-
1
-
-
0002362896
-
Molecular aspects of carbamoyl phosphate synthetase
-
In: Walsh PJ, Wright P, eds. Boca Raton, FL: CRC Press
-
Anderson PM (1995) Molecular aspects of carbamoyl phosphate synthetase. In: Walsh PJ, Wright P, eds. Nitrogen Metabolism and Excretion. Boca Raton, FL: CRC Press, 33-49.
-
(1995)
Nitrogen Metabolism and Excretion
, pp. 33-49
-
-
Anderson, P.M.1
-
2
-
-
0013957472
-
Bicarbonate-dependent cleavage of adenosine triphosphate and other reactions catalyzed by Escherichia coli carbamyl phosphate synthetase
-
Anderson PM, Meister A (1966) Bicarbonate-dependent cleavage of adenosine triphosphate and other reactions catalyzed by Escherichia coli carbamyl phosphate synthetase. Biochemistry 5: 3157-3163.
-
(1966)
Biochemistry
, vol.5
, pp. 3157-3163
-
-
Anderson, P.M.1
Meister, A.2
-
3
-
-
0028044494
-
Inborn errors of urea synthesis
-
Batshaw ML (1994) Inborn errors of urea synthesis. Ann Neurol 35: 133-141.
-
(1994)
Ann Neurol
, vol.35
, pp. 133-141
-
-
Batshaw, M.L.1
-
4
-
-
0017184389
-
A rapid and sensitive method for the quantification of microgram quantities of protein utilizing the principle of protein-dye binding
-
Bradford MM (1976) A rapid and sensitive method for the quantification of microgram quantities of protein utilizing the principle of protein-dye binding. Anal Biochem 72: 248-254.
-
(1976)
Anal Biochem
, vol.72
, pp. 248-254
-
-
Bradford, M.M.1
-
5
-
-
0023906214
-
Carbamoyl-phosphate synthetase I. Kinetics of binding and dissociation of acetylglutamate and of activation and deactivation
-
Britton HG, Rubio V (1988) Carbamoyl-phosphate synthetase I. Kinetics of binding and dissociation of acetylglutamate and of activation and deactivation. Eur J Biochem 171: 615-622.
-
(1988)
Eur J Biochem
, vol.171
, pp. 615-622
-
-
Britton, H.G.1
Rubio, V.2
-
6
-
-
0021890991
-
The apparent K m of ammonia for carbamoyl phosphate synthetase (ammonia) in situ
-
Cohen NS, Kyan FS, Kyan SS, Cheung CW, Raijman L (1985) The apparent K m of ammonia for carbamoyl phosphate synthetase (ammonia) in situ. Biochem J 229: 205-211.
-
(1985)
Biochem J
, vol.229
, pp. 205-211
-
-
Cohen, N.S.1
Kyan, F.S.2
Kyan, S.S.3
Cheung, C.W.4
Raijman, L.5
-
7
-
-
0028868820
-
Regulatory changes in the control of carbamoyl phosphate synthetase induced by truncation and mutagenesis of the allosteric binding domain
-
Czerwinski RM, Mareya SM, Raushel FM (1995) Regulatory changes in the control of carbamoyl phosphate synthetase induced by truncation and mutagenesis of the allosteric binding domain. Biochemistry 34: 13920-13927.
-
(1995)
Biochemistry
, vol.34
, pp. 13920-13927
-
-
Czerwinski, R.M.1
Mareya, S.M.2
Raushel, F.M.3
-
8
-
-
0031880377
-
Prenatal diagnosis of carbamoyl phosphate synthetase I deficiency by identification of a missense mutation in CPSI
-
Finckh U, Kohlschutter A, Schafer H, Sperhake K, Colombo J, Gal A (1998) Prenatal diagnosis of carbamoyl phosphate synthetase I deficiency by identification of a missense mutation in CPSI. Hum Mutat 12, 206-211.
