The heart in the Hurler syndrome. Gross, histologic and ultrastructural observations in five necropsy cases

The American Journal of Cardiology

Volumn 38, Issue 4, 1976, Pages 487-501

  Rentería, Vicente G ^a   Ferrans, Victor J ^a   Roberts, William C ^a  

^a NATIONAL HEART LUNG AND BLOOD INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AORTA WALL; AUTOPSY; CARDIOVASCULAR SYSTEM; COLLAGEN SYNTHESIS; CYTOLOGY; DIAGNOSIS; ELECTRON MICROSCOPY; ENZYME DEFICIENCY; HEART; HISTOLOGY; HURLER SYNDROME; MAJOR CLINICAL STUDY;

ADOLESCENT; AORTA; ARTERIOSCLEROSIS; CALCINOSIS; CHILD; CONNECTIVE TISSUE; CORONARY VESSELS; CYTOPLASMIC GRANULES; ELASTIC TISSUE; FEMALE; HEART MURMURS; HEART VALVES; HUMAN; MALE; MUCOPOLYSACCHARIDOSIS I; MUSCLE, SMOOTH; MYOCARDIUM; VACUOLES;

EID: 0017145225     PISSN: 00029149     EISSN: None     Source Type: Journal    
DOI: 10.1016/0002-9149(76)90468-9     Document Type: Review

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