Aumann V, Mittler U, Solenthaler M, Lammle B. Von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and the hemolytic-uremic syndrome. N Engl J Med 1998; 339: 1578-84.
-
(1998)
N Engl J Med
, vol.339
, pp. 1578-1584
-
-
Furlan, M.1
Robles, R.2
Galbusera, M.3
Remuzzi, G.4
Kyrle, P.A.5
Brenner, B.6
Krause, M.7
Scharrer, I.8
Aumann, V.9
Mittler, U.10
Solenthaler, M.11
Lammle, B.12
-
9
-
-
0030973267
-
Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocylopenic purpura
-
Furlan M, Robles R, Solenthaler M, Wassmer M, Sandoz P, Lammle B. Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocylopenic purpura. Blood 1997; 89: 3097-103.
-
(1997)
Blood
, vol.89
, pp. 3097-3103
-
-
Furlan, M.1
Robles, R.2
Solenthaler, M.3
Wassmer, M.4
Sandoz, P.5
Lammle, B.6
-
10
-
-
0032522952
-
Acquired deficiency of von Willebrand factor-cleaving protease in a patient with thrombolic thrombocytopenic purpura
-
Furlan M, Robles R, Solenthaler M, Lammle B. Acquired deficiency of von Willebrand factor-cleaving protease in a patient with thrombolic thrombocytopenic purpura. Blood 1998; 91: 2839-46.
-
(1998)
Blood
, vol.91
, pp. 2839-2846
-
-
Furlan, M.1
Robles, R.2
Solenthaler, M.3
Lammle, B.4
-
11
-
-
0020428664
-
Unusually large plasma factor VIII: Von Willebrand factor multimers in chronic relapsing thombotic thrombocytopenic purpura
-
Moake JL, Rudy CK, Troll JH, Weinstein MJ, Colannino NM, Azocar J, Seder RH, Hong SL, Deykin D. Unusually large plasma factor VIII: von Willebrand factor multimers in chronic relapsing thombotic thrombocytopenic purpura. N Engl J Med 1982; 307: 1432-5.
-
(1982)
N Engl J Med
, vol.307
, pp. 1432-1435
-
-
Moake, J.L.1
Rudy, C.K.2
Troll, J.H.3
Weinstein, M.J.4
Colannino, N.M.5
Azocar, J.6
Seder, R.H.7
Hong, S.L.8
Deykin, D.9
-
12
-
-
0028201807
-
A revised classification of von Willebrand disease
-
Sadler JE. A revised classification of von Willebrand disease. Thromb Haemost 1994; 71: 520-5.
-
(1994)
Thromb Haemost
, vol.71
, pp. 520-525
-
-
Sadler, J.E.1
-
13
-
-
0026630044
-
Impaired intracellular transport produced by a subset of type-IIA von Willebrand disease mutations
-
Lyons SE, Bruck ME, Bowie EJW, Ginsburg D. Impaired intracellular transport produced by a subset of type-IIA von Willebrand disease mutations. J Biol Chem 1992; 267: 4424-30.
-
(1992)
J Biol Chem
, vol.267
, pp. 4424-4430
-
-
Lyons, S.E.1
Bruck, M.E.2
Bowie, E.J.W.3
Ginsburg, D.4
-
14
-
-
0026457996
-
Characterization of recombinant von Willebrand factor corresponding to mutations in type-IIA and type-IIB von Willebrand disease
-
Ribba AS, Voorberg J, Meyer D, Pannekoek H, Pietu G. Characterization of recombinant von Willebrand Factor corresponding to mutations in Type-IIA and Type-IIB von Willebrand disease. J Biol Chem 1992; 267: 23209-15.