-
(1998)
Hum Mutat
, vol.12
, pp. 206-211
-
-
Finckh, U.1
Kohlschutter, A.2
Schafer, H.3
Sperhake, K.4
Colombo, J.5
Gal, A.6
-
9
-
-
0014410064
-
Modified determination of citrulline
-
Guthohrlein G, Knappe J (1968) Modified determination of citrulline. Anal Biochem 26: 188-191.
-
(1968)
Anal Biochem
, vol.26
, pp. 188-191
-
-
Guthohrlein, G.1
Knappe, J.2
-
10
-
-
1842833112
-
Mapping of protein phosphorylation by dual enzyme digestion and matrix-assisted laser desorption ionization-quadrupole orthogonal time-of-flight mass spectrometry
-
Han J, Pope M, Borchers C, Graves LM (2002) Mapping of protein phosphorylation by dual enzyme digestion and matrix-assisted laser desorption ionization-quadrupole orthogonal time-of-flight mass spectrometry. Anal Biochem 310: 215-218.
-
(2002)
Anal Biochem
, vol.310
, pp. 215-218
-
-
Han, J.1
Pope, M.2
Borchers, C.3
Graves, L.M.4
-
11
-
-
0025935047
-
Cloning and sequence of a cDNA encoding human carbamoyl phosphate synthetase I: Molecular analysis of hyperammonemia
-
Haraguchi Y, Uchino T, Takiguchi M, Endo F, Mori M, Matsuda I (1991) Cloning and sequence of a cDNA encoding human carbamoyl phosphate synthetase I: Molecular analysis of hyperammonemia. Gene 107: 335-340.
-
(1991)
Gene
, vol.107
, pp. 335-340
-
-
Haraguchi, Y.1
Uchino, T.2
Takiguchi, M.3
Endo, F.4
Mori, M.5
Matsuda, I.6
-
12
-
-
0033025947
-
S. pombe expression vector with 6X (His) tag for protein purification and potential for ligation-independent cloning
-
Hosfield TS, Lu Q (1999) S. pombe expression vector with 6X (His) tag for protein purification and potential for ligation-independent cloning. Biotechniques 27: 58-60
-
(1999)
Biotechniques
, vol.27
, pp. 58-60
-
-
Hosfield, T.S.1
Lu, Q.2
-
13
-
-
0027253962
-
Carbamyl phosphate synthetase I deficiency
-
Hoshide R, Matsuura T, Haraguchi Y, Endo F, Yoshinaga M, Matsuda I (1993) Carbamyl phosphate synthetase I deficiency. J Clin Invest 91: 1884-1887.
-
(1993)
J Clin Invest
, vol.91
, pp. 1884-1887
-
-
Hoshide, R.1
Matsuura, T.2
Haraguchi, Y.3
Endo, F.4
Yoshinaga, M.5
Matsuda, I.6
-
14
-
-
11144236655
-
Direct demonstration of carbamoyl phosphate formation on the C-terminal domain of carbamoyl phosphate synthetase
-
(Epub 2 Dec Epub 2004 Dec 2)
-
Kothe M, Purcarea C, Guy HI, Evans DR, Powers-Lee SG (2005) Direct demonstration of carbamoyl phosphate formation on the C-terminal domain of carbamoyl phosphate synthetase. Prot Sci 14: 37-44 (Epub 2 Dec Epub 2004 Dec 2).
-
(2005)
Prot Sci
, vol.14
, pp. 37-44
-
-
Kothe, M.1
Purcarea, C.2
Guy, H.I.3
Evans, D.R.4
Powers-Lee, S.G.5
-
15
-
-
0014949207
-
Cleavage of structural proteins during the assembly of the head of bacteriophage T4
-
Laemmli UK (1970) Cleavage of structural proteins during the assembly of the head of bacteriophage T4. Nature 227: 680-685.
