The mild form of mucopolysaccharidosis type I (Scheie syndrome) is associated with increased ascending aortic stiffness

Heart and Vessels

Volumn 23, Issue 2, 2008, Pages 108-111

  Nemes, Attila ^a,b   Timmermans, Remco G M ^a   Wilson, J H P ^a   Soliman, Osama I I ^a,c   Krenning, Boudewijn J ^a   ten Cate, Folkert J ^a   Geleijnse, Marcel L ^a  

^a ERASMUS MEDICAL CENTER   (Netherlands)

^b UNIVERSITY OF SZEGED   (Hungary)

^c AL AZHAR UNIVERSITY   (Egypt)

Author keywords

Aortic distensibility; Aortic stiffness; Echocardiography; Mucopolysaccharidosis

Indexed keywords

GLYCOSAMINOGLYCAN; LEVO IDURONIDASE;

ADULT; AORTA DISEASE; ARTERIAL STIFFNESS; ARTERY COMPLIANCE; ARTERY DIAMETER; ARTICLE; ASCENDING AORTA; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE SEVERITY; DOPPLER ECHOCARDIOGRAPHY; ENZYME ANALYSIS; ENZYME DEFICIENCY; FEMALE; FOLLOW UP; HEART DISEASE; HUMAN; HUMAN CELL; MALE; PRIORITY JOURNAL; SCHEIE SYNDROME; TRANSTHORACIC ECHOCARDIOGRAPHY;

ADULT; AORTA; BLOOD PRESSURE; CASE-CONTROL STUDIES; ECHOCARDIOGRAPHY, DOPPLER; ELASTICITY; FEMALE; HUMANS; MALE; MUCOPOLYSACCHARIDOSIS I; PHENOTYPE; SEVERITY OF ILLNESS INDEX; YOUNG ADULT;

EID: 41849125655     PISSN: 09108327     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00380-007-1013-x     Document Type: Article

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