-
(1992)
J Biol Chem
, vol.267
, pp. 23209-23215
-
-
Ribba, A.S.1
Voorberg, J.2
Meyer, D.3
Pannekoek, H.4
Pietu, G.5
-
15
-
-
0030980679
-
Proteolytic cleavage of recombinant type 2A von Willebrand factor mutants R834W and R834Q: Inhibition by doxycycline and by monoclonal antibody VP-1
-
Tsai HM, Sussman II, Ginsburg D, Lankhof H, Sixma JJ, Nagel RL. Proteolytic cleavage of recombinant type 2A von Willebrand factor mutants R834W and R834Q: Inhibition by doxycycline and by monoclonal antibody VP-1. Blood 1997; 89: 1954-62.
-
(1997)
Blood
, vol.89
, pp. 1954-1962
-
-
Tsai, H.M.1
Sussman, I.I.2
Ginsburg, D.3
Lankhof, H.4
Sixma, J.J.5
Nagel, R.L.6
-
16
-
-
0033151555
-
Von Willebrand factor proteolysis is deficient in classic, but not in bone marrow transplantation-associated, thrombotic thrombocytopenic purpura
-
van der Plas RM, Schiphorst ME, Huizinga EG, Hene RJ, Verdonck LF, Sixma JJ, Fijnheer R, von Willebrand factor proteolysis is deficient in classic, but not in bone marrow transplantation-associated, thrombotic thrombocytopenic purpura. Blood 1999; 93: 3798-802.
-
(1999)
Blood
, vol.93
, pp. 3798-3802
-
-
Van Der Plas, R.M.1
Schiphorst, M.E.2
Huizinga, E.G.3
Hene, R.J.4
Verdonck, L.F.5
Sixma, J.J.6
Fijnheer, R.7
-
17
-
-
0024425034
-
New variant of von Willebrand disease with defective binding to factor VIII
-
Nishino M, Girma JP, Rothschild C, Fressinaud E, Meyer D. New variant of von Willebrand disease with defective binding to Factor VIII. Blood 1989; 5: 1591-9.
-
(1989)
Blood
, vol.5
, pp. 1591-1599
-
-
Nishino, M.1
Girma, J.P.2
Rothschild, C.3
Fressinaud, E.4
Meyer, D.5
-
18
-
-
0021184617
-
Hybridoma antibodies to human von Willebrand factor. I. Characterization of seven clones
-
Meyer D, Zimmerman TS, Obert B, Edgington TS. Hybridoma antibodies to human von Willebrand Factor. I. Characterization of seven clones. Br J Haematol 1984; 57: 597-608.
-
(1984)
Br J Haematol
, vol.57
, pp. 597-608
-
-
Meyer, D.1
Zimmerman, T.S.2
Obert, B.3
Edgington, T.S.4
-
19
-
-
0017874586
-
Protein and cell membrane iodinations with a sparingly soluble chloroamide, 1, 3, 4, 6- tetrachloro-3a, 6a- diphenylglycoluril
-
Fraker PJ, Speck JC. Protein and cell membrane iodinations with a sparingly soluble chloroamide, 1, 3, 4, 6- tetrachloro-3a, 6a- diphenylglycoluril. Biochem Biophys Res Commun 1978; 80: 849-57.
-
(1978)
Biochem Biophys Res Commun
, vol.80
, pp. 849-857
-
-
Fraker, P.J.1
Speck, J.C.2
-
20
-
-
0033559304
-
Conformational changes in the A3 domain of von Willebrand factor modulate the interaction of the A1 domain with platelet glycoprotein Ib
-
Obert B, Houllier A, Meyer D, Girma JP. Conformational changes in the A3 domain of von Willebrand Factor modulate the interaction of the A1 domain with platelet glycoprotein Ib. Blood 1999; 93: 1959-68.
-
(1999)
Blood
, vol.93
, pp. 1959-1968
-
-
Obert, B.1
Houllier, A.2
Meyer, D.3
Girma, J.P.4
-
21
-
-
0019442145
-
The complex multimeric composition of factor VIII/von Willebrand factor
-
Ruggeri ZM, Zimmerman TS. The complex multimeric composition of Factor VIII/von Willebrand Factor. Blood 1981; 57: 1140-3.
-
(1981)
Blood
, vol.57
, pp. 1140-1143
-
-
Ruggeri, Z.M.1
Zimmerman, T.S.2
|