Progression of multiple behavioral deficits with various ages of onset in a murine model of Hurler syndrome

Brain Research

Volumn 1188, Issue 1, 2008, Pages 241-253

  Pan, Dao ^a,b   Sciascia II, Anthony ^a   Vorhees, Charles V ^a,b   Williams, Michael T ^a,b  

^a CINCINNATI CHILDREN S HOSPITAL RESEARCH FOUNDATION   (United States)

^b UNIVERSITY OF CINCINNATI COLLEGE OF MEDICINE   (United States)

Author keywords

Animal model; Behavior profile; Hurler syndrome; Locomotion; Lysosomal storage disease; Open field; Spatial learning

Indexed keywords

ANIMAL EXPERIMENT; ANIMAL MODEL; ANXIETY; ARTICLE; BEHAVIOR DISORDER; COMPULSION; CONTROLLED STUDY; FEMALE; HABITUATION; HURLER SYNDROME; LEARNING; LOCOMOTION; MALE; MATURITY; MAZE TEST; MEMORY; MEMORY CONSOLIDATION; MEMORY DISORDER; MOUSE; NONHUMAN; OPEN FIELD TEST; PHENOTYPE; PRIORITY JOURNAL; STARTLE REFLEX; VISUAL MEMORY;

AGE OF ONSET; ANIMALS; ANXIETY DISORDERS; BEHAVIOR, ANIMAL; BRAIN; DELIRIUM, DEMENTIA, AMNESTIC, COGNITIVE DISORDERS; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; FEMALE; HYPERKINESIS; IDURONIDASE; LEARNING DISORDERS; MALE; MEMORY DISORDERS; MENTAL DISORDERS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MUCOPOLYSACCHARIDOSIS I; PHENOTYPE; STARTLE REACTION;

ANIMALIA; MURINAE; MUS;

EID: 37349103032     PISSN: 00068993     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.brainres.2007.10.036     Document Type: Article

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