Disrupted membrane homeostasis and accumulation of ubiquitinated proteins in a mouse model of infantile neuroaxonal dystrophy caused by PLA2G6 mutations

American Journal of Pathology

Volumn 172, Issue 2, 2008, Pages 406-416

  Malik, Ibrahim ^a   Turk, John ^a   Mancuso, David J ^a   Montier, Laura ^a   Wohltmann, Mary ^a   Wozniak, David F ^a   Schmidt, Robert E ^a   Gross, Richard W ^a,b   Kotzbauer, Paul T ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b WASHINGTON UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA SYNUCLEIN; IRON; PHOSPHOLIPASE A2; PHOSPHOLIPASE A2 GROUP 6; UBIQUITIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANTIBODY LABELING; ARTICLE; BODY EQUILIBRIUM; BRAIN REGION; BRAIN TISSUE; CLIMBING; CONTROLLED STUDY; DEGENERATIVE DISEASE; GENE MUTATION; HOMEOSTASIS; MEMBRANE VESICLE; MOTOR DYSFUNCTION; MOUSE; NERVE DEGENERATION; NERVE FIBER; NERVE FIBER MEMBRANE; NEUROAXONAL DYSTROPHY; NEUROPATHOLOGY; NONHUMAN; ONSET AGE; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN DEGRADATION; ROTAROD TEST; SPHEROID CELL; UBIQUITINATION;

EID: 39549085125     PISSN: 00029440     EISSN: None     Source Type: Journal    
DOI: 10.2353/ajpath.2008.070823     Document Type: Article

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