-
(1970)
Nature
, vol.227
, pp. 680-685
-
-
Laemmli, U.K.1
-
16
-
-
0029815789
-
Phylogenetic analysis of carbamoylphosphate synthetase genes: Complex evolutionary history includes an internal duplication within a gene which can root the tree of life
-
Lawson FS, Charlesbois RL, Dillon JR (1996) Phylogenetic analysis of carbamoylphosphate synthetase genes: Complex evolutionary history includes an internal duplication within a gene which can root the tree of life. Mol Biol Evol 13: 970-977.
-
(1996)
Mol Biol Evol
, vol.13
, pp. 970-977
-
-
Lawson, F.S.1
Charlesbois, R.L.2
Dillon, J.R.3
-
17
-
-
17544379391
-
Requirement for the carboxyl-terminal domain of Saccharomyces cerevisiae carbamoyl phosphate synthetase
-
Lim AL, Powers-Lee SG (1996) Requirement for the carboxyl-terminal domain of Saccharomyces cerevisiae carbamoyl phosphate synthetase. J Biol Chem 271, 11400-11409.
-
(1996)
J Biol Chem
, vol.271
, pp. 11400-11409
-
-
Lim, A.L.1
Powers-Lee, S.G.2
-
18
-
-
0017900549
-
Carbamyl phosphate synthetase. Bicarbonate-dependent hydrolysis of ATP and potassium activation
-
Lusty CJ (1977) Carbamyl phosphate synthetase. Bicarbonate-dependent hydrolysis of ATP and potassium activation. J Biol Chem 253: 4270-4278.
-
(1977)
J Biol Chem
, vol.253
, pp. 4270-4278
-
-
Lusty, C.J.1
-
19
-
-
0017859652
-
Carbamoylphosphate synthetase I of rat-liver mitochondria
-
Lusty CJ (1978) Carbamoylphosphate synthetase I of rat-liver mitochondria. Eur J Biochem 85: 373-383.
-
(1978)
Eur J Biochem
, vol.85
, pp. 373-383
-
-
Lusty, C.J.1
-
20
-
-
0030016812
-
Required allosteric effector site for N-acetylglutamate on carbamoyl-phosphate synthetase I
-
McCudden CR, Powers-Lee SG (1996) Required allosteric effector site for N-acetylglutamate on carbamoyl-phosphate synthetase I. J Biol Chem 271: 18285-18294.
-
(1996)
J Biol Chem
, vol.271
, pp. 18285-18294
-
-
McCudden, C.R.1
Powers-Lee, S.G.2
-
21
-
-
0017765985
-
Glutamine-dependent carbamoyl phosphate synthetase: Catalysis and regulation
-
Meister A, Powers-Lee SG (1978) Glutamine-dependent carbamoyl phosphate synthetase: Catalysis and regulation. Adv Enzyme Regul 16: 289-315. 289-315.
-
(1978)
Adv Enzyme Regul
, vol.16
, pp. 289-315
-
-
Meister, A.1
Powers-Lee, S.G.2
-
22
-
-
0024494202
-
Evolution of urea synthesis in vertebrates: The piscine connection
-
Mommsen TP, Walsh PJ (1989) Evolution of urea synthesis in vertebrates: the piscine connection. Science 243: 72-75.
-
(1989)
Science
, vol.243
, pp. 72-75
-
-
Mommsen, T.P.1
Walsh, P.J.2
-
23
-
-
0029950031
-
Structural classification of proteins: New superfamilies
-
Murzin AG (1996) Structural classification of proteins: New superfamilies. Curr Opin Struct Biol 6: 386-394.
-
(1996)
Curr Opin Struct Biol
, vol.6
, pp. 386-394
-
-
Murzin, A.G.1
-
24
-
-
0020803887
-
The car B gene of Escherichia coli: A duplicated gene coding for the large subunit of carbamoyl-phosphate synthetase
-
Nyunoya H, Lusty CJ (1983) The car B gene of Escherichia coli: A duplicated gene coding for the large subunit of carbamoyl-phosphate synthetase. Proc Natl Acad Sci U S A 80: 4629-4633.
