The pore region of the skeletal muscle ryanodine receptor is a primary locus for excitation-contraction uncoupling in central core disease

Journal of General Physiology

Volumn 121, Issue 4, 2003, Pages 277-286

  Avila, Guillermo ^a   O'Connell, Kristen M S ^b   Dirksen, Robert T ^c  

^a DEPARTAMENTO DE FÍSICA   (Mexico)

^b Department of Environmental and Radiological Health Sciences   (United States)

^c UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

Author keywords

Calcium channel; Excitation contraction coupling; Muscle disease; Skeletal muscle

Indexed keywords

CALCIUM ION; RYANODINE RECEPTOR;

AMINO TERMINAL SEQUENCE; ANIMAL CELL; ANIMAL TISSUE; ARTICLE; CALCIUM TRANSPORT; CARBOXY TERMINAL SEQUENCE; CENTRAL CORE DISEASE; DEPOLARIZATION; EXCITATION CONTRACTION COUPLING; GENE DELETION; GENE LOCUS; GENE MUTATION; MOUSE; MUSCLE DISEASE; MYOTUBE; NEWBORN; NONHUMAN; SKELETAL MUSCLE;

AMINO ACID SEQUENCE; ANIMALS; CALCIUM; CALCIUM SIGNALING; CELLS, CULTURED; HUMANS; ION CHANNEL GATING; MICE; MOLECULAR SEQUENCE DATA; MUSCLE CONTRACTION; MUSCLE FIBERS; MUTAGENESIS, SITE-DIRECTED; MYOPATHY, CENTRAL CORE; POROSITY; RABBITS; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL; STRUCTURE-ACTIVITY RELATIONSHIP;

EID: 0037390156     PISSN: 00221295     EISSN: None     Source Type: Journal    
DOI: 10.1085/jgp.200308791     Document Type: Article

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