Cholesterol-deprivation increases mono-unsaturated very long-chain fatty acids in skin fibroblasts from patients with X-linked adrenoleukodystrophy

Biochimica et Biophysica Acta - Molecular and Cell Biology of Lipids

Volumn 1781, Issue 3, 2008, Pages 105-111

  Engelen, M ^a,b,c   Ofman, R ^a,b,c   Mooijer, P A W ^a,b,c   Poll The, B T ^a,b,c   Wanders, R J A ^a,b,c   Kemp, S ^a,b,c  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b EMMA CHILDREN S HOSPITAL   (Netherlands)

^c ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

ABCD1; Adrenoleukodystrophy; Cholesterol; Peroxisome; SCD; X ALD

Indexed keywords

ACYL COENZYME A DESATURASE; CHOLESTEROL; MONOUNSATURATED FATTY ACID; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ARTICLE; CHOLESTEROL METABOLISM; CHOLESTEROL SYNTHESIS; CONTROLLED STUDY; FATTY ACID DESATURATION; FATTY ACID OXIDATION; FIBROBLAST CULTURE; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN EXPRESSION; PROTEIN LIPID INTERACTION; SKIN FIBROBLAST; X CHROMOSOME LINKED DISORDER;

EID: 39849106740     PISSN: 13881981     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbalip.2007.12.003     Document Type: Article

References (32)

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