-
(1983)
Proc Natl Acad Sci U S A
, vol.80
, pp. 4629-4633
-
-
Nyunoya, H.1
Lusty, C.J.2
-
25
-
-
0022388322
-
Characterization and derivation of the gene coding for mitochondrial carbamoyl phosphate synthetase I of rat
-
Nyunoya H, Broglie KE, Widgren EE, Lusty CJ (1985) Characterization and derivation of the gene coding for mitochondrial carbamoyl phosphate synthetase I of rat. J Biol Chem 260: 9346-9356.
-
(1985)
J Biol Chem
, vol.260
, pp. 9346-9356
-
-
Nyunoya, H.1
Broglie, K.E.2
Widgren, E.E.3
Lusty, C.J.4
-
27
-
-
0017368370
-
Reversible binding of Pi by beef heart mitochondrial adenosine triphosphatase
-
Penefsky HS (1977) Reversible binding of Pi by beef heart mitochondrial adenosine triphosphatase. J Biol Chem 252: 2891-2899.
-
(1977)
J Biol Chem
, vol.252
, pp. 2891-2899
-
-
Penefsky, H.S.1
-
28
-
-
0019127301
-
Human carbamylphosphate synthetase I
-
Pierson DL, Brien JM (1980) Human carbamylphosphate synthetase I. J Biol Chem 255: 7891-7895.
-
(1980)
J Biol Chem
, vol.255
, pp. 7891-7895
-
-
Pierson, D.L.1
Brien, J.M.2
-
29
-
-
0022977864
-
Domain structure of rat liver carbamyl phosphate synthetase I
-
Powers-Lee SG, Corina K (1986) Domain structure of rat liver carbamyl phosphate synthetase I. J Biol Chem 261: 15349-15353.
-
(1986)
J Biol Chem
, vol.261
, pp. 15349-15353
-
-
Powers-Lee, S.G.1
Corina, K.2
-
30
-
-
0002847234
-
Urea synthesis and ammonia metabolism
-
In: Arias IM, Jakoby WB, Popper H, Schachter D, Shafritz DA, eds. 2nd edn. New York: Raven Press
-
Powers-Lee SG, Meister A (1988) Urea synthesis and ammonia metabolism. In: Arias IM, Jakoby WB, Popper H, Schachter D, Shafritz DA, eds. The Liver: Biology and Pathology, 2nd edn. New York: Raven Press, 317-329
-
(1988)
The Liver: Biology and Pathology
, pp. 317-329
-
-
Powers-Lee, S.G.1
Meister, A.2
-
31
-
-
0024598807
-
Physical location of the site for N-acetyl-L-glutamate, the allosteric activator of carbamoyl phosphate synthetase, in the 20-kilodalton COOH-terminal domain
-
Rodriguez-Aparicio LB, Guadalajara AM, Rubio V (1989) Physical location of the site for N-acetyl-L-glutamate, the allosteric activator of carbamoyl phosphate synthetase, in the 20-kilodalton COOH-terminal domain. Biochemistry 28: 3070-3074.
-
(1989)
Biochemistry
, vol.28
, pp. 3070-3074
-
-
Rodriguez-Aparicio, L.B.1
Guadalajara, A.M.2
Rubio, V.3
-
32
-
-
0020807785
-
Mitochondrial carbamoyl phosphate synthetase activity in the absence of N -acetyl-l-glutamate
-
Rubio V, Britton HG, Grisolia S (1983a) Mitochondrial carbamoyl phosphate synthetase activity in the absence of N -acetyl-l-glutamate. Eur J Biochem 134: 337-343.
-
(1983)
Eur J Biochem
, vol.134
, pp. 337-343
-
-
Rubio, V.1
Britton, H.G.2
Grisolia, S.3
-
33
-
-
0020650825
-
Activation of carbamoyl phosphate synthetase by cryoprotectants
-
Rubio V, Britton HG., Grisolia S (1983b) Activation of carbamoyl phosphate synthetase by cryoprotectants. Mol Cell Biochem 53-54, 279-298.
