GM1-ganglioside degradation and biosynthesis in human and murine GM1-gangliosidosis

Clinica Chimica Acta

Volumn 354, Issue 1-2, 2005, Pages 131-139

  Sano, Renata ^a,b,c   Trindade, Vera M T ^a   Tessitore, Alessandra ^c   D'Azzo, Alessandra ^c   Vieira, Matheus B ^a,b   Giugliani, Roberto ^a,b   Coelho, Janice C ^a,b  

^a FEDERAL UNIVERSITY OF RIO GRANDE DO SUL   (Brazil)

^b HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^c ST JUDE CHILDREN S RESEARCH HOSPITAL   (United States)

Author keywords

Acid galactosidase; GM1 synthase; GM1 ganglioside; GM1 gangliosidosis

Indexed keywords

ENZYME; GANGLIOSIDE; GANGLIOSIDE GM1; GANGLIOSIDE GM1 SYNTHASE; N ACETYLNEURAMINIC ACID; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BIOSYNTHESIS; CONTROLLED STUDY; DISEASE MODEL; ENZYME ACTIVITY; ENZYME ASSAY; ENZYME INHIBITION; GM1 GANGLIOSIDOSIS; HUMAN; HUMAN CELL; HUMAN TISSUE; INHIBITION KINETICS; LIPID DEGRADATION; LIPOGENESIS; NONHUMAN; PRIORITY JOURNAL; QUALITATIVE ANALYSIS; QUANTITATIVE ANALYSIS; REGULATORY MECHANISM; THIN LAYER CHROMATOGRAPHY;

EID: 14644394856     PISSN: 00098981     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.cccn.2004.11.035     Document Type: Article

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