X-linked adrenoleukodystrophy mice demonstrate abnormalities in cholesterol metabolism

FEBS Letters

Volumn 579, Issue 25, 2005, Pages 5512-5516

  Weinhofer, Isabelle ^a   Forss Petter, Sonja ^a   Kunze, Markus ^a   Žigman, Mihaela ^a,b   Berger, Johannes ^a  

^a MEDICAL UNIVERSITY OF VIENNA   (Austria)

^b ERICH SCHMID INSTITUTE OF MATERIALS SCIENCE   (Austria)

Author keywords

ABCD1; ABCD1 deficient mouse; ALDP; Cholesterol; X ALD

Indexed keywords

ABC TRANSPORTER; ABC TRANSPORTER D1; ABC TRANSPORTER D2; ADRENOLEUKODYSTROPHY PROTEIN; ANTILIPEMIC AGENT; CHOLESTEROL; COLESTIPOL; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE; LIVER ENZYME; MEVINOLIN; UNCLASSIFIED DRUG; VERY LONG CHAIN FATTY ACID;

ADRENOLEUKODYSTROPHY; ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL CULTURE; CHOLESTEROL BLOOD LEVEL; CHOLESTEROL INTAKE; CHOLESTEROL METABOLISM; CONTROLLED STUDY; DOWN REGULATION; EMBRYO; ENZYME REGULATION; FIBROBLAST; HUMAN; HUMAN CELL; LIPID BRAIN LEVEL; MALE; MOUSE; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SPECIES DIFFERENCE; X CHROMOSOME LINKED DISORDER;

ADRENOLEUKODYSTROPHY; ANIMALS; ATP-BINDING CASSETTE TRANSPORTERS; CELLS, CULTURED; CHOLESTEROL; FATTY ACIDS; FIBROBLASTS; GENE EXPRESSION; GENE EXPRESSION REGULATION; HUMANS; HYDROXYMETHYLGLUTARYL COA REDUCTASES; LIVER; MICE; MICE, INBRED C57BL; MOLECULAR SEQUENCE DATA; RNA, MESSENGER;

MURINAE;

EID: 26844531338     PISSN: 00145793     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.febslet.2005.09.014     Document Type: Article

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