Rationale for diagnosing human prion disease

World Journal of Biological Psychiatry

Volumn 5, Issue 2, 2004, Pages 83-91

  Kovács, Gábor ^a,b   Voigtländer, Till ^a   Gelpi, Ellen ^a   Budka, Herbert ^a  

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b NATIONAL INSTITUTE OF PSYCHIATRY AND NEUROLOGY   (Hungary)

Author keywords

14 3 3; Cerebrospinal fluid; Creutzfeldt Jakob disease; Prion protein; Prion protein gene

Indexed keywords

BINDING PROTEIN; COPPER; PRION PROTEIN; PROTEIN 14 3 3; PROTEINASE; AMYLOID; INFECTIOUS AMYLOID PRECURSOR PROTEIN; PRNP PROTEIN, HUMAN; PROTEIN PRECURSOR; TYROSINE 3 MONOOXYGENASE;

AUTOPSY; BIOACCUMULATION; BIOPSY TECHNIQUE; BODY FLUID; BOVINE SPONGIFORM ENCEPHALOPATHY; CELL LOSS; CODON; CREUTZFELDT JAKOB DISEASE; DEGENERATIVE DISEASE; DISEASE ASSOCIATION; DISEASE COURSE; ELECTROENCEPHALOGRAPHY; FAMILIAL DISEASE; FATAL FAMILIAL INSOMNIA; GENE EXPRESSION; GENE MUTATION; GENETIC POLYMORPHISM; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; IMMUNOHISTOCHEMISTRY; KURU; LABORATORY TEST; NERVE CELL; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PHENOTYPE; PRION DISEASE; PROTEIN CEREBROSPINAL FLUID LEVEL; PROTEIN CONFORMATION; PROTEIN FUNCTION; REVIEW; SENSITIVITY ANALYSIS; SYMPTOMATOLOGY; TONSIL; WESTERN BLOTTING; BRAIN; CEREBROSPINAL FLUID; DIFFERENTIAL DIAGNOSIS; GENETICS; METABOLISM; PATHOLOGY; POINT MUTATION; PRION;

14-3-3 PROTEINS; AMYLOID; BRAIN; DIAGNOSIS, DIFFERENTIAL; ELECTROENCEPHALOGRAPHY; HUMANS; MAGNETIC RESONANCE IMAGING; PHENOTYPE; POINT MUTATION; POLYMORPHISM, GENETIC; PRION DISEASES; PRIONS; PROTEIN PRECURSORS; TYROSINE 3-MONOOXYGENASE;

EID: 4944262820     PISSN: 15622975     EISSN: 18141412     Source Type: Journal    
DOI: 10.1080/15622970410029916     Document Type: Review

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