-
(1983)
Mol Cell Biochem
, vol.53-54
, pp. 279-298
-
-
Rubio, V.1
Britton, H.G.2
Grisolia, S.3
-
34
-
-
0036510389
-
Specificity determining residues in ammonia- and glutamine-dependent carbamoyl phosphate synthetases
-
Saeed-Kothe A, Powers-Lee SG (2002) Specificity determining residues in ammonia- and glutamine-dependent carbamoyl phosphate synthetases. J Biol Chem 277: 7231-7238.
-
(2002)
J Biol Chem
, vol.277
, pp. 7231-7238
-
-
Saeed-Kothe, A.1
Powers-Lee, S.G.2
-
35
-
-
0038035889
-
Gain of glutaminase function in mutants of the ammonia-specific frog carbamoyl phosphate synthetase
-
Saeed-Kothe A, Powers-Lee SG (2003) Gain of glutaminase function in mutants of the ammonia-specific frog carbamoyl phosphate synthetase. J Biol Chem 278: 26722-26726.
-
(2003)
J Biol Chem
, vol.278
, pp. 26722-26726
-
-
Saeed-Kothe, A.1
Powers-Lee, S.G.2
-
37
-
-
0027522463
-
Molecular studies on an ancient gene encoding for carbamoyl-phosphate synthetase
-
Schofield JP (1993) Molecular studies on an ancient gene encoding for carbamoyl-phosphate synthetase. Clin Sci 84: 119-128.
-
(1993)
Clin Sci
, vol.84
, pp. 119-128
-
-
Schofield, J.P.1
-
38
-
-
12144291030
-
Environmentally determined genetic expression: Clinical correlates with molecular variants of carbamyl phosphate synthetase I
-
Summar ML, Hall L, Christman B, et al (2004a) Environmentally determined genetic expression: Clinical correlates with molecular variants of carbamyl phosphate synthetase I. Mol Genet Metab 81 (Supplement 1): S12-S19.
-
(2004)
Mol Genet Metab
, vol.81
, Issue.SUPPL. 1
-
-
Summar, M.L.1
Hall, L.2
Christman, B.3
-
39
-
-
10744225397
-
Relationship between carbamoyl-phosphate synthetase genotype and systemic vascular function
-
Summar ML, Gainer JV, Pretorius M, et al (2004b) Relationship between carbamoyl-phosphate synthetase genotype and systemic vascular function. Hypertension 43: 186-191.
-
(2004)
Hypertension
, vol.43
, pp. 186-191
-
-
Summar, M.L.1
Gainer, J.V.2
Pretorius, M.3
-
40
-
-
0030957783
-
Structure of carbamoyl phosphate synthetase: A journey of 96 Å from substrate to product
-
Thoden JB, Holden HM, Wesenberg G, Raushel FM, Rayment I (1997) Structure of carbamoyl phosphate synthetase: A journey of 96 Å from substrate to product. Biochemistry 36: 6305-6316.
-
(1997)
Biochemistry
, vol.36
, pp. 6305-6316
-
-
Thoden, J.B.1
Holden, H.M.2
Wesenberg, G.3
Raushel, F.M.4
Rayment, I.5
-
41
-
-
13044313466
-
The structure of carbamoyl phosphate synthetase determined to 2.1 Å resolution
-
Thoden JB, Raushel FM, Benning MM, Rayment I, Holden HM (1999) The structure of carbamoyl phosphate synthetase determined to 2.1 Å resolution. Acta Crystallogr D Biol Crystallogr 55: 8-24.
-
(1999)
Acta Crystallogr D Biol Crystallogr
, vol.55
, pp. 8-24
-
-
Thoden, J.B.1
Raushel, F.M.2
Benning, M.M.3
Rayment, I.4
Holden, H.M.5
-
42
-
-
0037076028
-
Persistent pulmonary hypertension of the newborn
-
Vosatka RJ (2002) Persistent pulmonary hypertension of the newborn. N Engl J Med 346: 864.
-
(2002)
N Engl J Med
, vol.346
, pp. 864
-
-
Vosatka, R.J.1
|