Combined nutritional support and continuous extracorporeal removal therapy in the severe acute phase of maple syrup urine disease

Intensive Care Medicine

Volumn 27, Issue 11, 2001, Pages 1798-1806

  Jouvet, Philippe ^a   Jugie, Myriam ^a   Rabier, Daniel ^a   Desgrès, Jean ^b   Hubert, Philippe ^a   Marie Saudubray, Jean ^a   Khoa Man, Nguyen ^a  

^a HÔPITAL NECKER ENFANTS MALADES   (France)

^b Biochemistry Department   (France)

Author keywords

Children; Hemofiltration; Maple syrup urine disease; Neonates

Indexed keywords

BRANCHED CHAIN AMINO ACID; ISOLEUCINE; LEUCINE; OXOACID; VALINE;

ACUTE DISEASE; ADOLESCENT; AMINO ACID BLOOD LEVEL; ARTICLE; BRAIN INJURY; CHILD; CLINICAL ARTICLE; CLINICAL TRIAL; CONTROLLED CLINICAL TRIAL; CONTROLLED STUDY; ENTERIC FEEDING; EVALUATION; HEMODIALYSIS; HEMOFILTRATION; HUMAN; MAPLE SYRUP URINE DISEASE; METABOLITE; NEWBORN; NEWBORN INTENSIVE CARE; NUTRITIONAL SUPPORT; PROTEIN DEGRADATION; SURVIVAL RATE; TREATMENT OUTCOME;

ACUTE DISEASE; ADOLESCENT; CHILD; CHILD, PRESCHOOL; COHORT STUDIES; ENTERAL NUTRITION; FEMALE; HEMOFILTRATION; HUMANS; INFANT, NEWBORN; INTENSIVE CARE UNITS; LEUCINE; MALE; MAPLE SYRUP URINE DISEASE; NERVOUS SYSTEM DISEASES; PROTEINS; SURVIVAL RATE; TREATMENT OUTCOME;

EID: 0035214065     PISSN: 03424642     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00134-001-1124-2     Document Type: Article

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