The PHEX transgene corrects mineralization defects in 9-month-old hypophosphatemic mice

Calcified Tissue International

Volumn 84, Issue 2, 2009, Pages 126-137

  Boskey, Adele ^a   Frank, Aaron ^a   Fujimoto, Yukiji ^a   Spevak, Lyudmila ^a   Verdelis, Kostas ^a   Ellis, Bruce ^b   Troiano, Nancy ^b   Philbrick, William ^b   Carpenter, Thomas ^b  

^a HOSPITAL FOR SPECIAL SURGERY   (United States)

^b YALE UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

FT IR; Hypophosphatemic rickets; Mineralization; PHEX; X ray diffraction

Indexed keywords

ALKALINE PHOSPHATASE; CARBONIC ACID; COLLAGEN TYPE 1; FIBROBLAST GROWTH FACTOR 23; PHOSPHATE; PHOSPHATE REGULATING NEUTRAL ENDOPEPTIDASE;

ANIMAL TISSUE; ARTICLE; BLOOD CHEMISTRY; BONE MINERALIZATION; CONTROLLED STUDY; ENZYME ACTIVITY; FEMALE; GENE EXPRESSION; HUMERUS; HYPOPHOSPHATEMIA; INFRARED SPECTROSCOPY; MALE; MICRO-COMPUTED TOMOGRAPHY; MINERAL DEFICIENCY; MOLAR TOOTH; MORPHOMETRICS; MOUSE; NONHUMAN; OSTEOBLAST; PHENOTYPE; PHOSPHATE BLOOD LEVEL; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN BLOOD LEVEL; SEX DIFFERENCE; TIBIA; TRANSGENE; WILD TYPE; X RAY DIFFRACTION;

ANIMALS; BONE DENSITY; CALCIFICATION, PHYSIOLOGIC; DISEASE MODELS, ANIMAL; FEMALE; HYPOPHOSPHATEMIA; MALE; MICE; MICE, TRANSGENIC; OSTEOMALACIA; PHEX PHOSPHATE REGULATING NEUTRAL ENDOPEPTIDASE; SPECTROSCOPY, FOURIER TRANSFORM INFRARED; TRANSGENES; X-RAY DIFFRACTION;

EID: 59449106235     PISSN: 0171967X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00223-008-9201-y     Document Type: Article

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