Single channel properties of heterotetrameric mutant RyR1 ion channels linked to core myopathies

Journal of Biological Chemistry

Volumn 283, Issue 10, 2008, Pages 6321-6329

  Xu, Le ^a   Wang, Ying ^a   Yamaguchi, Naohiro ^a   Pasek, Daniel A ^a   Meissner, Gerhard ^a  

^a UNIVERSITY OF NORTH CAROLINA SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ANIMAL CELL CULTURE; COBALT; COBALT COMPOUNDS; LIPID BILAYERS; MUSCLE; PORT TERMINALS; SHRINKAGE;

293 CELLS; CENTRAL CORE DISEASES; CHANNEL ACTIVITIES; HUMAN EMBRYONIC KIDNEYS; ION CHANNELS; MUTANT ALLELES; PORE REGIONS; RAPID RELEASES; RYANODINE RECEPTORS; SARCOPLASMIC RETICULUM; SINGLE CHANNELS; SKELETAL MUSCLES; WILD TYPES;

CALCIUM;

ION CHANNEL; RECEPTOR SUBUNIT; RYANODINE RECEPTOR 1; CALCIUM; POTASSIUM; RYANODINE RECEPTOR;

ARTICLE; CALCIUM TRANSPORT; CONTROLLED STUDY; EXCITATION CONTRACTION COUPLING; GENE MUTATION; HUMAN; HUMAN CELL; MYOPATHY; POTASSIUM CONDUCTANCE; PRIORITY JOURNAL; SARCOPLASMIC RETICULUM; AMINO ACID SUBSTITUTION; ANIMAL; CELL LINE; CENTRAL CORE DISEASE; GENETICS; METABOLISM; MISSENSE MUTATION; MUSCLE CONTRACTION; RABBIT; SKELETAL MUSCLE;

AMINO ACID SUBSTITUTION; ANIMALS; CALCIUM; CELL LINE; HUMANS; MUSCLE CONTRACTION; MUSCLE, SKELETAL; MUTATION, MISSENSE; MYOPATHY, CENTRAL CORE; POTASSIUM; RABBITS; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL; SARCOPLASMIC RETICULUM;

EID: 44449105177     PISSN: 00219258     EISSN: 1083351X     Source Type: Journal    
DOI: 10.1074/jbc.M707353200     Document Type: Article

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