Inherited deficiency of mannan-binding lectin-associated serine protease 2

New England Journal of Medicine

Volumn 349, Issue 6, 2003, Pages 554-560

  Stengaard Pedersen, Kristian ^a   Thiel, Steffen ^b   Gadjeva, Mihaela ^b   Møller Kristensen, Mette ^b   Sørensen, Rikke ^b   Jensen, Lise T ^a   Sjöholm, Anders G ^d   Fugger, Lars ^a,c   Jensenius, Jens C ^b  

^a AARHUS UNIVERSITY HOSPITAL   (Denmark)

^b AARHUS UNIVERSITY   (Denmark)

^c JOHN RADCLIFFE HOSPITAL   (United Kingdom)

^d LUND UNIVERSITY   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENT; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEASE 2; PREDNISOLONE; PROTEINASE; UNCLASSIFIED DRUG; DIAGNOSTIC AGENT; MANNAN BINDING LECTIN ASSOCIATED SERINE PROTEINASE; MASP2 PROTEIN, HUMAN; MONOCLONAL ANTIBODY; SERINE PROTEINASE;

ADULT; ARTICLE; CASE REPORT; COMPLEMENT SYSTEM; CONTROLLED STUDY; ENZYME DEFICIENCY; ENZYME STRUCTURE; GENE MUTATION; GENETIC DISORDER; HETEROZYGOSITY; HUMAN; IMMUNE SYSTEM; IMMUNOSUPPRESSIVE TREATMENT; INFECTION; INFLAMMATORY DISEASE; MALE; PRIORITY JOURNAL; SYSTEMIC LUPUS ERYTHEMATOSUS; CHEMICAL STRUCTURE; CHEMISTRY; COMPLEMENT LECTIN PATHWAY; DNA SEQUENCE; GENETICS; LUNG FIBROSIS; POINT MUTATION; ULCERATIVE COLITIS;

ADULT; ANTIBODIES, MONOCLONAL; COLITIS, ULCERATIVE; COMPLEMENT PATHWAY, MANNOSE-BINDING LECTIN; COMPLEMENT SYSTEM PROTEINS; HUMANS; MALE; MANNOSE-BINDING PROTEIN-ASSOCIATED SERINE PROTEASES; MOLECULAR STRUCTURE; POINT MUTATION; PULMONARY FIBROSIS; SEQUENCE ANALYSIS, DNA; SERINE ENDOPEPTIDASES;

EID: 0042709606     PISSN: 00284793     EISSN: None     Source Type: Journal    
DOI: 10.1056/NEJMoa022836     Document Type: Article

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