Nutritional management of urea cycle disorders

Critical Care Clinics

Volumn 21, Issue 4 SUPPL., 2005, Pages

  Singh, Rani H ^a   Rhead, William J ^b   Smith, Wendy ^c,d   Lee, Brendan ^e   King, Lisa Sniderman ^f   Summar, Marshall ^g  

^a EMORY UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b MEDICAL COLLEGE OF WISCONSIN   (United States)

^c Barbara Bush Children's Hospital   (United States)

^d Maine Pediatric Specialty Group   (United States)

^e BAYLOR COLLEGE OF MEDICINE   (United States)

^f UNIVERSITY OF WASHINGTON SCHOOL OF MEDICINE   (United States)

^g VANDERBILT UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID MIXTURE; AMMONIA; ARGININE; ARYLBUTYRIC ACID DERIVATIVE; BENZOIC ACID; CITRULLINE; GLUCOSE; INSULIN; INTRALIPID; IRON; ORNITHINE CARBAMOYLTRANSFERASE; PHENYLACETIC ACID DERIVATIVE;

AMMONIA BLOOD LEVEL; CASE REPORT; CITRULLINEMIA; CONFERENCE PAPER; DISORDERS OF AMINO ACID AND PROTEIN METABOLISM; FEMALE; HUMAN; HYPERAMMONEMIA; INBORN ERROR OF METABOLISM; LABORATORY TEST; NUTRITIONAL SUPPORT; PHYSICAL EXAMINATION; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN RESTRICTION; SCHOOL CHILD; UREA CYCLE; UREA CYCLE DISORDER;

ACUTE DISEASE; ADOLESCENT; ADULT; AMINO ACID METABOLISM, INBORN ERRORS; CHILD; CHILD, PRESCHOOL; CHRONIC DISEASE; CITRULLINEMIA; FEMALE; HUMANS; HYPERAMMONEMIA; INFANT, NEWBORN; MALE; ORNITHINE CARBAMOYLTRANSFERASE DEFICIENCY DISEASE; PRACTICE GUIDELINES; UREA;

EID: 26844432821     PISSN: 07490704     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ccc.2005.08.003     Document Type: Conference Paper

References (19)

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