Impaired elastogenesis in Hurler disease: Dermatan sulfate accumulation linked to deficiency in elastin-binding protein and elastic fiber assembly

American Journal of Pathology

Volumn 156, Issue 3, 2000, Pages 925-938

  Hinek, Aleksander ^a,b   Wilson, Sarah E ^a  

^a HOSPITAL FOR SICK CHILDREN   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

BINDING PROTEIN; CHAPERONE; DERMATAN SULFATE; ELASTIN; GLYCOSAMINOGLYCAN; HEPARAN SULFATE; LEVO IDURONIDASE; TROPOELASTIN;

ARTICLE; CONNECTIVE TISSUE; ELASTIC FIBER; HUMAN; HUMAN TISSUE; HURLER SYNDROME; PHENOTYPE; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN DEFICIENCY; PROTEIN EXPRESSION; SKIN FIBROBLAST;

EID: 0033888320     PISSN: 00029440     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0002-9440(10)64961-9     Document Type: Article

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