Atp7b-/- mice as a model for studies of Wilson's disease

Biochemical Society Transactions

Volumn 36, Issue 6, 2008, Pages 1233-1238

  Lutsenko, Svetlana ^a  

^a OREGON HEALTH AND SCIENCE UNIVERSITY   (United States)

Author keywords

ATP7A; ATP7B; Copper; Liver; Mouse model; Wilson's disease

Indexed keywords

CERULOPLASMIN; COPPER; COPPER EXPORTING ADENOSINE TRIPHOSPHATASE; MESSENGER RNA; ADENOSINE TRIPHOSPHATASE; CATION TRANSPORT PROTEIN; WILSON DISEASE PROTEIN;

CLINICAL FEATURE; COPPER BLOOD LEVEL; DIAGNOSTIC TEST; DISEASE COURSE; DISEASE MODEL; GENE MUTATION; HUMAN; KNOCKOUT MOUSE; LIVER DISEASE; METAL METABOLISM; MOUSE STRAIN; NERVE DEGENERATION; NONHUMAN; ONSET AGE; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN FUNCTION; REVIEW; SPECIES DIFFERENCE; TRANSPORT KINETICS; URINE LEVEL; WILSON DISEASE; ANIMAL; BLOOD; METABOLISM; MOUSE; URINE;

ANIMALIA; MUS;

ADENOSINE TRIPHOSPHATASES; ANIMALS; CATION TRANSPORT PROTEINS; COPPER; DISEASE MODELS, ANIMAL; HEPATOLENTICULAR DEGENERATION; MICE;

EID: 59149094700     PISSN: 03005127     EISSN: 14708752     Source Type: Journal    
DOI: 10.1042/BST0361233     Document Type: Review

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