Insights into post-translational processing of β-galactosidase in an animal model resembling late infantile human GM1-gangliosidosis

Journal of Cellular and Molecular Medicine

Volumn 12, Issue 5A, 2008, Pages 1661-1671

  Kreutzer, R ^a   Kreutzer, M ^a   Propsting M J ^a   Sewell, A C ^b   Leeb, T ^c   Naim, H Y ^a   Baumgartner W ^a  

^a UNIVERSITY OF VETERINARY MEDICINE HANNOVER   (Germany)

^b UNIVERSITY HOSPITAL FRANKFURT   (Germany)

^c UNIVERSITY OF BERN   (Switzerland)

Author keywords

galactosidase; Animal model; GM1 gangliosidosis; Post translational processing

Indexed keywords

BETA GALACTOSIDASE;

ANIMAL; ARTICLE; CELL CULTURE; DISEASE MODEL; DOG; ENZYMOLOGY; GENETICS; GM1 GANGLIOSIDOSIS; HUMAN; METABOLISM; MUTATION; PATHOLOGY; PROTEIN PROCESSING; TRANSGENIC ANIMAL;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BETA-GALACTOSIDASE; CELLS, CULTURED; DISEASE MODELS, ANIMAL; DOGS; GANGLIOSIDOSIS, GM1; HUMANS; MUTATION; PROTEIN PROCESSING, POST-TRANSLATIONAL;

ANIMALIA;

EID: 54049118799     PISSN: 15821838     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.1582-4934.2007.00204.x     Document Type: Article

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