Prion encephalopathy with insertion of octapeptide repeats: The number of repeats determines the type of cerebellar deposits

Neuropathology and Applied Neurobiology

Volumn 24, Issue 2, 1998, Pages 125-130

  Vital, C ^a   Gray, F ^b   Vital, A ^a   Parchi, P ^c   Capellari, S ^c   Petersen, R B ^c   Ferrer, X ^a   Jarnier, D ^a   Julien, J ^a   Gambetti, P ^c  

^a UNIVERSITÉ DE BORDEAUX   (France)

^b RAYMOND POINCARÉ HOSPITAL   (France)

^c CASE WESTERN RESERVE UNIVERSITY   (United States)

Author keywords

Creutzfeldt Jakob disease; Gerstmann Straussler Scheinker disease; Immunocytochemistry; Prion protein; Spongiform encephalopathy

Indexed keywords

ANTIBODY; EOSIN; HEMATOXYLIN; OCTAPEPTIDE; PRION PROTEIN;

ADULT; ARTICLE; BRAIN DISEASE; BRAIN SPONGIOSIS; CLINICAL ARTICLE; CREUTZFELDT JAKOB DISEASE; FEMALE; GERSTMANN STRAUSSLER SCHEINKER SYNDROME; HUMAN; HUMAN CELL; IMMUNOCYTOCHEMISTRY; MALE; NEUROPATHOLOGY; PRION DISEASE; PRIORITY JOURNAL;

ADULT; AGE OF ONSET; CEREBELLUM; GERSTMANN-STRAUSSLER-SCHEINKER DISEASE; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; NEUROPEPTIDES; OLIGOPEPTIDES; PRION DISEASES; PRIONS;

EID: 15444352327     PISSN: 03051846     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2990.1998.00098.x     Document Type: Article

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