The Long-Evans Cinnamon rat: An animal model for Wilson's disease

Pediatrics International

Volumn 41, Issue 4, 1999, Pages 414-418

  Terada, Kunihiko ^a   Sugiyama, Toshihiro ^a  

^a AKITA UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

ATP7B; Ceruloplasmin; Copper transport; Golgi apparatus; Long Evans Cinnamon rat

Indexed keywords

CERULOPLASMIN; COPPER;

ANIMAL EXPERIMENT; ANIMAL MODEL; BILIARY EXCRETION; CERULOPLASMIN BLOOD LEVEL; CLINICAL FEATURE; CONTROLLED STUDY; COPPER BLOOD LEVEL; COPPER METABOLISM; GENE EXPRESSION; GENE MUTATION; INTRACELLULAR TRANSPORT; NONHUMAN; PATHOPHYSIOLOGY; PRIORITY JOURNAL; RAT; REVIEW; WILSON DISEASE;

ADENOSINE TRIPHOSPHATASES; ANIMALS; CARRIER PROTEINS; CATION TRANSPORT PROTEINS; CELL FRACTIONATION; COPPER; DISEASE MODELS, ANIMAL; GOLGI APPARATUS; HEPATOLENTICULAR DEGENERATION; LIVER; RATS; RATS, INBRED LEC;

EID: 0032806774     PISSN: 13288067     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1442-200x.1999.01089.x     Document Type: Review

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