RAGE signaling contributes to neuroinflammation in infantile neuronal ceroid lipofuscinosis

FEBS Letters

Volumn 582, Issue 27, 2008, Pages 3823-3831

  Saha, Arjun ^a   Kim, Sung Jo ^a   Zhang, Zhongjian ^a   Lee, Yi Ching ^a   Sarkar, Chinmoy ^a   Tsai, Pei Chih ^a   Mukherjee, Anil B ^a  

^a EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

Batten disease; Infantile neuronal ceroid lipofuscinosis; Neurodegeneration; Neuroinflammation; Palmitoyl protein thioesterase 1

Indexed keywords

ADVANCED GLYCATION END PRODUCT RECEPTOR; PALMITOYL PROTEIN THIOESTERASE; PALMITOYL PROTEIN THIOESTERASE 1; PROTEIN S100B; SMALL INTERFERING RNA; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; ASTROCYTE; CONTROLLED STUDY; CYTOKINE PRODUCTION; ENCEPHALITIS; HUMAN; HUMAN TISSUE; MOUSE; NERVE DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN SECRETION; SIGNAL TRANSDUCTION;

ANIMALS; APOPTOSIS; ASTROCYTES; BRAIN; CYTOKINES; ENCEPHALITIS; HUMANS; MICE; MICE, KNOCKOUT; MITOGEN-ACTIVATED PROTEIN KINASE KINASES; NERVE GROWTH FACTORS; NEURONAL CEROID-LIPOFUSCINOSES; NF-KAPPA B; RECEPTORS, IMMUNOLOGIC; RNA, SMALL INTERFERING; S100 PROTEINS; SIGNAL TRANSDUCTION; SRC-FAMILY KINASES; THIOLESTER HYDROLASES;

EID: 54849432622     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.febslet.2008.10.015     Document Type: Article

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