Early proteolytic cleavage with loss of a C-terminal fragment underlies altered processing of the β-galactosidase precursor in galactosialidosis

Biochemical Journal

Volumn 313, Issue 3, 1996, Pages 787-794

  Okamura Oho, Yuko ^a,d   Zhang, Sunqu ^a   Hilson, William ^a   Hinek, Aleksander ^a,c   Callahan, John W ^a,b,c  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

^c UNIVERSITY OF TORONTO   (Canada)

^d TOKYO METROPOLITAN INSTITUTE OF MEDICAL SCIENCE   (Japan)

Author keywords

[No Author keywords available]

Indexed keywords

AMMONIUM CHLORIDE; BETA GALACTOSIDASE; ENZYME PRECURSOR; LEUPEPTIN;

ADULT; ANIMAL CELL; ARTICLE; CARBOXY TERMINAL SEQUENCE; CASE REPORT; CHO CELL; CONTROLLED STUDY; ENZYME DEFICIENCY; FEMALE; FIBROBLAST; GALACTOSIALIDOSIS; GENETIC TRANSFECTION; GM1 GANGLIOSIDOSIS; HUMAN; HUMAN CELL; MALE; NONHUMAN; PRIORITY JOURNAL; PROTEIN DEGRADATION; PROTEIN PROCESSING; SCHOOL CHILD;

ANIMALIA; CRICETINAE; CRICETULUS GRISEUS;

EID: 0030061648     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/bj3130787     Document Type: Article

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